コーパス検索結果 (left1)
通し番号をクリックするとPubMedの該当ページを表示します
1 MCAD-deficiency is the most common inborn error of fatty
2 rst (fast) step involved the formation of an MCAD-IACoA collision complex in which the electronic str
4 pha paralleled NRRE-1 binding activities and MCAD expression during brown adipocyte differentiation,
5 een either human or P. denitrificans ETF and MCAD demonstrates that the human ETF functions optimally
6 inal adipose tissue, CL-upregulated FASN and MCAD in distinct cell populations: high MCAD expression
7 ures of the product analogue in its free and MCAD-bound forms have been characterized by Raman differ
10 , HCV infection significantly decreased both MCAD and SCAD expression, which is controlled by FoxA2.
14 ed to be the catalytic base in medium-chain (MCAD) and short-chain acyl-CoA dehydrogenases and is con
15 ed by the C1 and C3 HD carbons in the HD-CoA/MCAD complex is proposed to arise from the ring current
16 medium-chain acyl coenzyme A dehydrogenase (MCAD) and short-chain acyl coenzyme A dehydrogenase (SCA
18 medium-chain acyl coenzyme A dehydrogenase (MCAD), a nuclearly encoded mitochondrial fatty acid beta
19 medium chain acyl-coenzyme A dehydrogenase (MCAD), requires cis-acting elements located within the p
20 medium chain acyl-coenzyme A dehydrogenase (MCAD; 1.8+/-0.1 versus 2.9+/-0.3 micromol x min(-1) x g(
21 Medium-chain acyl-coenzyme A dehydrogenase (MCAD; mouse gene Acadm; human gene ACADM) catalyzes the
23 kidney medium chain acyl-CoA dehydrogenase (MCAD) by isothermal titration microcalorimetry under a v
27 376, of medium-chain acyl-CoA dehydrogenase (MCAD) has been known to abstract the alpha-proton from a
28 SN) and medium chain acyl-CoA dehydrogenase (MCAD) protein within the same cells in classic brown and
29 tion in medium chain acyl-CoA dehydrogenase (MCAD), creates a complementary cavity of 18 A(3) dimensi
30 porcine medium chain acyl-CoA dehydrogenase (MCAD), Glu254 in human isovaleryl-CoA dehydrogenase (IVD
31 r) with medium chain acyl-CoA dehydrogenase (MCAD), were essentially identical, suggesting that the p
32 ncoding medium-chain acyl-CoA dehydrogenase (MCAD), which catalyzes the initial step in mitochondrial
33 n liver medium chain acyl-CoA dehydrogenase (MCAD)-catalyzed reaction proceeds via abstraction of an
34 n liver medium-chain acyl-CoA dehydrogenase (MCAD)-catalyzed reaction, we became interested in deline
41 g human medium-chain acyl-CoA dehydrogenase (MCAD, which catalyzes a rate-limiting step in the FAO cy
46 lytic base (pK(a,ox) approximately 6.5, free MCAD), it has little effect on the pK of Glu99 (pK(a,ox)
49 ociation constant of MCAD +octenoyl-CoA <==> MCAD-octenoyl-CoA yields a pKa for the free enzyme of 6.
50 ation mixture of MCAD and IACoA ([IACoA] >> [MCAD] > Kd) increases from 12 to 35 degrees C, the resul
51 and MCAD in distinct cell populations: high MCAD expression occurred in multilocular adipocytes that
53 atment options, we explored the use of human MCAD (hMCAD) mRNA in fibroblasts from patients with MCAD
60 cient patient cells resulted in an increased MCAD protein that localized to mitochondria, concomitant
63 or the binding of octenoyl-CoA to pig kidney MCAD (which is believed to be structurally identical to
64 r Glu376 and Glu99 in the reduced pig kidney MCAD.HD-CoA complex, 9.8 and 8.6, respectively, suggest
68 to be structurally identical to human liver MCAD) is only -0.37 kcal mol-1 K-1 prompt us to question
70 ous doses of the hMCAD mRNA-LNP complex (LNP-MCAD) into Acadm-/- mice produced a significant level of
73 estion that the carboxyl group of Glu-376 of MCAD is intimately involved in modulating the microscopi
76 pH dependence of the association constant of MCAD +octenoyl-CoA <==> MCAD-octenoyl-CoA yields a pKa f
80 ro-AST formation is not a special feature of MCAD-deficiency but rather a non-specific, coincidental
82 cadm-/- mice produced a significant level of MCAD protein with increased enzyme activity in liver, he
83 the temperature of the incubation mixture of MCAD and IACoA ([IACoA] >> [MCAD] > Kd) increases from 1
84 ry (n) of 0.89 mole of octenoyl-CoA/(mole of MCAD subunit), delta G = -8.75 kcal/mol, delta H = -10.3
86 ferase reporter confirmed that repression of MCAD gene expression in the hypertrophied ventricle occu
88 (pK(a,ox) approximately 7.4) in the oxidized MCAD.HD-CoA complex indicate that while binding of the C
89 duct analogue that binds tightly to oxidized MCAD (K(dox) = 3.5 +/- 0.1 microM, pH 7.6) and elicits a
90 A), a product analogue, with recombinant pig MCAD (pMCAD) has been studied using (13)C NMR and (1)H-(
92 Therefore, targeting the caspase-1/PPARgamma/MCAD pathway might be a promising therapeutic approach t
94 hepatic expression of key PPAR-alpha target (MCAD, mitochondrial HMG CoA synthase, ACO, CYP4A3) and o
100 he spectral changes, binding constant of the MCAD-IACoA complex, and the rate constants for the conve
101 thalpies, we discerned that formation of the MCAD-octenoyl-CoA complex, at pH 7.6, accompanies abstra
103 ntaining an estrogen response element or the MCAD gene promoter by ERRalpha and the related isoform E
104 enone fragment is polarized upon binding to MCAD such that the electron density at the C3 and C1 car
105 These results suggest that, upon binding to MCAD, HD-CoA is selectively polarized such that partial
106 s are narrower when the ligands are bound to MCAD than when they are free in the protein solution.
107 n the NMR and Raman data for HD-CoA bound to MCAD, (13)C NMR spectra have been obtained for HD-CoA bo
108 the fact that the binding of octenoyl-CoA to MCAD is primarily dominated by the hydrophobic forces.
109 data for the binding of 2-azaoctanoyl-CoA to MCAD revealed that the overall interaction proceeds via
110 acetoacetyl-CoA when bound as an enolate to MCAD and enoyl-CoA hydratase and is used to rationalize
111 rimetric studies for the binding of IACoA to MCAD reveal that the overall binding energy at 25 degree
112 tic consequences for the binding of IACoA to MCAD, the apparent similarity between the van't Hoff and
113 s of the two reaction steps in the wild-type MCAD demonstrate that the reaction proceeds by a stepwis
114 te hippurate and identify beta-oxidation via MCAD as a novel mechanism by which mammals metabolize mi
116 MCAD) mRNA in fibroblasts from patients with MCAD deficiency to provide functional MCAD protein and r
117 horetic mobility-shift assays performed with MCAD promoter fragments and nuclear protein extracts pre