ライフサイエンスコーパス: lymphohistiocytosis

1 crophage activation syndrome-haemophagocytic lymphohistiocytosis).

2 ficiencies including familial hemophagocytic lymphohistiocytosis.

3 in the development of lethal hemophagocytic lymphohistiocytosis.

4 assified as X-linked familial hemophagocytic lymphohistiocytosis.

5 ce disease in mouse models of hemophagocytic lymphohistiocytosis.

6 erhans cell histiocytosis and hemophagocytic lymphohistiocytosis.

7 veral human diseases, such as hemophagocytic lymphohistiocytosis.

8 ge or younger and had primary hemophagocytic lymphohistiocytosis.

9 phoproliferative disease, and hemophagocytic lymphohistiocytosis.

10 nc13-4 as a cause of familial hemophagocytic lymphohistiocytosis.

11 and virus-associated reactive hemophagocytic lymphohistiocytosis.

12 ied in humans with familial hematophagocytic lymphohistiocytosis.

13 with some cases of CAEBV with hemophagocytic lymphohistiocytosis.

14 ferative disease and familial hemophagocytic lymphohistiocytosis.

15 ytokine release syndrome and haemophagocytic lymphohistiocytosis.

16 acrophage activation syndrome/hemophagocytic lymphohistiocytosis.

17 organ failure associated with hemophagocytic lymphohistiocytosis.

18 een reported in patients with hemophagocytic lymphohistiocytosis.

19 e of whom developed secondary hemophagocytic lymphohistiocytosis.

20 valuable diagnostic tool for hemophagocytic lymphohistiocytosis.

21 severely elevated ferritin is hemophagocytic lymphohistiocytosis.

22 sociated with younger age and hemophagocytic lymphohistiocytosis.

23 gulatory disorders, including hemophagocytic lymphohistiocytosis.

24 e (MAS), a secondary form of haemophagocytic lymphohistiocytosis.

25 ogression, and development of hemophagocytic lymphohistiocytosis.

26 maglobulinemia, lymphoma, and hemophagocytic lymphohistiocytosis.

27 plantation in severe familial hemophagocytic lymphohistiocytosis.

28 asmussen's encephalitis, and haemophagocytic lymphohistiocytosis.

29 iated with signs of fulminant hemophagocytic lymphohistiocytosis.

30 ing the diagnosis of familial hemophagocytic lymphohistiocytosis.

31 apy for patients with primary hemophagocytic lymphohistiocytosis.

32 e eight HLH-2004 criteria for hemophagocytic lymphohistiocytosis.

33 or, in adults with secondary haemophagocytic lymphohistiocytosis.

34 g in patients with secondary haemophagocytic lymphohistiocytosis.

35 ted in the setting of primary hemophagocytic lymphohistiocytosis.

36 mining patients with familial hemophagocytic lymphohistiocytosis.

37 sing a specific treatment for hemophagocytic lymphohistiocytosis.

38 only for infection-triggered hemophagocytic lymphohistiocytosis.

39 a, 40 were considered to have hemophagocytic lymphohistiocytosis (1.52%).

40 Meeting five or more of eight hemophagocytic lymphohistiocytosis 2004 diagnostic criteria serves as a

41 ytosis diagnosis was based on Hemophagocytic Lymphohistiocytosis-2004 criteria and the HScore.

42 a protein mutated in familial hemophagocytic lymphohistiocytosis 3, as a WPB-tethering factor.

43 nt for 20% to 40% of familial hemophagocytic lymphohistiocytosis, a fatal disease of early childhood

44 these genes develop familial hemophagocytic lymphohistiocytosis, a primary immunodeficiency characte

45 3.54; 95% CI, 1.80-6.95), and hemophagocytic lymphohistiocytosis (adjusted odds ratio, 2.79; 95% CI,

46 1.86; 95% CI, 1.15-2.99), and hemophagocytic lymphohistiocytosis (adjusted odds ratio, 3.09; 95% CI,

47 atients (2/4, grade 3-4), and hemophagocytic lymphohistiocytosis affected 2 patients.

48 mes in childhood survivors of hemophagocytic lymphohistiocytosis after hematopoietic stem cell transp

49 usly associated with familial hemophagocytic lymphohistiocytosis and a novel homozygous missense vari

50 tment-related deaths (due to haemophagocytic lymphohistiocytosis and cardiac arrest) were previously

51 ically suspected diagnosis of hemophagocytic lymphohistiocytosis and found 28 patients with single he

52 AKI is frequent in severe hemophagocytic lymphohistiocytosis and has been attributed to multiorga

53 0.99 (95% CI, 0.99-0.99) for hemophagocytic lymphohistiocytosis and HScore, respectively.

54 ed for patients with familial hemophagocytic lymphohistiocytosis and is often valuable in patients wi

55 as been proposed that in both hemophagocytic lymphohistiocytosis and macrophage activation syndrome,

56 died during follow-up due to haemophagocytic lymphohistiocytosis and macrophage activation syndrome.

57 Rosai-Dorfman disease and (5) hemophagocytic lymphohistiocytosis and macrophage activation syndrome.

58 preclinical disease models of hemophagocytic lymphohistiocytosis and multiple sclerosis, which are dr

59 plications for patients with haemophagocytic lymphohistiocytosis and other cytokine-release syndromes

60 ages, is seen in the disorder hemophagocytic lymphohistiocytosis and other inflammatory contexts.

61 auto-inflammation, including hemophagocytic lymphohistiocytosis and rash in the most severe form (NO

62 In familial hemophagocytic lymphohistiocytosis and severe, persistent, or relapsing

63 y syndromes, however, such as hemophagocytic lymphohistiocytosis and the newly classified proteasome

64 the diagnostic criteria for haemophagocytic lymphohistiocytosis), and pharmacodynamic biomarkers.

65 cciniforme-like lymphoma with hemophagocytic lymphohistiocytosis, and 2 had EBV-positive smooth muscl

66 peripheral T-cell lymphomas, hemophagocytic lymphohistiocytosis, and chronic active EBV disease.

67 SARS-CoV-2 infection, sepsis, hemophagocytic lymphohistiocytosis, and cytokine shock.

68 SARS-CoV-2 infection, sepsis, hemophagocytic lymphohistiocytosis, and cytokine shock.

69 une-effector cell associated haemophagocytic lymphohistiocytosis, and septic shock, and the second du

70 ymphoproliferative disorders, hemophagocytic lymphohistiocytosis, and smooth muscle and epithelial tu

71 fy the frequency of secondary hemophagocytic lymphohistiocytosis, and the main prognostic factors for

72 such as hyperinflammation or hemophagocytic lymphohistiocytosis are a frequent yet paradoxical accom

73 mmary, childhood survivors of hemophagocytic lymphohistiocytosis are at risk of long-term cognitive a

74 ies in patients with familial hemophagocytic lymphohistiocytosis are decreased natural killer and cyt

75 ity and 91.9% specificity for hemophagocytic lymphohistiocytosis (area under the curve, 0.963; 95% CI

76 nib in adults with secondary haemophagocytic lymphohistiocytosis at the University of Michigan Rogel

77 some cases of type 2 familial hemophagocytic lymphohistiocytosis, based on the pharmacologic inhibiti

78 d with suspected or diagnosed hemophagocytic lymphohistiocytosis, between January 1, 2000, and August

79 ral nervous system-restricted hemophagocytic lymphohistiocytosis, can be non-invasively diagnosed wit

80 immunodeficiency and a fatal hemophagocytic lymphohistiocytosis caused by impaired function of cytot

81 Multiple prior malignancies, hemophagocytic lymphohistiocytosis, congenital immunodeficiency, and he

82 0.98 (95% CI, 0.96-0.99) for hemophagocytic lymphohistiocytosis criteria and 0.99 (95% CI, 0.99-1) f

83 our study suggests HScore and hemophagocytic lymphohistiocytosis criteria to be highly discriminant i

84 Median number of hemophagocytic lymphohistiocytosis criteria was 4 (4-5) in hemophagocyt

85 tients (p < 0.001); number of hemophagocytic lymphohistiocytosis criteria was 4 (4-5) vs 1 (0-1), res

86 XBP2 associated with familial hemophagocytic lymphohistiocytosis, CTL and NK cell degranulation were

87 ammatory syndromes, including hemophagocytic lymphohistiocytosis, developed after SARS-CoV-2 mRNA vac

88 Hemophagocytic lymphohistiocytosis diagnosis was based on Hemophagocyti

89 Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis (EBV-HLH) is a fatal hyperinflammato

90 Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis (EBV-HLH).

91 Familial hemophagocytic lymphohistiocytosis (F-HLH) and Griscelli syndrome type

92 as both acquired and familial hemophagocytic lymphohistiocytosis (FHL) forms.

93 Familial hemophagocytic lymphohistiocytosis (FHL) is a genetically determined hy

94 Familial hemophagocytic lymphohistiocytosis (FHL) is a life-threatening disorder

95 Familial hemophagocytic lymphohistiocytosis (FHL) is a rare and often fatal diso

96 Familial hemophagocytic lymphohistiocytosis (FHL) is a rare, genetically heterog

97 Familial hemophagocytic lymphohistiocytosis (FHL) is a rare, rapidly fatal, auto

98 Familial hemophagocytic lymphohistiocytosis (FHL) is an inherited, fatal disorde

99 Familial hemophagocytic lymphohistiocytosis (FHL) is caused by genetic defects i

100 d from patients with familial hemophagocytic lymphohistiocytosis (FHL) to screen for biologic correla

101 m syndromes, such as familial hemophagocytic lymphohistiocytosis (FHL), are lethal disorders caused b

102 eferred to as having familial hemophagocytic lymphohistiocytosis (FHL), have various underlying genet

103 been associated with familial hemophagocytic lymphohistiocytosis (FHL).

104 result in a form of familial hemophagocytic lymphohistiocytosis (FHL).

105 tations cause type 3 familial hemophagocytic lymphohistiocytosis (FHL3), a fatal disease marked by ma

106 ty, and give rise to familial hemophagocytic lymphohistiocytosis (FHL4 or FHL5, respectively).

107 Patients with familial hemophagocytic lymphohistiocytosis (fHLH) showed prominent peaks in IFN

108 ollectively known as familial hemophagocytic lymphohistiocytosis (FHLH), all associated with various

109 to meningoencephalitis and/or hemophagocytic lymphohistiocytosis following live-attenuated viral vacc

110 ritin levels to differentiate hemophagocytic lymphohistiocytosis from other causes of hyperferritinem

111 sing pneumonia (grade 3) and haemophagocytic lymphohistiocytosis (grade 5) which led to one death.

112 hyperferritinemia, and other hemophagocytic lymphohistiocytosis hallmarks were apparent.

113 patients with severe forms of hemophagocytic lymphohistiocytosis have been developed.

114 Haemophagocytic syndromes (haemophagocytic lymphohistiocytosis) have a wide range of causes, sympto

115 oped all clinical symptoms of hemophagocytic lymphohistiocytosis (HLH) after infection with lymphocyt

116 vation and the fatal disorder hemophagocytic lymphohistiocytosis (HLH) after infection.

117 ated with a high incidence of hemophagocytic lymphohistiocytosis (HLH) and a lack of lymphoma, sugges

118 Hemophagocytic lymphohistiocytosis (HLH) and macrophage activation synd

119 The clinical syndromes of hemophagocytic lymphohistiocytosis (HLH) and macrophage activation synd

120 Hemophagocytic lymphohistiocytosis (HLH) and macrophage activation synd

121 atory state characteristic of hemophagocytic lymphohistiocytosis (HLH) and macrophage activation synd

122 vere immunoregulatory disease hemophagocytic lymphohistiocytosis (HLH) arise from biallelic mutations

123 ll transplantation (HSCT) for hemophagocytic lymphohistiocytosis (HLH) at the cost of more frequent m

124 9 has parallels to secondary haemophagocytic lymphohistiocytosis (HLH) both clinically and based on m

125 9) has parallels to secondary hemophagocytic lymphohistiocytosis (HLH) both clinically and based on m

126 Primary hemophagocytic lymphohistiocytosis (HLH) can be caused by biallelic mut

127 and develop spontaneous fatal hemophagocytic lymphohistiocytosis (HLH) characterized by inflammatory

128 Hemophagocytic lymphohistiocytosis (HLH) comprises a severe hyperinflam

129 Hemophagocytic lymphohistiocytosis (HLH) comprises an emerging spectrum

130 etic cell transplantation for hemophagocytic lymphohistiocytosis (HLH) disorders is associated with s

131 mary and infection-associated hemophagocytic lymphohistiocytosis (HLH) from patients with early sepsi

132 Hemophagocytic lymphohistiocytosis (HLH) is a devastating disorder of u

133 Hemophagocytic lymphohistiocytosis (HLH) is a disorder that has been re

134 Hemophagocytic lymphohistiocytosis (HLH) is a fatal disorder of immune

135 Hemophagocytic lymphohistiocytosis (HLH) is a hyperinflammatory disorde

136 Hemophagocytic lymphohistiocytosis (HLH) is a hyperinflammatory disorde

137 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening conditio

138 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening disorder

139 Primary hemophagocytic lymphohistiocytosis (HLH) is a life-threatening disorder

140 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening hematolo

141 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening hyperinf

142 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening hyperinf

143 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening immunolo

144 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening syndrome

145 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening syndrome

146 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening syndrome

147 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening syndrome

148 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening systemic

149 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening, heterog

150 Hemophagocytic lymphohistiocytosis (HLH) is a potentially fatal cytokin

151 Hemophagocytic lymphohistiocytosis (HLH) is a rare disorder of immune d

152 Hemophagocytic lymphohistiocytosis (HLH) is a rare disorder with famili

153 Hemophagocytic lymphohistiocytosis (HLH) is a rare inflammatory disorde

154 Hemophagocytic lymphohistiocytosis (HLH) is a rare life-threatening dis

155 Familial hemophagocytic lymphohistiocytosis (HLH) is a rare primary immunodefici

156 Hemophagocytic lymphohistiocytosis (HLH) is a rare syndrome of uncontro

157 Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening di

158 Adult-onset hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening di

159 Hemophagocytic lymphohistiocytosis (HLH) is a severe inflammatory condi

160 Hemophagocytic lymphohistiocytosis (HLH) is a syndrome describing patie

161 Hemophagocytic lymphohistiocytosis (HLH) is a syndrome of hyperinflamma

162 Hemophagocytic lymphohistiocytosis (HLH) is a syndrome of pathologic im

163 Hemophagocytic lymphohistiocytosis (HLH) is a systemic hyperinflammator

164 Hemophagocytic lymphohistiocytosis (HLH) is an immune dysregulatory syn

165 Hemophagocytic lymphohistiocytosis (HLH) is an inborn disorder of immun

166 Hemophagocytic lymphohistiocytosis (HLH) is an inflammatory disorder in

167 Haemophagocytic lymphohistiocytosis (HLH) is an inflammatory syndrome th

168 Hemophagocytic lymphohistiocytosis (HLH) is an interferon-gamma-driven

169 Hemophagocytic lymphohistiocytosis (HLH) is an often-fatal disorder cha

170 Hemophagocytic lymphohistiocytosis (HLH) is characterized by hyperinfla

171 Hemophagocytic lymphohistiocytosis (HLH) is characterized by immune dys

172 forms from secondary forms of hemophagocytic lymphohistiocytosis (HLH) is crucial for treatment decis

173 T-cell toxicities resembling hemophagocytic lymphohistiocytosis (HLH) occur in a subset of patients

174 Frequently fatal, primary hemophagocytic lymphohistiocytosis (HLH) occurs in infancy resulting fr

175 mmatory toxicities resembling hemophagocytic lymphohistiocytosis (HLH) or macrophage activation syndr

176 x virus (HSV)-1 infection and hemophagocytic lymphohistiocytosis (HLH) postpartum, and a fatal course

177 consequences, including fatal hemophagocytic lymphohistiocytosis (HLH) triggered predominantly by Eps

178 the outcomes of patients with hemophagocytic lymphohistiocytosis (HLH) undergoing allogeneic hematopo

179 Hemophagocytic lymphohistiocytosis (HLH) was only observed in SPTCL cas

180 d adult patients with primary hemophagocytic lymphohistiocytosis (HLH) with refractory, recurrent, or

181 Hemophagocytic lymphohistiocytosis (HLH), a disease often associated wi

182 ering signals can precipitate hemophagocytic lymphohistiocytosis (HLH), a life-threatening systemic i

183 with parallels proposed with hemophagocytic lymphohistiocytosis (HLH), a life-threating condition as

184 okine storm syndromes such as hemophagocytic lymphohistiocytosis (HLH), Adult-onset Still's disease (

185 and cytopenias are present in hemophagocytic lymphohistiocytosis (HLH), and somatic mutations in hema

186 AS bears strong similarity to hemophagocytic lymphohistiocytosis (HLH), and some authors prefer the t

187 xolitinib in murine models of hemophagocytic lymphohistiocytosis (HLH), and the HLH-sibling macrophag

188 m syndromes (CSSs), including hemophagocytic lymphohistiocytosis (HLH), are increasingly recognized a

189 develop clinical features of hemophagocytic lymphohistiocytosis (HLH), but do so when infected with

190 scribed in some patients with hemophagocytic lymphohistiocytosis (HLH), but the role of perforin defe

191 e-threatening immune disorder hemophagocytic lymphohistiocytosis (HLH), characterized by uncontrolled

192 nt with recurrent episodes of hemophagocytic lymphohistiocytosis (HLH), though the exact mechanisms l

193 It is clinically similar to hemophagocytic lymphohistiocytosis (HLH), which is caused by viral infe

194 mmune regulation and underlie hemophagocytic lymphohistiocytosis (HLH), which requires hematopoietic

195 racterize 2 novel monoallelic hemophagocytic lymphohistiocytosis (HLH)-associated mutations affecting

196 and functional data from our hemophagocytic lymphohistiocytosis (HLH)-network registry with UK Bioba

197 xicity predispose patients to hemophagocytic lymphohistiocytosis (HLH).

198 iTE antibodies and leading to hemophagocytic lymphohistiocytosis (HLH).

199 r earlier reports of familial hemophagocytic lymphohistiocytosis (HLH).

200 inflammatory disorder called hemophagocytic lymphohistiocytosis (HLH).

201 ns of hemophagocytic syndrome/hemophagocytic lymphohistiocytosis (HLH).

202 nflammatory syndromes such as hemophagocytic lymphohistiocytosis (HLH).

203 ritinemic inflammation termed hemophagocytic lymphohistiocytosis (HLH).

204 pping clinical phenotype with hemophagocytic lymphohistiocytosis (HLH).

205 tein abrogation presents with hemophagocytic lymphohistiocytosis (HLH).

206 ferative disorders, including hemophagocytic lymphohistiocytosis (HLH).

207 can have features of reactive hemophagocytic lymphohistiocytosis (HLH).

208 tors to the severity of adult hemophagocytic lymphohistiocytosis (HLHa) remains unclear.

209 ble in patients with acquired hemophagocytic lymphohistiocytosis (i.e., secondary hemophagocytic lymp

210 in the treatment of primary haemophagocytic lymphohistiocytosis in clinical trials and initial promi

211 ne severity of illness versus hemophagocytic lymphohistiocytosis in higher baseline severity of illne

212 bute to improved diagnosis of hemophagocytic lymphohistiocytosis in ICU.

213 l treatment for patients with hemophagocytic lymphohistiocytosis in ICUs, including the use of novel

214 nd treatment of patients with hemophagocytic lymphohistiocytosis in ICUs.

215 mg/kg cohort and one case of haemophagocytic lymphohistiocytosis in the 3.4 mg/kg cohort).

216 Mortality of hemophagocytic lymphohistiocytosis in the ICU is high.

217 of the underlying triggers of hemophagocytic lymphohistiocytosis, including infections, malignancies,

218 n various forms of secondary haemophagocytic lymphohistiocytosis, including macrophage activation syn

219 , various forms of secondary haemophagocytic lymphohistiocytosis, including macrophage activation syn

220 ence of reversible AKI due to hemophagocytic lymphohistiocytosis-induced activated macrophage infiltr

221 , including severe cases like hemophagocytic lymphohistiocytosis (irHLH), and to distinguish these fr

222 he better understood familial hemophagocytic lymphohistiocytosis is a constellation of rare, autosoma

223 Hemophagocytic lymphohistiocytosis is a cytokine release syndrome cause

224 Hemophagocytic lymphohistiocytosis is a cytokine-driven inflammatory sy

225 Hemophagocytic lymphohistiocytosis is a disease of abnormally activated

226 Hemophagocytic lymphohistiocytosis is a hyperinflammatory disorder resu

227 Hemophagocytic lymphohistiocytosis is a hyperinflammatory syndrome that

228 Hemophagocytic lymphohistiocytosis is a life-threatening disorder chara

229 Familial hemophagocytic lymphohistiocytosis is a life-threatening hyperinflammat

230 Primary hemophagocytic lymphohistiocytosis is a rare syndrome characterized by

231 By contrast, haemophagocytic lymphohistiocytosis is associated with macrophage activa

232 The hemophagocytic lymphohistiocytosis is probably underdiagnosed in the IC

233 ion, fulfilling criteria for haemophagocytic lymphohistiocytosis, is an emerging phenotype accompanyi

234 tion, fulfilling criteria for hemophagocytic lymphohistiocytosis, is an emerging phenotype accompanyi

235 ed inflammatory episodes with hemophagocytic lymphohistiocytosis-like disease, early-onset seizures,

236 Hemophagocytic lymphohistiocytosis-like manifestations were seen in 19/

237 une effector cell-associated haemophagocytic lymphohistiocytosis-like syndrome (IEC-HS), as well as t

238 mune effector cell-associated hemophagocytic lymphohistiocytosis-like syndrome may occur.

239 mune effector cell-associated hemophagocytic lymphohistiocytosis-like syndrome was observed.

240 une effector cell-associated haemophagocytic lymphohistiocytosis-like syndrome.

241 tal infectious mononucleosis, hemophagocytic lymphohistiocytosis, lymphoproliferative disease, and/or

242 ant infectious mononucleosis, hemophagocytic lymphohistiocytosis, lymphoproliferative disease, organo

243 nd neurologic dysfunction, or hemophagocytic lymphohistiocytosis-macrophage-activation syndrome.

244 m several diseases, including hemophagocytic lymphohistiocytosis/macrophage activation syndrome, seve

245 aluated malignancy-associated hemophagocytic lymphohistiocytosis (mal-HLH) in Sweden regarding popula

246 malignant neoplasm-associated hemophagocytic lymphohistiocytosis (MN-HLH), cytokine release syndrome

247 ral nervous system-restricted hemophagocytic lymphohistiocytosis (n = 3), anti-GABA(A) receptor encep

248 ic infection (n=1 [3%]), and haemophagocytic lymphohistiocytosis (n=1 [3%]).

249 It does not cover EBV and hemophagocytic lymphohistiocytosis nor lymphomagenesis related to EBV.

250 c, and neurologic toxicities, hemophagocytic lymphohistiocytosis, opportunistic infections, and endoc

251 s of immunity (i.e., familial hemophagocytic lymphohistiocytosis) or develop as a complication of inf

252 ers such as leukodystrophies, hemophagocytic lymphohistiocytosis, or genetic vasculopathies can mimic

253 toinflammation, and recurrent hemophagocytic lymphohistiocytosis, p.C188Y and p.*192Cext*24 promoted

254 argely considered a driver of hemophagocytic lymphohistiocytosis pathology, IFN-gamma neutralization

255 nt tailored to critically ill hemophagocytic lymphohistiocytosis patients are highly warranted.

256 rritin levels were highest in hemophagocytic lymphohistiocytosis patients compared with all other dis

257 imately one third of familial hemophagocytic lymphohistiocytosis patients, these immunologic abnormal

258 ality in critically ill adult hemophagocytic lymphohistiocytosis patients.

259 t ferritin levels observed in hemophagocytic lymphohistiocytosis patients.

260 asma cell hepatitis, familial hemophagocytic lymphohistiocytosis, pediatric nonalcoholic fatty liver

261 ficiency that overshadows the hemophagocytic lymphohistiocytosis phenotype.

262 Primary hemophagocytic lymphohistiocytosis (pHLH) is a life-threatening hyperin

263 curative treatment in primary hemophagocytic lymphohistiocytosis (pHLH).

264 al-IRIS overlaps with primary hemophagocytic lymphohistiocytosis (pHLH).

265 In familial hemophagocytic lymphohistiocytosis, Prf-deficient infants suffer a fata

266 dult patients with secondary haemophagocytic lymphohistiocytosis remains suboptimal, and novel therap

267 cytokine release syndrome and hemophagocytic lymphohistiocytosis, represented only a minority of nonr

268 a and severe autoinflammation/hemophagocytic lymphohistiocytosis requiring emapalumab and bone marrow

269 crophage activation syndrome (hemophagocytic lymphohistiocytosis secondary to autoimmune/autoinflamma

270 ritin levels in patients with hemophagocytic lymphohistiocytosis, sepsis, septic shock, and other con

271 atients were categorized into hemophagocytic lymphohistiocytosis, sepsis, septic shock, and other dia

272 included in a postinfectious hemophagocytic lymphohistiocytosis setting.

273 Secondary hemophagocytic lymphohistiocytosis (sHLH) is a highly mortal complicati

274 Secondary hemophagocytic lymphohistiocytosis (sHLH) is a potentially fatal hyperi

275 A hallmark of secondary hemophagocytic lymphohistiocytosis (sHLH), a severe form of cytokine st

276 ymphoproliferative disorders, hemophagocytic lymphohistiocytosis, solid tumors, and other diseases.

277 phage activation syndrome and hemophagocytic lymphohistiocytosis still remain to be determined.

278 acrophage activation syndrome/hemophagocytic lymphohistiocytosis, such as interleukin (IL)-10 and IL-

279 laboratory manifestations of hemophagocytic lymphohistiocytosis syndrome (HLS), also known as macrop

280 sms, possibly integrated into hemophagocytic lymphohistiocytosis syndrome, of infectious origin in th

281 ll dysfunction leading to the hemophagocytic lymphohistiocytosis syndromes.

282 um of diseases, from familial hemophagocytic lymphohistiocytosis to an increased risk of tumorigenesi

283 We investigated familial hemophagocytic lymphohistiocytosis type 2 (FHL2), caused by PRF1 varian

284 are associated with familial hemophagocytic lymphohistiocytosis type 3 (FHL3).

285 mutation of which in familial hemophagocytic lymphohistiocytosis type 3 results in a profound defect

286 escribe a child with familial hemophagocytic lymphohistiocytosis type 3 who developed AKI requiring p

287 man immunodeficiency familial hemophagocytic lymphohistiocytosis type 3.

288 exocytosis, causing familial hemophagocytic lymphohistiocytosis type 4 (FHL-4).

289 e strains and from a Familial Hemophagocytic Lymphohistiocytosis type 4 (FHL4) patient.

290 1 deficiency develop familial hemophagocytic lymphohistiocytosis type 4 (FHL4), a life-threatening di

291 Familial hemophagocytic lymphohistiocytosis type 5 (FHL5) is caused by defects i

292 sis of patients with familial hemophagocytic lymphohistiocytosis type 5 has identified the E132A muta

293 regulation disorder, familial hemophagocytic lymphohistiocytosis (type 2 FHL, FHL2).

294 eating children with familial hemophagocytic lymphohistiocytosis using reduced intensity conditioning

295 ry diseases, such as primary haemophagocytic lymphohistiocytosis, various forms of secondary haemopha

296 e have been found in familial hemophagocytic lymphohistiocytosis, which shares some features with CAE

297 A liver biopsy showed hemophagocytic lymphohistiocytosis with exuberant infiltrates of CD8+ T

298 istiocytosis (i.e., secondary hemophagocytic lymphohistiocytosis) without previous therapy, including