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1 ory-filter characteristics of listeners with sensorineural hearing loss.
2 ogenitors and mutations in these genes cause sensorineural hearing loss.
3 of the inner ear, which ultimately leads to sensorineural hearing loss.
4 recurring episodes of sudden or progressive sensorineural hearing loss.
5 lit-foot type 1 malformation associated with sensorineural hearing loss.
6 rder characterized by ovarian dysgenesis and sensorineural hearing loss.
7 ardiomyopathy, kidney and liver disease, and sensorineural hearing loss.
8 of this protection results in cell death and sensorineural hearing loss.
9 Hair cell loss is a major cause of sensorineural hearing loss.
10 obodontia) segregating with a high-frequency sensorineural hearing loss.
11 own as a major target antigen for autoimmune sensorineural hearing loss.
12 lar disease associated with a high-frequency sensorineural hearing loss.
13 auses is irreversible and leads to permanent sensorineural hearing loss.
14 ice hear well initially but show progressive sensorineural hearing loss.
15 ent and prognosis for patients with profound sensorineural hearing loss.
16 ersonalized strategies to diagnose and treat sensorineural hearing loss.
17 trated to improve outcomes for patients with sensorineural hearing loss.
18 l dominant form of progressive non-syndromic sensorineural hearing loss.
19 mice had a hyperactive circling behavior and sensorineural hearing loss.
20 pigmentary retinopathy and/or cataracts, and sensorineural hearing loss.
21 mentary retinopathy, cataracts, or both; and sensorineural hearing loss.
22 e witnessed a revolution in the treatment of sensorineural hearing loss.
23 ous parents and had an early onset bilateral sensorineural hearing loss.
24 significant cause of morbidity, particularly sensorineural hearing loss.
25 DFNBL, for autosomal recessive non-syndromic sensorineural hearing loss.
26 ed by progressive pigmentary retinopathy and sensorineural hearing loss.
27 orm of dominant, early-onset and progressive sensorineural hearing loss.
28 d of care for patients with mild to moderate sensorineural hearing loss.
29 ed bilateral mild to moderate high-frequency sensorineural hearing loss.
30 commonly revealed severe-profound bilateral sensorineural hearing loss.
31 ircular canals as an anatomical correlate of sensorineural hearing loss.
32 agent with a nearly universal side effect of sensorineural hearing loss.
33 y, morbidity, or long-term sequelae, such as sensorineural hearing loss.
34 oactivity in novel environments, tremor, and sensorineural hearing loss.
35 ctions, including ataxia, optic atrophy, and sensorineural hearing loss.
36 ide and the most common cause of non-genetic sensorineural hearing loss.
37 ich was identified in a 4-year-old girl with sensorineural hearing loss.
38 d lineage, impaired lymphoid maturation, and sensorineural hearing loss.
39 al underlying mechanism of CHARGE-associated sensorineural hearing loss.
40 opathy, branch retinal artery occlusion, and sensorineural hearing loss.
41 of lockdowns during the pandemic with sudden sensorineural hearing loss.
42 presage pathological hyperactivity following sensorineural hearing loss.
43 ontine angle, and it typically presents with sensorineural hearing loss.
44 ng GJB2 gene lead to many skin disorders and sensorineural hearing loss.
45 g mental retardation, vision impairment, and sensorineural hearing loss.
46 mited due to serious side effects, including sensorineural hearing loss.
47 (p.Trp24*), which is an established cause of sensorineural hearing loss.
48 circuits, and its mutation may contribute to sensorineural hearing loss.
49 ane in the middle ear may be able to reverse sensorineural hearing loss.
50 siblings had poor balance and 1 sibling had sensorineural hearing loss.
51 with a broad clinical spectrum that includes sensorineural hearing loss.
52 ble in the adult mammalian ear, resulting in sensorineural hearing loss.
53 s a rare disease that results in progressive sensorineural hearing loss.
54 ipheral facial paralysis and 2 patients with sensorineural hearing loss.
55 anguineous family with moderate nonsyndromic sensorineural hearing loss.
56 articipants were 36 adults with symmetrical, sensorineural hearing loss (18 experienced hearing instr
57 sequential probands referred for congenital sensorineural hearing loss, 22 (42%) were found to have
58 tic (venous thrombosis 25%, lymphedema 11%), sensorineural hearing loss 76%, miscarriage 33%, and hyp
59 elopmental delay (94%), optic atrophy (83%), sensorineural hearing loss (78%), and cerebellar ataxia
61 dy examines the national incidence of sudden sensorineural hearing loss after COVID-19 vaccination us
62 fy mutations in Gipc3 underlying progressive sensorineural hearing loss (age-related hearing loss 5,
63 loss may represent the most common causes of sensorineural hearing loss also known as hidden hearing
64 oms can help predict which infants will have sensorineural hearing loss, among asymptomatic cCMV ther
65 r, 9/21 epilepsy, 12/15 clumsiness, 3/21 had sensorineural hearing loss and 4/20 feeding difficulties
67 otogl with morpholinos in zebrafish leads to sensorineural hearing loss and anatomical changes in the
70 292 had no polyneuropathy or ataxia, and the sensorineural hearing loss and cataract were attributed
71 a good animal model to evaluate the role of sensorineural hearing loss and central inhibition in aud
72 ion in multiple tissues, suggesting that the sensorineural hearing loss and characteristic brain malf
73 ilitate early detection and intervention for sensorineural hearing loss and developmental delay, wher
75 developmental abnormalities of the cochlea, sensorineural hearing loss and diffuse thyroid enlargeme
76 dered in patients presenting with congenital sensorineural hearing loss and disorders of cornificatio
79 erturn a long-standing dogma in the study of sensorineural hearing loss and highlight the importance
80 progressive motor disturbance with variable sensorineural hearing loss and language/cognitive dysfun
81 ty of hearing-loss disorders, such as sudden sensorineural hearing loss and Meniere's disease that ar
82 d is the main nongenetic cause of congenital sensorineural hearing loss and neurological damage, yet
84 resentations ranging from Perrault syndrome (sensorineural hearing loss and ovarian insufficiency) to
85 autosomal recessive disorder associated with sensorineural hearing loss and pili torti, is caused by
86 d that an absence of Np65 causes early-onset sensorineural hearing loss and prevented the normal syna
87 ant mice, absence of Np65 causes early-onset sensorineural hearing loss and prevents normal neurotran
88 disorder characterized by moderate to severe sensorineural hearing loss and progressive retinitis pig
89 disorder characterized by moderate to severe sensorineural hearing loss and progressive retinitis pig
90 pmental disorder and bilateral non-syndromic sensorineural hearing loss and provide further data supp
91 racterized by progressive pontobulbar palsy, sensorineural hearing loss and respiratory insufficiency
92 syndrome type 2, characterized by congenital sensorineural hearing loss and retinitis pigmentosa (RP)
93 , age-adjusted blood m.3243A>G heteroplasmy, sensorineural hearing loss and serum lactate were signif
94 der characterized by the association between sensorineural hearing loss and thyroid swelling or goitr
95 ree individuals with non-syndromic bilateral sensorineural hearing loss and vestibular areflexia.
96 ) gene, causing the adult-onset, progressive sensorineural hearing loss and vestibular disorder at th
97 e etiologic for the late-onset, progressive, sensorineural hearing loss and vestibular dysfunction kn
98 an follow-up of 24 months, the proportion of sensorineural hearing loss and/or neurologic sequelae we
99 ral nervous system and include microcephaly, sensorineural hearing loss, and cognitive developmental
100 a syndrome consisting of encephalomyopathy, sensorineural hearing loss, and hypertrophic cardiomyopa
101 lities, insulin-dependent diabetes mellitus, sensorineural hearing loss, and mild intellectual disabi
102 who presented with osteoporosis, cataracts, sensorineural hearing loss, and mild learning defects.
103 s much to learn about pathogenesis of sudden sensorineural hearing loss, and more clinical trials are
104 wo thirds of respondents were male, most had sensorineural hearing loss, and most were older than 50;
105 including peripheral neuropathy, progressive sensorineural hearing loss, and neurodegeneration, are r
106 ed disorder characterized by kidney disease, sensorineural hearing loss, and ocular abnormalities.
107 al-recessive inheritance, severe to profound sensorineural hearing loss, and partial agenesis of the
108 of the GATA3 gene causes hypoparathyroidism, sensorineural hearing loss, and renal disease (HDR) synd
109 nction, cachetic dwarfism, photosensitivity, sensorineural hearing loss, and retinal degradation.
110 llar ataxia, early-onset cerebellar atrophy, sensorineural hearing loss, and the distinctive associat
111 etely penetrant, predominantly low-frequency sensorineural hearing loss, and the Fgfr3(P244R) mice sh
113 members inherited pili torti and prelingual sensorineural hearing loss as autosomal recessive traits
118 e received a diagnosis of bilateral profound sensorineural hearing loss at neonatal hearing screening
119 spontaneous attacks of vertigo, fluctuating sensorineural hearing loss, aural fullness, and tinnitus
120 d-responsive, rapidly progressive, bilateral sensorineural hearing loss (autoimmune inner ear disease
121 obtained from 49 participants with moderate sensorineural hearing loss before fitting and after 3 we
122 cause of neurological problems, particularly sensorineural hearing loss, but data on long-term sequel
123 vide significant benefit for a wide range of sensorineural hearing loss, but no carefully controlled,
124 gs to more clinically relevant conditions of sensorineural hearing loss by examining the role of frac
125 ia, areflexia, pes cavus, optic atrophy, and sensorineural hearing loss (CAPOS) syndrome is caused by
126 lar ataxia-areflexia-pes cavus-optic atrophy-sensorineural hearing loss (CAPOS), and none were suspec
128 that this variant may modify the severity of sensorineural hearing loss caused by a variety of factor
130 cterized by pigmentary retinal degeneration, sensorineural hearing loss, childhood obesity, non-insul
132 Patients with ATP6B1 mutations also have sensorineural hearing loss; consistent with this finding
133 disability, hypotonia, spasticity, seizures, sensorineural hearing loss, cortical visual impairment,
134 oximately 20-30% of patients with congenital sensorineural hearing loss demonstrate radiographic abno
135 plantation, the current therapy for profound sensorineural hearing loss, depends on a functional nerv
136 ocus responsible for postlingual progressive sensorineural hearing loss (designated DFNA9) that maps
138 nalysis of dominantly inherited, progressive sensorineural hearing loss DFNA41 in a six-generation ki
141 rophy, neuropathy, myopathy, cardiomyopathy, sensorineural hearing loss, diabetes mellitus, and other
142 ohort study compares the incidence of sudden sensorineural hearing loss during the COVID-19 pandemic
143 rg syndrome (MTS), which is characterised by sensorineural hearing loss, dystonia and blindness.
144 oding connexin 26 (cx26) have been linked to sensorineural hearing loss either alone or as part of a
145 results in vertebral compression fractures, sensorineural hearing loss, eye defects, and heart defec
146 bers show a bilateral, sloping, progressive, sensorineural hearing loss, first evident at 6000 and 80
147 elin plasticity and how this could relate to sensorineural hearing loss following peripheral impairme
153 either common (hearing loss) or distinctive (sensorineural hearing loss in a child), they are importa
154 t, progressive, high-frequency, nonsyndromic sensorineural hearing loss in a large, multigenerational
155 te OPG at high levels and lack of OPG causes sensorineural hearing loss in addition to the previously
160 channel-like gene 1 (TMC1) cause progressive sensorineural hearing loss in humans and Beethoven (Tmc1
163 GED1 loss, and a diversity of conductive and sensorineural hearing loss in nearly half of AGS patient
164 53G > A), of NLRP3 causes autosomal-dominant sensorineural hearing loss in two unrelated families.
165 oss in which the cochleae are not damaged or sensorineural hearing loss in which both cochleae are re
166 cted in two unrelated persons with increased sensorineural hearing loss, in the other caused by a mut
167 coustic trauma, one of the leading causes of sensorineural hearing loss, induces sensory hair cell da
168 evere form of spondylo-epiphyseal dysplasia, sensorineural hearing loss, intellectual disability and
174 g children with bilateral severe to profound sensorineural hearing loss is associated with improved l
175 e not precipitated by cold exposure and that sensorineural hearing loss is frequently also present.
176 In the US, most childhood-onset bilateral sensorineural hearing loss is genetic, with more than 12
180 sible causes of hearing loss, such as sudden sensorineural hearing loss, is important to maximize the
182 sly unknown autosomal-recessive nonsyndromic sensorineural hearing loss locus (DFNB91) to chromosome
183 stablished means to treat severe-to-profound sensorineural hearing loss, may induce inflammation, fib
184 known about the effects of mild-to-moderate sensorineural hearing loss (MMHL) during development.
185 temic symptoms including intermittent fever, sensorineural hearing loss, nasal tenderness, and hoarse
186 , developmental delay, brain dysmyelination, sensorineural hearing loss, nystagmus, progressive chole
191 more likely than controls to have bilateral sensorineural hearing loss of 40 dB or more (unmatched 1
192 t first-time hearing aid users with averaged sensorineural hearing losses of more than 25 dB were pro
193 GNIFICANCE STATEMENT People with age-related sensorineural hearing loss often struggle to follow spee
194 syndrome that includes the subacute onset of sensorineural hearing loss, often accompanied by vertigo
195 verlapping clinical features, manifesting as sensorineural hearing loss, often associated with vertig
196 spasticity, cerebellar ataxia and nystagmus, sensorineural hearing loss, optic atrophy and bulbar dys
197 racterized by mental retardation, hypotonia, sensorineural hearing loss, optic atrophy, and other fea
198 f identification of syndromic or progressive sensorineural hearing loss or auditory neuropathy spectr
199 n 18 years with bilateral severe to profound sensorineural hearing loss or complete hearing loss for
200 s a higher risk of adverse neonatal outcome (sensorineural hearing loss or neurological deficits).
201 otitis media (OM), including high-frequency sensorineural hearing loss or vertigo, is not uncommon.
202 included primary immunodeficiency, bilateral sensorineural hearing loss, organ anomalies and skeletal
203 autosomal dominant disorder characterized by sensorineural hearing loss, palmoplantar keratoderma, kn
204 t enables us to differentiate conductive and sensorineural hearing loss, perceive sounds despite a di
205 regating an autosomal dominant, progressive, sensorineural hearing loss phenotype that has been linke
207 man with a history of progressive bilateral sensorineural hearing loss presented to a neuro-ophthalm
208 trial involving 250 patients with unilateral sensorineural hearing loss presenting within 14 days of
209 mbrane abnormalities may be one aetiology of sensorineural hearing loss primarily affecting the mid-f
210 resented with variable phenotypes comprising sensorineural hearing loss, primary ovarian insufficienc
211 mined included dipstick hematuria, bilateral sensorineural hearing loss, proteinuria, lower eGFR, and
212 (ISRCTN59733689), adults with mild-moderate sensorineural hearing loss received 3 intratympanic inje
213 iginally identified in Persian families with sensorineural hearing loss, regulates peroxisomal dynami
214 ic TBS patients by displaying high-frequency sensorineural hearing loss, renal cystic hypoplasia and
215 year-old female has intellectual disability, sensorineural hearing loss requiring bilateral cochlear
216 cochlea, caused by macular degeneration and sensorineural hearing loss, respectively, affect a growi
218 diagnosis and treatment for individuals with sensorineural hearing loss.SIGNIFICANCE STATEMENT Differ
219 ns have reported the sporadic development of sensorineural hearing loss (SNHL) after intravenous or h
220 ry, 5 of whom developed teprotumumab-related sensorineural hearing loss (SNHL) and 1 patient also dev
221 infection worldwide and is a major cause of sensorineural hearing loss (SNHL) and developmental dela
222 d whole-exome sequencing in individuals with sensorineural hearing loss (SNHL) and identified pathoge
224 Hippel-Lindau disease and cause irreversible sensorineural hearing loss (SNHL) and vestibulopathy.
226 c.325A>T (p.I109F) in a child with profound sensorineural hearing loss (SNHL) associated with incomp
229 Behavioral studies in humans suggest that sensorineural hearing loss (SNHL) decreases sensitivity
232 e to four decades, the incidence of acquired sensorineural hearing loss (SNHL) in children living in
234 Lassa virus (LASV)-infected patients develop sensorineural hearing loss (SNHL) in the late stages of
243 audiology clinics and can leave people with sensorineural hearing loss (SNHL) suffering from communi
244 ngenital cytomegalovirus (CMV) infection and sensorineural hearing loss (SNHL) was first described al
246 nts lead to a human disease characterized by sensorineural hearing loss (SNHL) with or without a nonp
247 s a rare recessive disorder characterized by sensorineural hearing loss (SNHL), amelogenesis imperfec
248 terized by vascularizing keratitis, profound sensorineural hearing loss (SNHL), and progressive eryth
249 rated that noise exposure, a common cause of sensorineural hearing loss (SNHL), leads to cognitive im
257 -five percent of people with VS present with sensorineural hearing loss (SNHL); the mechanism of this
258 termining the etiology of severe-to-profound sensorineural hearing loss (SP-SNHL) in pediatric subjec
260 howed an increase in the incidence of sudden sensorineural hearing loss (SSNHL) following vaccination
261 atients who need urgent treatment for sudden sensorineural hearing loss (SSNHL) from those who do not
267 transcriptional co-activator EYA4 gene cause sensorineural hearing loss that can occur in association
268 2 represents a locus for congenital profound sensorineural hearing loss that has yet to be mapped.
269 However, one in eight Americans suffers from sensorineural hearing loss that is great enough to adver
270 describe 2 unrelated pedigrees with MTP and sensorineural hearing loss that segregate with a DIAPH1
271 anging from highly restricted pili torti and sensorineural hearing loss (the Bjornstad syndrome) to p
272 of hair cells or auditory neurons results in sensorineural hearing loss, the consequence of supportin
273 s (CI) are the standard of care for profound sensorineural hearing loss they are technically constrai
274 chronic disorder of the inner ear defined by sensorineural hearing loss, tinnitus and episodic vertig
275 ting from minutes to hours, with fluctuating sensorineural hearing loss, tinnitus, and aural pressure
276 syndrome (primary ovarian insufficiency and sensorineural hearing loss) to severe childhood onset of
277 siblings presented with autosomal recessive sensorineural hearing loss: two had high-frequency loss,
279 rized by fever, chronic meningitis, uveitis, sensorineural hearing loss, urticarial skin rash, and a
280 ific algorithms that predict the presence of sensorineural hearing loss using only miRNA expression p
281 essive disorder characterized by progressive sensorineural hearing loss, vestibular dysfunction, and
282 These birth defects include microcephaly, sensorineural hearing loss, vision loss, and cognitive i
286 l sensory and sensorimotor neuropathies, and sensorineural hearing loss were common findings in patie
292 of NLRP3 demonstrated a higher prevalence of sensorineural hearing loss while being less prone to ski
293 49 children from 406 families with bilateral sensorineural hearing loss with an onset younger than 18
296 utosomal dominant, nonsyndromic, progressive sensorineural hearing loss with vestibular pathology.
297 sease erythrokeratoderma variabilis (EKV) or sensorineural hearing loss with/without peripheral neuro
300 lds were closely aligned after noise-induced sensorineural hearing loss, yet FME growth slopes were d