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1 romes (e.g., flecainide in catecholaminergic polymorphic ventricular tachycardia).
2 rhythmia and sudden death (catecholaminergic polymorphic ventricular tachycardia).
3 mphetamine, marijuana, and catecholaminergic polymorphic ventricular tachycardia.
4 in an established model of catecholaminergic polymorphic ventricular tachycardia.
5 tically modified mice with catecholaminergic polymorphic ventricular tachycardia.
6 ome, Brugada syndrome, and catecholaminergic polymorphic ventricular tachycardia.
7 n CASQ2 has been linked to catecholaminergic polymorphic ventricular tachycardia.
8 te as [corrected] "shifting" foci resembling polymorphic ventricular tachycardia.
9 ons and extrasystolic Ca2+ waves, leading to polymorphic ventricular tachycardia.
10 dentified in patients with catecholaminergic polymorphic ventricular tachycardia.
11 nged QT intervals, QT interval lability, and polymorphic ventricular tachycardia.
12  variant classification in catecholaminergic polymorphic ventricular tachycardia.
13 ression represent a novel inherited cause of polymorphic ventricular tachycardia.
14 ifth) paper will deal with catecholaminergic polymorphic ventricular tachycardia.
15 nherited disorders such as catecholaminergic polymorphic ventricular tachycardia.
16 und to underlie the mechanism of spontaneous polymorphic ventricular tachycardia.
17 gthy delay to diagnosis in catecholaminergic polymorphic ventricular tachycardia.
18  outcomes in children with catecholaminergic polymorphic ventricular tachycardia.
19 ong-QT syndrome (LQTS) and catecholaminergic polymorphic ventricular tachycardia.
20 tic denervation in LQTS or catecholaminergic polymorphic ventricular tachycardia.
21 , cardiac hypertrophy, and catecholaminergic polymorphic ventricular tachycardia.
22 as the long-QT syndrome or catecholaminergic polymorphic ventricular tachycardia.
23 lve RyRs, such as malignant hyperthermia and polymorphic ventricular tachycardia.
24 iac arrhythmias, including catecholaminergic polymorphic ventricular tachycardia.
25 tricular noncompaction and catecholaminergic polymorphic ventricular tachycardia.
26 rome, Brugada Syndrome, or Catecholaminergic Polymorphic Ventricular Tachycardia.
27 rhythmogenic mechanism for catecholaminergic polymorphic ventricular tachycardia.
28 other raised suspicion for catecholaminergic polymorphic ventricular tachycardia.
29 n that was consistent with catecholaminergic polymorphic ventricular tachycardia.
30 cytes, and correlated with catecholaminergic polymorphic ventricular tachycardia.
31 gaming-associated event (3 catecholaminergic polymorphic ventricular tachycardia, 1 long QT syndrome,
32   Complications other than AV block included polymorphic ventricular tachycardia 10 to 24 h after the
33  syndrome, 3/18 (17%); and catecholaminergic polymorphic ventricular tachycardia, 2/18 (11%).
34 ted patients were sustained and nonsustained polymorphic ventricular tachycardia (3.6%).
35 e, 9; Brugada syndrome, 8; catecholaminergic polymorphic ventricular tachycardia, 3; short QT syndrom
36 ng Long-QT syndrome (13%), catecholaminergic polymorphic ventricular tachycardia (4%), arrhythmogenic
37  disease factors (18; 38%; catecholaminergic polymorphic ventricular tachycardia [6], near-drowning [
38 ts, increased susceptibility to induction of polymorphic ventricular tachycardia (60 vs. 24% in Kcne5
39  noncompaction (7%), and 1 catecholaminergic polymorphic ventricular tachycardia (7%).
40 f-function mutations cause catecholaminergic polymorphic ventricular tachycardia, a condition charact
41  was sufficient to prevent catecholaminergic polymorphic ventricular tachycardia, a congenital source
42 CASQ2) genes are linked to catecholaminergic polymorphic ventricular tachycardia, a life-threatening
43  have been associated with catecholaminergic polymorphic ventricular tachycardia and a form of arrhyt
44 ndrome, short QT syndrome, catecholaminergic polymorphic ventricular tachycardia and Brugada syndrome
45 mural reentry over transmural reentry during polymorphic ventricular tachycardia and fibrillation.
46  cardiac diseases, such as catecholaminergic polymorphic ventricular tachycardia and heart failure (H
47 ird proband diagnosed with catecholaminergic polymorphic ventricular tachycardia and his father with
48 ) in genes associated with catecholaminergic polymorphic ventricular tachycardia and long QT syndrome
49 ed the predominant role of catecholaminergic polymorphic ventricular tachycardia and long QT syndrome
50 tiologies established were catecholaminergic polymorphic ventricular tachycardia and long QT syndrome
51 an in-depth review of the different forms of polymorphic ventricular tachycardia and propose a practi
52 d premature ventricular beats with bursts of polymorphic ventricular tachycardia and then died sudden
53 ontaneous ventricular arrhythmias, including polymorphic ventricular tachycardia and ventricular fibr
54 iac arrest secondary to multiple episodes of polymorphic ventricular tachycardia and ventricular fibr
55 r in which mutation carriers are at risk for polymorphic ventricular tachycardia and/or sudden cardia
56 logists: long QT syndrome, catecholaminergic polymorphic ventricular tachycardia, and Brugada syndrom
57  ventricular fibrillation, catecholaminergic polymorphic ventricular tachycardia, and risk of sudden
58 ome; 4 long-QT syndrome; 1 catecholaminergic polymorphic ventricular tachycardia; and 2 cardiomyopath
59 s with clinically definite catecholaminergic polymorphic ventricular tachycardia are classified ambig
60 ered the treatment of choice for one form of polymorphic ventricular tachycardia, are contraindicated
61 ns in long QT syndrome and catecholaminergic polymorphic ventricular tachycardia-associated genes in
62 o predict pathogenicity of catecholaminergic polymorphic ventricular tachycardia-associated RYR2 VUS
63 roperties of wild-type and catecholaminergic polymorphic ventricular tachycardia-associated RyR2(R449
64       One exception is the catecholaminergic polymorphic ventricular tachycardia-causing N53I substit
65                                            A polymorphic ventricular tachycardia closely resembling T
66 thmia syndromes, including catecholaminergic polymorphic ventricular tachycardia, congenital long QT
67 rome (BrS) (n = 16 [14%]), catecholaminergic polymorphic ventricular tachycardia (CPVT) (n = 9 [8%]),
68 ecently been identified in catecholaminergic polymorphic ventricular tachycardia (CPVT) and arrhythmo
69  mutations associated with catecholaminergic polymorphic ventricular tachycardia (CPVT) and atrial fi
70 ong QT syndrome (LQTS) and catecholaminergic polymorphic ventricular tachycardia (CPVT) and deal spec
71  cause arrhythmias such as catecholaminergic polymorphic ventricular tachycardia (CPVT) and long QT s
72                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) and short QT
73              Patients with catecholaminergic polymorphic ventricular tachycardia (CPVT) are at risk f
74 ong QT syndrome (LQTS) and catecholaminergic polymorphic ventricular tachycardia (CPVT) are electric
75  mutations associated with catecholaminergic polymorphic ventricular tachycardia (CPVT) are postulate
76                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) causes sudden
77 ation R33Q leads to lethal catecholaminergic polymorphic ventricular tachycardia (CPVT) implies a cru
78                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a conditio
79                        Catecholamine-induced polymorphic ventricular tachycardia (CPVT) is a familial
80                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a familial
81                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a genetic
82                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a lethal,
83                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a potentia
84                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a potentia
85                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a potentia
86                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a rare inh
87                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a stress-i
88                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherit
89                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherit
90                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherit
91                            Catecholaminergic polymorphic ventricular tachycardia (CPVT) is caused by
92 efficacy of flecainide for catecholaminergic polymorphic ventricular tachycardia (CPVT) is unclear.
93 rgent clinical features of catecholaminergic polymorphic ventricular tachycardia (CPVT) or long QT sy
94 ong-QT syndrome (LQTS) and catecholaminergic polymorphic ventricular tachycardia (CPVT) represent tre
95 sms of arrhythmogenesis in catecholaminergic polymorphic ventricular tachycardia (CPVT) require spont
96  type 2 knockout) model of catecholaminergic polymorphic ventricular tachycardia (CPVT) was used for
97 gene (RYR2) cause dominant catecholaminergic polymorphic ventricular tachycardia (CPVT), a leading ca
98 utosomal recessive form of catecholaminergic polymorphic ventricular tachycardia (CPVT), although iso
99                            Catecholaminergic polymorphic ventricular tachycardia (CPVT), an inherited
100                         In catecholaminergic polymorphic ventricular tachycardia (CPVT), cardiac Purk
101  These arrhythmias include catecholaminergic polymorphic ventricular tachycardia (CPVT), certain case
102  of concealed LQT1, namely catecholaminergic polymorphic ventricular tachycardia (CPVT), may also und
103 c Ca(2+) release events in catecholaminergic polymorphic ventricular tachycardia (CPVT), yet evidence
104 em cells (hiPSCs) model of catecholaminergic polymorphic ventricular tachycardia (CPVT).
105 at are associated with catecholamine-induced polymorphic ventricular tachycardia (CPVT).
106 e been associated with catecholamine-induced polymorphic ventricular tachycardia (CPVT).
107 T) may distinguish it from catecholaminergic polymorphic ventricular tachycardia (CPVT).
108 sion medicine, we focus on catecholaminergic polymorphic ventricular tachycardia (CPVT).
109 udden cardiac death called catecholaminergic polymorphic ventricular tachycardia (CPVT).
110  sudden death-predisposing catecholaminergic polymorphic ventricular tachycardia (CPVT).
111 ms of long QT syndrome and catecholaminergic polymorphic ventricular tachycardia (CPVT).
112 rial fibrillation (AF) and catecholaminergic polymorphic ventricular tachycardia (CPVT).
113 lethal familial arrhythmia catecholaminergic polymorphic ventricular tachycardia (CPVT).
114 lar tachycardia in humans [catecholaminergic polymorphic ventricular tachycardia (CPVT)].
115  assessed in patients with catecholaminergic polymorphic ventricular tachycardia (CPVT; n=8) and in r
116 hythmias (in patients with catecholaminergic polymorphic ventricular tachycardia [CPVT]) reduced the
117 uced sudden cardiac death (catecholaminergic polymorphic ventricular tachycardia [CPVT]).
118 cise-induced sudden death (catecholaminergic polymorphic ventricular tachycardia [CPVT]).
119 tions in RYR2 cause type 1 catecholaminergic polymorphic ventricular tachycardia (CPVT1), a cardiac c
120 mutations can cause type-1 catecholaminergic polymorphic ventricular tachycardia (CPVT1), a lethal, a
121 olecular mechanism for the catecholaminergic polymorphic ventricular tachycardia (CPVT2) mutation, K2
122    Foremost are those with catecholaminergic polymorphic ventricular tachycardia due to abnormalities
123 tilide-treated patients, 15 (8.3%) developed polymorphic ventricular tachycardia during or soon after
124                         In catecholaminergic polymorphic ventricular tachycardia, excess mortality wa
125 long QT syndrome (1/2) and catecholaminergic polymorphic ventricular tachycardia families (1/2) who w
126 QT prolongation (14%), torsades de pointe or polymorphic ventricular tachycardia/fibrillation (6% [su
127                                     Familial polymorphic ventricular tachycardia (FPVT) is characteri
128  and patients referred for catecholaminergic polymorphic ventricular tachycardia had the highest rate
129 ase dysfunction underlying catecholaminergic polymorphic ventricular tachycardia has only been invest
130 ome, Brugada syndrome, and catecholaminergic polymorphic ventricular tachycardia have been associated
131                             Several types of polymorphic ventricular tachycardia have similar electro
132  1.65, p < 0.0001), ventricular fibrillation/polymorphic ventricular tachycardia (HR: 2.10, p < 0.000
133 to study long QT syndrome, catecholaminergic polymorphic ventricular tachycardia, hypertrophic cardio
134  transmural repolarization in the genesis of polymorphic ventricular tachycardia in a canine model of
135 in leaky channels and cause exercise induced polymorphic ventricular tachycardia in humans [catechola
136                            The initiation of polymorphic ventricular tachycardia in long QT syndrome
137 . high sympathetic tone, are associated with polymorphic ventricular tachycardia in LQTS patients.
138 nts manifest ventricular premature beats and polymorphic ventricular tachycardia in response to exerc
139        Flecainide prevents catecholaminergic polymorphic ventricular tachycardia in RyR2(R4496C+/-) m
140 monstrate that azithromycin can cause rapid, polymorphic ventricular tachycardia in the absence of QT
141                  The potential for producing polymorphic ventricular tachycardia in the rabbit model
142                            Bidirectional and polymorphic ventricular tachycardias in CASQ2 KO mice in
143 rrhythmogenic rat model of catecholaminergic polymorphic ventricular tachycardia, induced by RyR2 gai
144                            Catecholaminergic polymorphic ventricular tachycardia is a form of exercis
145                            Catecholaminergic polymorphic ventricular tachycardia is a heritable arrhy
146                            Catecholaminergic polymorphic ventricular tachycardia is an inherited dise
147                            Catecholaminergic polymorphic ventricular tachycardia is an uncommon, pote
148      The recessive form of catecholaminergic polymorphic ventricular tachycardia is caused by mutatio
149                            Catecholaminergic polymorphic ventricular tachycardia is characterized by
150                            Catecholaminergic polymorphic ventricular tachycardia is directly linked t
151                                     Familial polymorphic ventricular tachycardia is due to a defect i
152 in-2 gene; this variant of catecholaminergic polymorphic ventricular tachycardia is less well charact
153 CASQ2 protein carrying the catecholaminergic polymorphic ventricular tachycardia-linked mutation D307
154 dling in mice carrying the catecholaminergic polymorphic ventricular tachycardia-linked mutation of r
155         We have shown that catecholaminergic polymorphic ventricular tachycardia-linked RyR2 mutation
156 terozygous mice carrying a catecholaminergic polymorphic ventricular tachycardia-linked RyR2 mutation
157              Patients with catecholaminergic polymorphic ventricular tachycardia manifest sinoatrial
158 ogenic mutation, as in the catecholaminergic polymorphic ventricular tachycardia mice studies, or mor
159 ythmias in CASQ2-defective catecholaminergic polymorphic ventricular tachycardia mice.
160 previously identified in a catecholaminergic polymorphic ventricular tachycardia model.
161 ic contractions (DCs) in a catecholaminergic polymorphic ventricular tachycardia mouse model with a m
162 dria structural defects in catecholaminergic polymorphic ventricular tachycardia myocytes and reduced
163 oxygen species emission in catecholaminergic polymorphic ventricular tachycardia myocytes.
164 ), supraventricular tachycardia (n = 1), and polymorphic ventricular tachycardia (n = 1).
165 thmogenic disease included catecholaminergic polymorphic ventricular tachycardia (n=13), Jervell and
166 ients with LQTS (N=40) and catecholaminergic polymorphic ventricular tachycardia (N=7) underwent vide
167                                    Sustained polymorphic ventricular tachycardia occurred in 2 of the
168 polarization that could potentially initiate polymorphic ventricular tachycardia or fibrillation.
169 iac arrhythmias, including catecholaminergic polymorphic ventricular tachycardia or long QT syndrome
170 forms of long QT syndrome, catecholaminergic polymorphic ventricular tachycardia, or idiopathic ventr
171 entricular tachycardia, ventricular flutter, polymorphic ventricular tachycardia, or ventricular fibr
172 us to what was observed in catecholaminergic polymorphic ventricular tachycardia patients after exerc
173 rospective cohort study of catecholaminergic polymorphic ventricular tachycardia patients diagnosed b
174  to the SAN dysfunction in catecholaminergic polymorphic ventricular tachycardia patients.
175  model systems exhibited a catecholaminergic polymorphic ventricular tachycardia phenotype.
176                                              Polymorphic ventricular tachycardia (PMVT) has been repo
177 ation play a critical role in the genesis of polymorphic ventricular tachycardia (PVT) when QT interv
178 monomorphic ventricular tachycardia (MVT) or polymorphic ventricular tachycardia (PVT)/ventricular fi
179 sed by early afterdepolarizations (EADs) and polymorphic ventricular tachycardias (PVTs).
180  with long QT syndrome and catecholaminergic polymorphic ventricular tachycardia received routine bet
181 nd to be a protocol violation, had sustained polymorphic ventricular tachycardia requiring direct cur
182 NQ1, KCNH2, and SCN5A) and catecholaminergic polymorphic ventricular tachycardia-susceptibility gene
183  and long QT, Brugada, and catecholaminergic polymorphic ventricular tachycardia syndromes) should al
184 ase, such as hypertension, catecholaminergic polymorphic ventricular tachycardia, takotsubo cardiomyo
185 gment elevation in V1 through V3 and a rapid polymorphic ventricular tachycardia that can degenerate
186 diac death cases linked to catecholaminergic polymorphic ventricular tachycardia that feature lethal
187 tions in 2 genes linked to catecholaminergic polymorphic ventricular tachycardia, the first located i
188 rval prolongation, and the potentially fatal polymorphic ventricular tachycardia torsade de pointes,
189 tening cardiac arrhythmias, specifically the polymorphic ventricular tachycardia torsades de pointes.
190 ion of the cardiac action potential leads to polymorphic ventricular tachycardia (torsades de pointes
191 rdiogram and the morphologically distinctive polymorphic ventricular tachycardia ('torsades de pointe
192                            Catecholaminergic polymorphic ventricular tachycardia type 1 (CPVT1) is a
193                            Catecholaminergic polymorphic ventricular tachycardia type 2 (CPVT2) resul
194 ale and 1 of 2 female preparations developed polymorphic ventricular tachycardia/ventricular fibrilla
195 enting with malignant syncope and documented polymorphic ventricular tachycardia/ventricular fibrilla
196 tachycardia, n = 44; pause/asystole, n = 36; polymorphic ventricular tachycardia/ventricular fibrilla
197 function and an increased incidence of rapid polymorphic ventricular tachycardia (VT) and sudden card
198 rapy for the management of catecholaminergic polymorphic ventricular tachycardia (VT) in young patien
199                            Catecholaminergic polymorphic ventricular tachycardia (VT) is a lethal fam
200                                              Polymorphic ventricular tachycardia (VT) is rare and gen
201                                              Polymorphic ventricular tachycardia (VT) without QT prol
202 yndrome, Brugada syndrome, catecholaminergic polymorphic ventricular tachycardia (VT), and short QT s
203 %) died suddenly, one with Holter-documented polymorphic ventricular tachycardia (VT).
204 uding long-QT syndrome and catecholaminergic polymorphic ventricular tachycardia (VT).
205 st clinical probability of catecholaminergic polymorphic ventricular tachycardia was determined for a
206  specific genetic test for catecholaminergic polymorphic ventricular tachycardia was sent.
207                                              Polymorphic ventricular tachycardia was the most serious
208                  All patients with sustained polymorphic ventricular tachycardia were successfully tr
209 icular cardiomyopathy, and catecholaminergic polymorphic ventricular tachycardia were the most common
210          Spontaneous and stimulation-induced polymorphic ventricular tachycardia with characteristics
211 genetic arrhythmia syndrome characterized by polymorphic ventricular tachycardia with physical or emo
212 n, and demonstrated facilitated induction of polymorphic ventricular tachycardia, without antecedent

 
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