ライフサイエンスコーパス: transmembrane conductance regulator

1 o for lumen formation, CFTR (cystic fibrosis transmembrane conductance regulator).

2 tide-binding domain from the cystic fibrosis transmembrane conductance regulator.

3 en through activation of the cystic fibrosis transmembrane conductance regulator.

4 lesser effects on misfolded cystic fibrosis transmembrane conductance regulator.

5 ells with a functional or mutated form of CF transmembrane conductance regulator.

6 stance arteries ex vivo, the cystic fibrosis transmembrane conductance regulator (1) is critical for

7 nger regulatory factor-1 and cystic fibrosis transmembrane conductance regulator (a key player in the

8 Because the cystic fibrosis transmembrane conductance regulator (ABCC7) is closely r

9 cells via a reduction in the cystic fibrosis transmembrane conductance regulator activity and biosynt

10 essure resulted in decreased cystic fibrosis transmembrane conductance regulator activity and liquid

11 /adenylyl cyclase-dependent, cystic fibrosis transmembrane conductance regulator activity.

12 Reduced expression of cystic fibrosis transmembrane conductance regulator and dilation of acin

13 secretion appears to require cystic fibrosis transmembrane conductance regulator and electrogenic Na(

14 porters (ABC), including the cystic fibrosis transmembrane conductance regulator and P-glycoprotein.

15 was completely dependent on cystic fibrosis transmembrane conductance regulator and partially depend

16 al exocytosis of NHE3, CFTR (cystic fibrosis transmembrane conductance regulator), and GLUT5 required

17 cellular adhesion molecule, cystic fibrosis transmembrane conductance regulator, and anion exchanger

18 -dependent activation of the cystic fibrosis transmembrane conductance regulator anion channel was in

19 codon in mRNAs encoding the cystic fibrosis transmembrane conductance regulator anion channel.

20 cidic pH produced by loss of cystic fibrosis transmembrane conductance regulator anion channels or pr

21 Opening and closing of the cystic fibrosis transmembrane conductance regulator are controlled by AT

22 We identify the cystic fibrosis transmembrane conductance regulator as a critical regula

23 es, at least in part through cystic fibrosis transmembrane conductance regulator-associated channels,

24 unction mutations in the chloride channel CF transmembrane conductance regulator can elevate the acti

25 in gross mislocalization of cystic fibrosis transmembrane conductance regulator, causing marked redu

26 s to the gating mutations of cystic fibrosis transmembrane conductance regulator (CFTR or ABCC7; i.e.

27 Cystic fibrosis transmembrane conductance regulator (CFTR) (ABCC7), uniq

28 ol of cell proliferation and cystic fibrosis transmembrane conductance regulator (CFTR) -driven fluid

29 coid dexamethasone increases cystic fibrosis transmembrane conductance regulator (CFTR) abundance in

30 linone CFTRact-J027 (4) as a cystic fibrosis transmembrane conductance regulator (CFTR) activator wit

31 ates that ivacaftor improves cystic fibrosis transmembrane conductance regulator (CFTR) activity and

32 The cystic fibrosis transmembrane conductance regulator (CFTR) acts as a cha

33 tal cells and frequently coexpressed with CF transmembrane conductance regulator (CFTR) along with tr

34 ons to the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) also cause pa

35 membrane, which include the cystic fibrosis transmembrane conductance regulator (CFTR) and Ca(2+)-ac

36 ainst other proteins such as cystic fibrosis transmembrane conductance regulator (CFTR) and dystrophi

37 ulated by apically expressed cystic fibrosis transmembrane conductance regulator (CFTR) and large-con

38 nal HCO3(-) exit mediated by cystic fibrosis transmembrane conductance regulator (CFTR) and solute ca

39 regulates the biogenesis of cystic fibrosis transmembrane conductance regulator (CFTR) and the epith

40 l permeability and decreased cystic fibrosis transmembrane conductance regulator (Cftr) and the Na-K-

41 hrough the chloride channels cystic fibrosis transmembrane conductance regulator (CFTR) and TMEM16A (

42 g cassette (ABC) transporter cystic fibrosis transmembrane conductance regulator (CFTR) and two other

43 alanine 508 (F508del) in the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

44 on special properties of the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

45 The Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) anion channel

46 fibrosis (CF) pigs, loss of cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

47 in the gene that encodes the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

48 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

49 and secrete Cl- through the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

50 s caused by mutations of the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) anion channel

51 alanine 508 (F508del) in the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

52 loride permeation pathway in cystic fibrosis transmembrane conductance regulator (CFTR) as a short na

53 three nonsense mutations of cystic fibrosis transmembrane conductance regulator (CFTR) associated wi

54 minal truncation mutation of cystic fibrosis transmembrane conductance regulator (CFTR) associated wi

55 ts in functional expression defect of the CF transmembrane conductance regulator (CFTR) at the apical

56 ions that stabilize the cystic fibrosis (CF) transmembrane conductance regulator (CFTR) at the apical

57 Small-molecule modulators of cystic fibrosis transmembrane conductance regulator (CFTR) biology show

58 Mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) cause recurri

59 ginine would enhance F508del-cystic fibrosis transmembrane conductance regulator (CFTR) channel activ

60 The cystic fibrosis transmembrane conductance regulator (CFTR) channel is ac

61 F) mice with a nonfunctional cystic fibrosis transmembrane conductance regulator (CFTR) channel was r

62 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) channel, whic

63 caused by loss of functional cystic fibrosis transmembrane conductance regulator (CFTR) channel.

64 The role of epithelial cystic fibrosis (CF) transmembrane conductance regulator (CFTR) chloride chan

65 used by loss of a functional cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

66 e: functional defects of the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

67 eine scanning studies of the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

68 y the functional expression defect of the CF transmembrane conductance regulator (CFTR) chloride chan

69 of-function mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

70 ssive disease, caused by mutations in the CF transmembrane conductance regulator (CFTR) chloride chan

71 ppropriate activation of the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

72 esults from mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

73 eads to an inhibition of the cystic fibrosis transmembrane conductance regulator (CFTR) Cl(-) channel

74 Cystic fibrosis transmembrane conductance regulator (CFTR) Cl(-) channel

75 tation DeltaF508 on the gene encoding the CF transmembrane conductance regulator (CFTR) Cl(-) channel

76 ability, and function of the cystic fibrosis transmembrane conductance regulator (CFTR) Cl(-) channel

77 the loss of function of the cystic fibrosis transmembrane conductance regulator (CFTR) combined with

78 of-function mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) compromise ep

79 A pathway for cystic fibrosis transmembrane conductance regulator (CFTR) degradation i

80 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) disrupt epith

81 Smoking is reported to cause cystic fibrosis transmembrane conductance regulator (CFTR) dysfunction i

82 um (OE) of mice deficient in cystic fibrosis transmembrane conductance regulator (CFTR) exhibits ion

83 els (TMEM16A), including the cystic fibrosis transmembrane conductance regulator (CFTR) expressed on

84 n epithelial cells decreases cystic fibrosis transmembrane conductance regulator (CFTR) expression an

85 arette smoke decreased AMPhi cystic fibrosis transmembrane conductance regulator (CFTR) expression, p

86 main interaction between the cystic fibrosis transmembrane conductance regulator (CFTR) first cytosol

87 as correctors of the F508del-cystic fibrosis transmembrane conductance regulator (CFTR) folding defec

88 re needed to reliably assess Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) function in v

89 e findings are directly caused by loss of CF transmembrane conductance regulator (CFTR) function or s

90 is a genetic disorder caused by defective CF Transmembrane Conductance Regulator (CFTR) function.

91 attributable to increases in cystic fibrosis transmembrane conductance regulator (CFTR) function.

92 Mutations in the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) gene affect C

93 Mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene cause cy

94 hesis that disruption of the cystic fibrosis transmembrane conductance regulator (CFTR) gene directly

95 of-function mutations of the cystic fibrosis transmembrane conductance regulator (CFTR) gene encoding

96 The F508del mutation in the CF transmembrane conductance regulator (Cftr) gene induces

97 ted since the cloning of the cystic fibrosis transmembrane conductance regulator (CFTR) gene is being

98 The F508del mutation in the cystic fibrosis transmembrane conductance regulator (Cftr) gene is belie

99 kb -35 (DHS-35kb) 5' to the cystic fibrosis transmembrane conductance regulator (CFTR) gene is evide

100 ease-causing mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) gene is the o

101 The most common cystic fibrosis transmembrane conductance regulator (CFTR) gene mutation

102 The cystic fibrosis transmembrane conductance regulator (CFTR) gene provides

103 sease, caused by genetic diversity in the CF transmembrane conductance regulator (CFTR) gene, a cycli

104 s caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene, encodin

105 ssive disorder caused by mutations in the CF transmembrane conductance regulator (CFTR) gene, encodin

106 V1, expressing a full-length cystic fibrosis transmembrane conductance regulator (CFTR) gene, is capa

107 enetic disease caused by mutations in the CF transmembrane conductance regulator (CFTR) gene, resulti

108 e caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene, resulti

109 s caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene, which e

110 e caused by mutations of the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

111 the F508del mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

112 g chromatin structure at the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

113 CF), a disease caused by mutations in the CF transmembrane conductance regulator (CFTR) gene.

114 oss 250 kb, encompassing the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

115 r caused by mutations in the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) gene.

116 hibitor gene (SPINK1) or the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

117 e caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

118 In those with severe CF transmembrane conductance regulator (CFTR) genotypes, IR

119 binding domain (NBD2) of the cystic fibrosis transmembrane conductance regulator (CFTR) has lagged be

120 e than 2000 mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) have been des

121 es (MPhis) with mutations in cystic fibrosis transmembrane conductance regulator (CFTR) have blunted

122 binding domain (NBD1) of the cystic fibrosis transmembrane conductance regulator (CFTR) have distinct

123 2)AR)-mediated activation of cystic fibrosis transmembrane conductance regulator (CFTR) in epithelial

124 function of Slc26a6 and the cystic fibrosis transmembrane conductance regulator (CFTR) in HeLa cells

125 rosis homozygous for F508del-cystic fibrosis transmembrane conductance regulator (CFTR) in placebo-co

126 The role of Pseudomonas aeruginosa and CF transmembrane conductance regulator (CFTR) in Treg regul

127 st to assess the role of the cystic fibrosis transmembrane conductance regulator (CFTR) in urinary HC

128 used by the F508 mutation in cystic fibrosis transmembrane conductance regulator (CFTR) include a "co

129 demonstrate the efficacy of cystic fibrosis transmembrane conductance regulator (CFTR) inhibitor (R)

130 The virulence factor cystic fibrosis transmembrane conductance regulator (CFTR) inhibitory fa

131 PTEN and the CF transmembrane conductance regulator (CFTR) interacted di

132 Cystic fibrosis transmembrane conductance regulator (CFTR) is a chloride

133 The cystic fibrosis transmembrane conductance regulator (CFTR) is a chloride

134 Cystic fibrosis transmembrane conductance regulator (CFTR) is a Cl(-)-se

135 cAMP-activated Cl(-) channel cystic fibrosis transmembrane conductance regulator (CFTR) is a major pr

136 brates, the chloride channel cystic fibrosis transmembrane conductance regulator (CFTR) is a master r

137 The cystic fibrosis transmembrane conductance regulator (CFTR) is a member o

138 Cystic fibrosis transmembrane conductance regulator (CFTR) is a multidom

139 The cystic fibrosis transmembrane conductance regulator (CFTR) is a plasma m

140 The cystic fibrosis transmembrane conductance regulator (CFTR) is a plasma-m

141 Expression of the cystic fibrosis transmembrane conductance regulator (CFTR) is altered in

142 The cystic fibrosis transmembrane conductance regulator (CFTR) is an anion c

143 The cystic fibrosis transmembrane conductance regulator (CFTR) is an anion c

144 Cystic fibrosis transmembrane conductance regulator (CFTR) is an anion c

145 The cystic fibrosis transmembrane conductance regulator (CFTR) is an anion c

146 The cystic fibrosis transmembrane conductance regulator (CFTR) is an apical

147 The cystic fibrosis transmembrane conductance regulator (CFTR) is an ATP-bin

148 ABSTRACT: Cystic fibrosis transmembrane conductance regulator (CFTR) is an ATP-gat

149 The cystic fibrosis transmembrane conductance regulator (CFTR) is an epithel

150 The cystic fibrosis transmembrane conductance regulator (CFTR) is an epithel

151 The cystic fibrosis transmembrane conductance regulator (CFTR) is an ion cha

152 an DeltaF508 mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) is associated

153 Endocytic recycling of the cystic fibrosis transmembrane conductance regulator (CFTR) is blocked by

154 modulator compounds for the cystic fibrosis transmembrane conductance regulator (CFTR) is key for th

155 The cystic fibrosis transmembrane conductance regulator (CFTR) is mutated in

156 Cystic fibrosis transmembrane conductance regulator (CFTR) is one ERAD s

157 08 deletion (F508del) in the cystic fibrosis transmembrane conductance regulator (CFTR) is the most c

158 Cystic fibrosis transmembrane conductance regulator (CFTR) is the only l

159 Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) is the secret

160 gamma stimulation in vivo in cystic fibrosis transmembrane conductance regulator (Cftr) knockout mice

161 s or dysfunction of the cystic fibrosis (CF) transmembrane conductance regulator (CFTR) leads to impa

162 We hypothesized that cystic fibrosis transmembrane conductance regulator (CFTR) may be critic

163 s (FPOP) for footprinting of cystic fibrosis transmembrane conductance regulator (CFTR) membrane tran

164 Cystic fibrosis transmembrane conductance regulator (CFTR) modulators co

165 mbination treatment with the cystic fibrosis transmembrane conductance regulator (CFTR) modulators te

166 o boost the response to cystic fibrosis (CF) transmembrane conductance regulator (CFTR) modulators, l

167 The most prevalent cystic fibrosis transmembrane conductance regulator (CFTR) mutation caus

168 e carrying the most frequent cystic fibrosis transmembrane conductance regulator (CFTR) mutation in h

169 es the common human Phe508del (DeltaF508) CF transmembrane conductance regulator (CFTR) mutation, whe

170 Using 20 variants from cystic fibrosis transmembrane conductance regulator (CFTR) nucleotide-bi

171 Inhibition of either cystic fibrosis transmembrane conductance regulator (CFTR) or Na(+)-K(+)

172 . explored the role that the cystic fibrosis transmembrane conductance regulator (CFTR) plays in plat

173 Ivacaftor is a cystic fibrosis transmembrane conductance regulator (CFTR) potentiator r

174 Ivacaftor, a cystic fibrosis transmembrane conductance regulator (CFTR) potentiator,

175 ed by defective or deficient cystic fibrosis transmembrane conductance regulator (CFTR) protein activ

176 Cystic fibrosis transmembrane conductance regulator (CFTR) protein is a

177 and decreased apical cilia, cystic fibrosis transmembrane conductance regulator (CFTR) protein level

178 unction or deficiency of the cystic fibrosis transmembrane conductance regulator (CFTR) protein, an e

179 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) protein, and

180 sing of the DeltaF508 mutant cystic fibrosis transmembrane conductance regulator (CFTR) protein.

181 is (CF) is due to a folding defect in the CF transmembrane conductance regulator (CFTR) protein.

182 (CF) is caused by defective Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) protein.

183 In the liver, the cystic fibrosis (CF) transmembrane conductance regulator (CFTR) regulates bil

184 hly PKA-phosphorylated human cystic fibrosis transmembrane conductance regulator (CFTR) regulatory re

185 binding domain (NBD1) of the cystic fibrosis transmembrane conductance regulator (CFTR) results in de

186 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) that compromi

187 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) that impair i

188 ftor is a potentiator of the cystic fibrosis transmembrane conductance regulator (CFTR) that reduces

189 Misfolding of DeltaF508 cystic fibrosis (CF) transmembrane conductance regulator (CFTR) underlies pat

190 amino acids inserted at the cystic fibrosis transmembrane conductance regulator (CFTR) W1282X PTC (a

191 ons of the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) which is an a

192 the apical chloride channel cystic fibrosis transmembrane conductance regulator (CFTR) with 90% of p

193 ons of the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) with a preval

194 nique ATP-gated ion channel (cystic fibrosis transmembrane conductance regulator (CFTR)).

195 functional abnormalities of cystic fibrosis transmembrane conductance regulator (CFTR), a 25% reduct

196 f apoptosis and involves the cystic fibrosis transmembrane conductance regulator (CFTR), a cAMP-regul

197 caused by mutations in the gene encoding CF transmembrane conductance regulator (CFTR), a chloride c

198 Malfunction of the cystic fibrosis transmembrane conductance regulator (CFTR), a gated path

199 oss-of-function mutations of cystic fibrosis transmembrane conductance regulator (CFTR), a phosphoryl

200 F508del cystic fibrosis transmembrane conductance regulator (CFTR), a well-studi

201 al PDZ domains bind the cystic fibrosis (CF) transmembrane conductance regulator (CFTR), an epithelia

202 ajor anion channels, such as cystic fibrosis transmembrane conductance regulator (CFTR), anoctamin-1(

203 genes such as PRSS1, SPINK1, cystic fibrosis transmembrane conductance regulator (CFTR), chymotrypsin

204 ntify the interactome of the cystic fibrosis transmembrane conductance regulator (CFTR), demonstratin

205 of the common mutant of the cystic fibrosis transmembrane conductance regulator (CFTR), F508del, is

206 cal translation speed of the cystic fibrosis transmembrane conductance regulator (CFTR), leading to d

207 s caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR), of which the

208 t VX-809, a corrector of the cystic fibrosis transmembrane conductance regulator (CFTR), reduces cyst

209 in Cl(-) extrusion, such as cystic fibrosis transmembrane conductance regulator (CFTR), should reduc

210 illustrate that disrupted function of the CF transmembrane conductance regulator (CFTR), such as that

211 ies targeting defects in the cystic fibrosis transmembrane conductance regulator (CFTR), which are li

212 KEY POINTS: The cystic fibrosis transmembrane conductance regulator (CFTR), which is def

213 the epithelial Cl(-) channel cystic fibrosis transmembrane conductance regulator (CFTR), which is def

214 smembrane channel called the cystic fibrosis transmembrane conductance regulator (CFTR), which regula

215 ts of low serum IGF-1 on the cystic fibrosis transmembrane conductance regulator (CFTR), whose defect

216 brosis (CF) is caused by mutations in the CF transmembrane conductance regulator (CFTR), with approxi

217 Golgi-localized cystic fibrosis transmembrane conductance regulator (CFTR)-associated li

218 assessed by forskolin-induced swelling in CF transmembrane conductance regulator (CFTR)-deficient org

219 % compared with control) and cystic fibrosis transmembrane conductance regulator (CFTR)-dependent and

220 estines that inherently lack cystic fibrosis transmembrane conductance regulator (CFTR)-dependent HCO

221 s, cAMP is known to regulate cystic fibrosis transmembrane conductance regulator (CFTR)-mediated anio

222 partially restored DeltaF508-cystic fibrosis transmembrane conductance regulator (CFTR)-mediated cAMP

223 These drugs activate cystic fibrosis transmembrane conductance regulator (CFTR)-mediated flui

224 ells, motile ciliated cells, cystic fibrosis transmembrane conductance regulator (CFTR)-rich ionocyte

225 e transporter (AlgE) and the cystic fibrosis transmembrane conductance regulator (CFTR).

226 se (PKG), and opening of the cystic fibrosis transmembrane conductance regulator (CFTR).

227 ATP-gated anion channel, the cystic fibrosis transmembrane conductance regulator (CFTR).

228 lls expressing the misfolded cystic fibrosis transmembrane conductance regulator (CFTR).

229 ue the trafficking mutant of cystic fibrosis transmembrane conductance regulator (CFTR).

230 e epithelial-cell chloride channel called CF transmembrane conductance regulator (CFTR).

231 e result of mutations in the cystic fibrosis transmembrane conductance regulator (CFTR).

232 secretin receptor, cilia and cystic fibrosis transmembrane conductance regulator (CFTR).

233 c fibrosis (CF) is caused by mutations in CF transmembrane conductance regulator (CFTR).

234 coding for the anion channel cystic fibrosis transmembrane conductance regulator (CFTR).

235 the epithelial anion channel cystic fibrosis transmembrane conductance regulator (CFTR).

236 n caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR).

237 f Phe-508 (DeltaF508) in the cystic fibrosis transmembrane conductance regulator (CFTR).

238 pression and function of the cystic fibrosis transmembrane conductance regulator (CFTR).

239 lial Cl(-) secretion via the cystic fibrosis transmembrane conductance regulator (CFTR).

240 e caused by mutations of the cystic fibrosis transmembrane conductance regulator (CFTR).

241 des for a Cl(-) channel, the cystic fibrosis transmembrane conductance regulator (CFTR).

242 binding domain (NBD1) of the cystic fibrosis transmembrane conductance regulator (CFTR).

243 active Cl- secretion via the cystic fibrosis transmembrane conductance regulator (CFTR).

244 ase causing mutations within cystic fibrosis transmembrane conductance regulator (CFTR).

245 e caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR).

246 s caused by mutations of the cystic fibrosis transmembrane conductance regulator (Cftr).

247 ssive disorder affecting the cystic fibrosis transmembrane conductance regulator (CFTR).

248 The cystic fibrosis transmembrane conductance regulator (CFTR, ABCC7), mutat

249 The cystic fibrosis transmembrane-conductance regulator (CFTR) chloride chan

250 ciated degradation (ERAD) of Cystic fibrosis transmembrane-conductance regulator (CFTR) is largely un

251 on through activation of the cystic fibrosis transmembrane conductance regulator, CFTR.

252 n amino acid deletion in the cystic fibrosis transmembrane conductance regulator, CFTR.

253 red an rAAV vector containing a truncated CF transmembrane conductance regulator (CFTRDeltaR) combine

254 denosine 3',5'-monophosphate/cystic fibrosis transmembrane conductance regulator/chloride bicarbonate

255 TT, in deletion of Phe508 in cystic fibrosis transmembrane conductance regulator (DeltaF508 CFTR), th

256 These findings link loss of cystic fibrosis transmembrane conductance regulator-dependent alkaliniza

257 of phenylalanine 508 of the cystic fibrosis transmembrane conductance regulator (F508 CFTR) is the m

258 e used mice deficient in the cystic fibrosis transmembrane conductance regulator gene (Cftr) to test

259 ate gene studies include the cystic fibrosis transmembrane conductance regulator gene (CFTR), as well

260 enetic disease caused by mutations in the CF transmembrane conductance regulator gene (CFTR).

261 almost 2,000 variants in the cystic fibrosis transmembrane conductance regulator gene CFTR have empir

262 d to efficiently deliver the cystic fibrosis transmembrane conductance regulator gene to human airway

263 ed by mutations in the CFTR (cystic fibrosis transmembrane conductance regulator) gene that encodes a

264 phils confirm a role for the cystic fibrosis transmembrane conductance regulator in maintaining HOCl

265 lucose co-transporter-1, and cystic fibrosis transmembrane conductance regulator in the jejunum.

266 ) cells after treatment with cystic fibrosis transmembrane conductance regulator inhibitor CFTR(inh)-

267 ence factors alkaline protease (AprA) and CF transmembrane conductance regulator inhibitory factor (C

268 eruginosa epoxide hydrolase, cystic fibrosis transmembrane conductance regulator inhibitory factor (C

269 tionale: Enhancing non-CFTR (cystic fibrosis transmembrane conductance regulator)-mediated anion secr

270 oncentration of bicarbonate, which mimics CF transmembrane conductance regulator-mediated anion secre

271 TEER) (>400 Ohms.cm(2)), and cystic fibrosis transmembrane conductance regulator-mediated short-circu

272 veolar macrophages from cystic fibrosis (CF) transmembrane conductance regulator(-/-) mice have impai

273 toxemia, unaffected by CFTR (cystic fibrosis transmembrane conductance regulator) modulation, and res

274 acaftor-ivacaftor is a CFTR (cystic fibrosis transmembrane conductance regulator) modulator combinati

275 n of our editase can correct cystic fibrosis transmembrane conductance regulator mRNA, restore full-l

276 As an ion channel, the cystic fibrosis transmembrane conductance regulator must form a continuo

277 y the retention of the CFTR (cystic fibrosis transmembrane conductance regulator) mutant protein in t

278 F lung disease in a manner independent of CF transmembrane conductance regulator mutation.

279 ociliary function in the absence of CFTR (CF transmembrane conductance regulator).Objectives: To test

280 ation with and activation of cystic fibrosis transmembrane conductance regulator, one of its binding

281 zed that transgenic expression of porcine CF transmembrane conductance regulator (pCFTR) cDNA under c

282 Cystic fibrosis transmembrane conductance regulator potentiation by ivac

283 ch was partially reversed by cystic fibrosis transmembrane conductance regulator potentiation with iv

284 e the feasibility of using a cystic fibrosis transmembrane conductance regulator potentiator, ivacaft

285 The Cystic Fibrosis Transmembrane Conductance Regulator protein (CFTR) is a

286 he loss of chloride transport through the CF transmembrane conductance regulator protein (CFTR).

287 -length plasmid encoding the cystic fibrosis transmembrane conductance regulator protein was achieved

288 bed in CF including disabled cystic fibrosis transmembrane conductance regulator recruitment to phago

289 ficient degradation of human cystic fibrosis transmembrane conductance regulator requires function of

290 ) lung disease, the absence of functional CF transmembrane conductance regulator results in Cl(-)/HCO

291 egion Y-box 9+) to a mature (cystic fibrosis transmembrane conductance regulator+/secretin receptor+)

292 ngiocyte functions including cystic fibrosis transmembrane conductance regulator, secretin receptor,

293 embrane K(ATP) channels, the cystic fibrosis transmembrane conductance regulator, the transient recep

294 ing functional defect in the cystic fibrosis transmembrane conductance regulator, there is still an u

295 romone, Ste6* (sterile), and cystic fibrosis transmembrane conductance regulator, undergo Ubr1-depend

296 icate a human-relevant CFTR (cystic fibrosis transmembrane conductance regulator) variant.Objectives:

297 Cystic fibrosis transmembrane conductance regulator was internalized in

298 creased levels of functional cystic fibrosis transmembrane conductance regulator were associated with

299 including the anion channel cystic fibrosis transmembrane conductance regulator, which shunt the tra

300 -fibrosis-associated protein cystic fibrosis transmembrane conductance regulator, which upon deletion