ライフサイエンスコーパス: pulmonary atresia

1 ogenitors, and embryos predominantly develop pulmonary atresia.

2 r airway was not sufficient for diagnosis of pulmonary atresia.

3 onduit replacement in patients with TOF with pulmonary atresia.

4 lving pulmonary valves or arteries or due to pulmonary atresia.

5 nging from mild pulmonary stenosis to severe pulmonary atresia.

6 diac diagnoses were Ebstein's anomaly (40%), pulmonary atresia (11%), and tetralogy of Fallot (8%).

7 Among TOF, 35 (9%) had pulmonary atresia, 98 (26%) had a palliative procedure b

8 patients with cases of TOF, including 3 with pulmonary atresia and 5 with right aortic arch; none had

9 d with the Fontan procedure in patients with pulmonary atresia and an intact ventricular septum and t

10 that occurs in response to Shh knockdown is pulmonary atresia and is directly related to the abnorma

11 on can be performed in >90% of patients with pulmonary atresia and MAPCAs, even those with absent tru

12 It was associated with pulmonary atresia and moderate or severe aortic regurgit

13 rome suffering from tetralogy of Fallot with pulmonary atresia and multiple aortopulmonary collateral

14 Four patients had tetralogy of Fallot, 1 had pulmonary atresia, and 1 had rheumatic valve disease.

15 ypoplastic left heart (HLH) syndrome, 10 had pulmonary atresia, and 1 had tricuspid atresia.

16 patients (48%) with tetralogy of Fallot and pulmonary atresia, and 4 of 54 (8%) with prosthetic valv

17 TOF with pulmonary stenosis, 24 had TOF with pulmonary atresia, and 6 had TOF with nonconfluent pulmo

18 Male sex, pulmonary atresia, and previous palliations emerged as p

19 applications include traversing occlusions (pulmonary atresia, arterial and venous occlusion, and ia

20 In hearts with pulmonary atresia, cardiac neural crest-derived cells, w

21 n=44), primary repair (aged <3 months) with pulmonary atresia (early-PA group; n=49), and primary re

22 Preoperative hemodynamics and overall pulmonary atresia growth were similar, although right pu

23 Both groups demonstrated good pulmonary atresia growth.

24 onary trunk formation, and that embryos with pulmonary atresia have an outflow tract septum.

25 phenotypic mimic of Tetralogy of Fallot with pulmonary atresia; however, subsequent reports describe

26 resent in 23 subjects and was accompanied by pulmonary atresia in 8.

27 .1% (95% confidence interval, 49.9 to 61.7); pulmonary atresia intact ventricular septum, 55.7% (95%

28 tients with hypoplastic left heart syndrome, pulmonary atresia intact ventricular septum, single vent

29 noses included pulmonary stenosis (n = 433), pulmonary atresia (n = 121), common atrioventricular can

30 rtery stenosis (n = 94), tetralogy of Fallot/pulmonary atresia (n = 72), congenital branch pulmonary

31 oses included tetralogy of Fallot (TOF) with pulmonary atresia (n=13), TOF with pulmonary stenosis (n

32 tresia (n=103), tetralogy of Fallot (n=127), pulmonary atresia (n=177), heterotaxy syndrome (n=38), a

33 strategy for the management of patients with pulmonary atresia or severe stenosis and major aortopulm

34 ent prior surgery, outcomes of patients with pulmonary atresia or stenosis and MAPCAs have continued

35 ependent risk factors for mortality, whereas pulmonary atresia or stenosis and pulmonary artery bandi

36 In TOF, pulmonary atresia (P=0.003), male sex (P=0.01) and previ

37 OF) patients with pulmonary stenosis (PS) or pulmonary atresia (PA).

38 diseases like tetralogy of Fallot (TOF) and pulmonary atresia (PA).

39 crest, and compared these phenotypes to the pulmonary atresia phenotype observed following the syste

40 , embryos treated with cyclopamine exhibited pulmonary atresia, pulmonary stenosis, and persistent tr

41 ructive lesions, including nine fetuses with pulmonary atresia, six with severe obstructive tricuspid

42 and more common in tetralogy of Fallot with pulmonary atresia than tetralogy of Fallot alone.

43 rare and resembles tetralogy of Fallot with pulmonary atresia: There is a high incidence of aortopul

44 120 infants (7.5% [95% CI, 3.5%-13.8%]) with pulmonary atresia to 497 of 801 (62.0% [58.7%-65.4%]) wi

45 PCs) in infants with tetralogy of Fallot and pulmonary atresia (TOF/PA) and to prospectively validate

46 with TOF pulmonary stenosis (TOF/PS) or TOF pulmonary atresia (TOF/PA) who were <90 days of age unde

47 Twenty-three children with pulmonary atresia underwent 48 cardiac-triggered dynamic

48 Since 1992, 85 patients with pulmonary atresia, VSD, and MAPCAs have undergone unifoc

49 ilation, prematurity, DiGeorge syndrome, and pulmonary atresia were more common in the SR group (p 0.

50 rdiac defects including overriding aorta and pulmonary atresia, while none of the sham-operated contr

51 ete atrioventricular septal defect, 5.3% for pulmonary atresia with an intact ventricular septum, and

52 balanced atrioventricular septal defect, and pulmonary atresia with intact ventricular septum (15 fet

53 sociated with higher risk of thrombosis were pulmonary atresia with intact ventricular septum (hazard

54 (n=39), valvar pulmonary stenosis (n=10), or pulmonary atresia with intact ventricular septum (n=5) w

55 Pulmonary atresia with intact ventricular septum (PA/IVS

56 ts undergoing catheter valve perforation for pulmonary atresia with intact ventricular septum (PAIVS)

57 way in a longitudinal series of fetuses with pulmonary atresia with intact ventricular septum (PAIVS)

58 We describe the morphologic variability in pulmonary atresia with intact ventricular septum (PAIVS)

59 ased study was to determine the incidence of pulmonary atresia with intact ventricular septum (PAIVS)

60 Ninety-nine patients (71 with pulmonary atresia with intact ventricular septum and 28

61 Patients with pulmonary atresia with intact ventricular septum deemed

62 Pulmonary atresia with intact ventricular septum is rare

63 ventricle (RV) decompression in infants with pulmonary atresia with intact ventricular septum vary wi

64 AND Neonates undergoing RV decompression for pulmonary atresia with intact ventricular septum were in

65 tions, and mice lacking connexin43 developed pulmonary atresia with intact ventricular septum.

66 Pulmonary atresia with ventricular septal defect (VSD) a

67 n components of the major anomalies, include pulmonary atresia with ventricular septal defect, pulmon

68 h surgically repaired tetralogy of Fallot or pulmonary atresia with ventricular septal defect.

69 h an intact ventricular septum, and 6.4% for pulmonary atresia with ventricular septal defect.