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1 romes (e.g., flecainide in catecholaminergic polymorphic ventricular tachycardia).
2 rhythmia and sudden death (catecholaminergic polymorphic ventricular tachycardia).
3 mphetamine, marijuana, and catecholaminergic polymorphic ventricular tachycardia.
4 in an established model of catecholaminergic polymorphic ventricular tachycardia.
5 tically modified mice with catecholaminergic polymorphic ventricular tachycardia.
6 ome, Brugada syndrome, and catecholaminergic polymorphic ventricular tachycardia.
7 n CASQ2 has been linked to catecholaminergic polymorphic ventricular tachycardia.
8 te as [corrected] "shifting" foci resembling polymorphic ventricular tachycardia.
9 ons and extrasystolic Ca2+ waves, leading to polymorphic ventricular tachycardia.
10 dentified in patients with catecholaminergic polymorphic ventricular tachycardia.
11 nged QT intervals, QT interval lability, and polymorphic ventricular tachycardia.
12 variant classification in catecholaminergic polymorphic ventricular tachycardia.
13 ression represent a novel inherited cause of polymorphic ventricular tachycardia.
14 ifth) paper will deal with catecholaminergic polymorphic ventricular tachycardia.
15 nherited disorders such as catecholaminergic polymorphic ventricular tachycardia.
16 und to underlie the mechanism of spontaneous polymorphic ventricular tachycardia.
17 gthy delay to diagnosis in catecholaminergic polymorphic ventricular tachycardia.
18 outcomes in children with catecholaminergic polymorphic ventricular tachycardia.
19 ong-QT syndrome (LQTS) and catecholaminergic polymorphic ventricular tachycardia.
20 tic denervation in LQTS or catecholaminergic polymorphic ventricular tachycardia.
21 , cardiac hypertrophy, and catecholaminergic polymorphic ventricular tachycardia.
22 as the long-QT syndrome or catecholaminergic polymorphic ventricular tachycardia.
23 lve RyRs, such as malignant hyperthermia and polymorphic ventricular tachycardia.
24 iac arrhythmias, including catecholaminergic polymorphic ventricular tachycardia.
25 tricular noncompaction and catecholaminergic polymorphic ventricular tachycardia.
26 rome, Brugada Syndrome, or Catecholaminergic Polymorphic Ventricular Tachycardia.
27 rhythmogenic mechanism for catecholaminergic polymorphic ventricular tachycardia.
28 other raised suspicion for catecholaminergic polymorphic ventricular tachycardia.
29 n that was consistent with catecholaminergic polymorphic ventricular tachycardia.
30 cytes, and correlated with catecholaminergic polymorphic ventricular tachycardia.
31 gaming-associated event (3 catecholaminergic polymorphic ventricular tachycardia, 1 long QT syndrome,
32 Complications other than AV block included polymorphic ventricular tachycardia 10 to 24 h after the
35 e, 9; Brugada syndrome, 8; catecholaminergic polymorphic ventricular tachycardia, 3; short QT syndrom
36 ng Long-QT syndrome (13%), catecholaminergic polymorphic ventricular tachycardia (4%), arrhythmogenic
37 disease factors (18; 38%; catecholaminergic polymorphic ventricular tachycardia [6], near-drowning [
38 ts, increased susceptibility to induction of polymorphic ventricular tachycardia (60 vs. 24% in Kcne5
40 f-function mutations cause catecholaminergic polymorphic ventricular tachycardia, a condition charact
41 was sufficient to prevent catecholaminergic polymorphic ventricular tachycardia, a congenital source
42 CASQ2) genes are linked to catecholaminergic polymorphic ventricular tachycardia, a life-threatening
43 have been associated with catecholaminergic polymorphic ventricular tachycardia and a form of arrhyt
44 ndrome, short QT syndrome, catecholaminergic polymorphic ventricular tachycardia and Brugada syndrome
45 mural reentry over transmural reentry during polymorphic ventricular tachycardia and fibrillation.
46 cardiac diseases, such as catecholaminergic polymorphic ventricular tachycardia and heart failure (H
47 ird proband diagnosed with catecholaminergic polymorphic ventricular tachycardia and his father with
48 ) in genes associated with catecholaminergic polymorphic ventricular tachycardia and long QT syndrome
49 ed the predominant role of catecholaminergic polymorphic ventricular tachycardia and long QT syndrome
50 tiologies established were catecholaminergic polymorphic ventricular tachycardia and long QT syndrome
51 an in-depth review of the different forms of polymorphic ventricular tachycardia and propose a practi
52 d premature ventricular beats with bursts of polymorphic ventricular tachycardia and then died sudden
53 ontaneous ventricular arrhythmias, including polymorphic ventricular tachycardia and ventricular fibr
54 iac arrest secondary to multiple episodes of polymorphic ventricular tachycardia and ventricular fibr
55 r in which mutation carriers are at risk for polymorphic ventricular tachycardia and/or sudden cardia
56 logists: long QT syndrome, catecholaminergic polymorphic ventricular tachycardia, and Brugada syndrom
57 ventricular fibrillation, catecholaminergic polymorphic ventricular tachycardia, and risk of sudden
58 ome; 4 long-QT syndrome; 1 catecholaminergic polymorphic ventricular tachycardia; and 2 cardiomyopath
59 s with clinically definite catecholaminergic polymorphic ventricular tachycardia are classified ambig
60 ered the treatment of choice for one form of polymorphic ventricular tachycardia, are contraindicated
61 ns in long QT syndrome and catecholaminergic polymorphic ventricular tachycardia-associated genes in
62 o predict pathogenicity of catecholaminergic polymorphic ventricular tachycardia-associated RYR2 VUS
63 roperties of wild-type and catecholaminergic polymorphic ventricular tachycardia-associated RyR2(R449
66 thmia syndromes, including catecholaminergic polymorphic ventricular tachycardia, congenital long QT
67 rome (BrS) (n = 16 [14%]), catecholaminergic polymorphic ventricular tachycardia (CPVT) (n = 9 [8%]),
68 ecently been identified in catecholaminergic polymorphic ventricular tachycardia (CPVT) and arrhythmo
69 mutations associated with catecholaminergic polymorphic ventricular tachycardia (CPVT) and atrial fi
70 ong QT syndrome (LQTS) and catecholaminergic polymorphic ventricular tachycardia (CPVT) and deal spec
71 cause arrhythmias such as catecholaminergic polymorphic ventricular tachycardia (CPVT) and long QT s
74 ong QT syndrome (LQTS) and catecholaminergic polymorphic ventricular tachycardia (CPVT) are electric
75 mutations associated with catecholaminergic polymorphic ventricular tachycardia (CPVT) are postulate
77 ation R33Q leads to lethal catecholaminergic polymorphic ventricular tachycardia (CPVT) implies a cru
92 efficacy of flecainide for catecholaminergic polymorphic ventricular tachycardia (CPVT) is unclear.
93 rgent clinical features of catecholaminergic polymorphic ventricular tachycardia (CPVT) or long QT sy
94 ong-QT syndrome (LQTS) and catecholaminergic polymorphic ventricular tachycardia (CPVT) represent tre
95 sms of arrhythmogenesis in catecholaminergic polymorphic ventricular tachycardia (CPVT) require spont
96 type 2 knockout) model of catecholaminergic polymorphic ventricular tachycardia (CPVT) was used for
97 gene (RYR2) cause dominant catecholaminergic polymorphic ventricular tachycardia (CPVT), a leading ca
98 utosomal recessive form of catecholaminergic polymorphic ventricular tachycardia (CPVT), although iso
101 These arrhythmias include catecholaminergic polymorphic ventricular tachycardia (CPVT), certain case
102 of concealed LQT1, namely catecholaminergic polymorphic ventricular tachycardia (CPVT), may also und
103 c Ca(2+) release events in catecholaminergic polymorphic ventricular tachycardia (CPVT), yet evidence
115 assessed in patients with catecholaminergic polymorphic ventricular tachycardia (CPVT; n=8) and in r
116 hythmias (in patients with catecholaminergic polymorphic ventricular tachycardia [CPVT]) reduced the
119 tions in RYR2 cause type 1 catecholaminergic polymorphic ventricular tachycardia (CPVT1), a cardiac c
120 mutations can cause type-1 catecholaminergic polymorphic ventricular tachycardia (CPVT1), a lethal, a
121 olecular mechanism for the catecholaminergic polymorphic ventricular tachycardia (CPVT2) mutation, K2
122 Foremost are those with catecholaminergic polymorphic ventricular tachycardia due to abnormalities
123 tilide-treated patients, 15 (8.3%) developed polymorphic ventricular tachycardia during or soon after
125 long QT syndrome (1/2) and catecholaminergic polymorphic ventricular tachycardia families (1/2) who w
126 QT prolongation (14%), torsades de pointe or polymorphic ventricular tachycardia/fibrillation (6% [su
128 and patients referred for catecholaminergic polymorphic ventricular tachycardia had the highest rate
129 ase dysfunction underlying catecholaminergic polymorphic ventricular tachycardia has only been invest
130 ome, Brugada syndrome, and catecholaminergic polymorphic ventricular tachycardia have been associated
132 1.65, p < 0.0001), ventricular fibrillation/polymorphic ventricular tachycardia (HR: 2.10, p < 0.000
133 to study long QT syndrome, catecholaminergic polymorphic ventricular tachycardia, hypertrophic cardio
134 transmural repolarization in the genesis of polymorphic ventricular tachycardia in a canine model of
135 in leaky channels and cause exercise induced polymorphic ventricular tachycardia in humans [catechola
137 . high sympathetic tone, are associated with polymorphic ventricular tachycardia in LQTS patients.
138 nts manifest ventricular premature beats and polymorphic ventricular tachycardia in response to exerc
140 monstrate that azithromycin can cause rapid, polymorphic ventricular tachycardia in the absence of QT
143 rrhythmogenic rat model of catecholaminergic polymorphic ventricular tachycardia, induced by RyR2 gai
148 The recessive form of catecholaminergic polymorphic ventricular tachycardia is caused by mutatio
152 in-2 gene; this variant of catecholaminergic polymorphic ventricular tachycardia is less well charact
153 CASQ2 protein carrying the catecholaminergic polymorphic ventricular tachycardia-linked mutation D307
154 dling in mice carrying the catecholaminergic polymorphic ventricular tachycardia-linked mutation of r
156 terozygous mice carrying a catecholaminergic polymorphic ventricular tachycardia-linked RyR2 mutation
158 ogenic mutation, as in the catecholaminergic polymorphic ventricular tachycardia mice studies, or mor
161 ic contractions (DCs) in a catecholaminergic polymorphic ventricular tachycardia mouse model with a m
162 dria structural defects in catecholaminergic polymorphic ventricular tachycardia myocytes and reduced
165 thmogenic disease included catecholaminergic polymorphic ventricular tachycardia (n=13), Jervell and
166 ients with LQTS (N=40) and catecholaminergic polymorphic ventricular tachycardia (N=7) underwent vide
168 polarization that could potentially initiate polymorphic ventricular tachycardia or fibrillation.
169 iac arrhythmias, including catecholaminergic polymorphic ventricular tachycardia or long QT syndrome
170 forms of long QT syndrome, catecholaminergic polymorphic ventricular tachycardia, or idiopathic ventr
171 entricular tachycardia, ventricular flutter, polymorphic ventricular tachycardia, or ventricular fibr
172 us to what was observed in catecholaminergic polymorphic ventricular tachycardia patients after exerc
173 rospective cohort study of catecholaminergic polymorphic ventricular tachycardia patients diagnosed b
177 ation play a critical role in the genesis of polymorphic ventricular tachycardia (PVT) when QT interv
178 monomorphic ventricular tachycardia (MVT) or polymorphic ventricular tachycardia (PVT)/ventricular fi
180 with long QT syndrome and catecholaminergic polymorphic ventricular tachycardia received routine bet
181 nd to be a protocol violation, had sustained polymorphic ventricular tachycardia requiring direct cur
182 NQ1, KCNH2, and SCN5A) and catecholaminergic polymorphic ventricular tachycardia-susceptibility gene
183 and long QT, Brugada, and catecholaminergic polymorphic ventricular tachycardia syndromes) should al
184 ase, such as hypertension, catecholaminergic polymorphic ventricular tachycardia, takotsubo cardiomyo
185 gment elevation in V1 through V3 and a rapid polymorphic ventricular tachycardia that can degenerate
186 diac death cases linked to catecholaminergic polymorphic ventricular tachycardia that feature lethal
187 tions in 2 genes linked to catecholaminergic polymorphic ventricular tachycardia, the first located i
188 rval prolongation, and the potentially fatal polymorphic ventricular tachycardia torsade de pointes,
189 tening cardiac arrhythmias, specifically the polymorphic ventricular tachycardia torsades de pointes.
190 ion of the cardiac action potential leads to polymorphic ventricular tachycardia (torsades de pointes
191 rdiogram and the morphologically distinctive polymorphic ventricular tachycardia ('torsades de pointe
194 ale and 1 of 2 female preparations developed polymorphic ventricular tachycardia/ventricular fibrilla
195 enting with malignant syncope and documented polymorphic ventricular tachycardia/ventricular fibrilla
196 tachycardia, n = 44; pause/asystole, n = 36; polymorphic ventricular tachycardia/ventricular fibrilla
197 function and an increased incidence of rapid polymorphic ventricular tachycardia (VT) and sudden card
198 rapy for the management of catecholaminergic polymorphic ventricular tachycardia (VT) in young patien
202 yndrome, Brugada syndrome, catecholaminergic polymorphic ventricular tachycardia (VT), and short QT s
205 st clinical probability of catecholaminergic polymorphic ventricular tachycardia was determined for a
209 icular cardiomyopathy, and catecholaminergic polymorphic ventricular tachycardia were the most common
211 genetic arrhythmia syndrome characterized by polymorphic ventricular tachycardia with physical or emo
212 n, and demonstrated facilitated induction of polymorphic ventricular tachycardia, without antecedent