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1 including amyotrophic lateral sclerosis and frontotemporal dementia.
2 s of amyotrophic lateral sclerosis (ALS) and frontotemporal dementia.
3 have previously been associated with risk of frontotemporal dementia.
4 lbeing of family caregivers of patients with frontotemporal dementia.
5 ene causes amyotrophic lateral sclerosis and frontotemporal dementia.
6 c cause of amyotrophic lateral sclerosis and frontotemporal dementia.
7 nsufficiency are prevalent genetic causes of frontotemporal dementia.
8 the clinicopathological overlap of ALS with frontotemporal dementia.
9 c cause of amyotrophic lateral sclerosis and frontotemporal dementia.
10 clusion body myopathy with Paget disease and frontotemporal dementia.
11 e of amyotrophic lateral sclerosis (ALS) and frontotemporal dementia.
12 ive diseases such as Alzheimer's disease and frontotemporal dementia.
13 genesis of amyotrophic lateral sclerosis and frontotemporal dementia.
14 ntify whether such changes could be shown in frontotemporal dementia.
15 ms in asymptomatic adults at risk of genetic frontotemporal dementia.
16 ic criteria for possible behavioural-variant frontotemporal dementia.
17 Genetics is an important risk factor for frontotemporal dementia.
18 f familial amyotrophic lateral sclerosis and frontotemporal dementia.
19 sources were impaired by behavioural variant frontotemporal dementia.
20 l forms of amyotrophic lateral sclerosis and frontotemporal dementia.
21 h familial amyotrophic lateral sclerosis and frontotemporal dementia.
22 nificantly attenuated by behavioural variant frontotemporal dementia.
23 c cause of amyotrophic lateral sclerosis and frontotemporal dementia.
24 d to amyotrophic lateral sclerosis (ALS) and frontotemporal dementia.
25 he most frequent genetic causes of inherited frontotemporal dementia.
26 nism, or a predominant behavioral variant of frontotemporal dementia.
27 orf72 can present with MSA as well as ALS or frontotemporal dementia.
28 ding amyotrophic lateral sclerosis (ALS) and frontotemporal dementia.
29 lusively in social and emotion processing in frontotemporal dementia.
30 S or related TDP-43 proteinopathies, such as frontotemporal dementia.
31 nd the accepted relationship between ALS and frontotemporal dementia.
32 course in a discussion of behavioral variant frontotemporal dementia.
33 ead to multisystem proteinopathies including frontotemporal dementia.
34 s, and include Alzheimer disease and certain frontotemporal dementias.
35 hort of 19 patients with behavioural variant frontotemporal dementia, 13 with Alzheimer's disease and
36 esented 28 patients with behavioural variant frontotemporal dementia, 14 patients with semantic varia
37 istics of family caregivers of patients with frontotemporal dementia, (2) explore the impact of provi
38 icularly associated with behavioural variant frontotemporal dementia (40% of symptomatic cases) and h
39 articularly prevalent in behavioural variant frontotemporal dementia (71% of cases) and semantic deme
40 d the patients with vascular dementia (91%), frontotemporal dementia (94%), Parkinson's disease demen
41 generative lesion model: behavioural variant frontotemporal dementia, a condition characterized by gr
42 ia, are a common autosomal dominant cause of frontotemporal dementia, a neurodegenerative disease com
43 65-year-old female with behavioural variant frontotemporal dementia accompanied by focal degeneratio
44 fects, respectively, in clinical subtypes of frontotemporal dementia against neurologically normal co
46 ng Alzheimer's disease; tauopathies, such as frontotemporal dementia; alpha-synucleinopathies, such a
47 with amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (ALS-FTD) showed reduced motor a
50 myotrophic lateral sclerosis with associated frontotemporal dementia (ALS/FTD) are major neurodegener
51 d with the spectrum of familial and sporadic frontotemporal dementia-amyotrophic lateral sclerosis (F
53 ticle other mutations were reported to cause frontotemporal dementia-amyotrophic lateral sclerosis sy
54 rt of 21 families with pathologically proven frontotemporal dementia-amyotrophic lateral sclerosis.
55 gnosis of Alzheimer's disease (AD, n = 289), frontotemporal dementia/amyotrophic lateral sclerosis (F
56 hy associated with Paget disease of bone and frontotemporal dementia/amyotrophic lateral sclerosis.
57 roup of 25 patients with behavioural variant frontotemporal dementia and 21 control subjects, diagnos
58 Game in 22 patients with behavioural variant frontotemporal dementia and 22 age-matched controls, to
59 articipating in the Genetic Investigation in Frontotemporal Dementia and Alzheimer's Disease (GIFT) S
64 ich is both deficient in behavioural variant frontotemporal dementia and closely associated with inhi
65 s did not differ between behavioural variant frontotemporal dementia and controls for pleasant or neu
67 worse memory scores than behavioural variant frontotemporal dementia and did not differ from typical
68 oncept of progranulin-boosting therapies for frontotemporal dementia and highlight an important role
69 thology of amyotrophic lateral sclerosis and frontotemporal dementia and is observed in numerous othe
70 ch has not been tested in an animal model of frontotemporal dementia and it is unclear if boosting pr
72 tiple neurodegenerative disorders, including frontotemporal dementia and parkinsonism linked to chrom
74 ificantly higher risk for clinically defined frontotemporal dementia and progressive supranuclear pal
76 st analysis restricted to behavioral variant frontotemporal dementia and semantic variant primary pro
78 vioural disinhibition in behavioural variant frontotemporal dementia and the effect of selective sero
79 s were lower compared to behavioural variant frontotemporal dementia and typical Alzheimer's disease.
80 ith C9orf72 in amyotrophic lateral sclerosis/frontotemporal dementia and with polyglutamine diseases,
81 yndrome shares pathobiological features with frontotemporal dementia and, indeed, many patients show
82 GGGGCC repeat expansion in C9orf72 leads to frontotemporal dementia and/or amyotrophic lateral scler
83 rrying a C9orf72 repeat expansion leading to frontotemporal dementia and/or amyotrophic lateral scler
84 9 developed dementia due to AD, 2 developed frontotemporal dementia, and 1 developed moderate dement
86 changes are prevalent in behavioural variant frontotemporal dementia, and are associated with changes
87 of APOE and TOMM40 with behavioural variant frontotemporal dementia, and ARHGAP35 and SERPINA1 with
88 is uniquely impaired in behavioural variant frontotemporal dementia, and may explain other common fe
89 rd-seeking behaviours in behavioural variant frontotemporal dementia, and may relate to degeneration
90 implicated in amyotrophic lateral sclerosis, frontotemporal dementia, and multisystem proteinopathy-d
91 with Alzheimer's disease, behavioral variant frontotemporal dementia, and other neuropsychiatric cond
93 results showed that Alzheimer's disease and frontotemporal dementia are associated with distinct and
98 n in amyotrophic lateral sclerosis (ALS) and frontotemporal dementia, but it is unknown whether loss
99 M106B are thought to modify disease onset in frontotemporal dementia, but its relation to myelination
100 portion of patients with behavioural variant frontotemporal dementia (bvFTD) develop amyotrophic late
101 lzheimer disease (AD) and behavioral variant frontotemporal dementia (bvFTD) in individual patients b
103 agnosis in patients with behavioural variant frontotemporal dementia (bvFTD) poses a daunting challen
104 ypic heterogeneity within behavioral variant frontotemporal dementia (bvFTD) will help uncover underl
105 were diagnosed with (1) behavioural variant frontotemporal dementia (bvFTD), (2) right temporal vari
106 AD), 171 patients with behavioral variant of frontotemporal dementia (bvFTD), 89 patients with semant
107 of the core features of behavioural variant frontotemporal dementia (bvFTD), a neurodegenerative dis
109 on (EF) in patients with behavioural variant frontotemporal dementia (bvFTD), primary progressive aph
110 eria for the diagnosis of behavioral variant frontotemporal dementia (bvFTD), yet their occurrence in
111 hat exists between early behavioural variant frontotemporal dementia (bvFTD)--the most common clinica
116 mutations, and 79 FTD (45 behavioral variant frontotemporal dementia [bvFTD], 18 progressive nonfluen
117 n cause of amyotrophic lateral sclerosis and frontotemporal dementia (C9ALS/FTD), however, the precis
121 associated amyotrophic lateral sclerosis and frontotemporal dementia (C9RAN) and at CGG repeats that
123 e inhibition deficits in behavioural variant frontotemporal dementia can be partially restored by inc
124 iation studies on 3348 clinically identified frontotemporal dementia cases and 9390 controls (discove
125 neuron disease, cognitive decline resembling frontotemporal dementia, cerebellar ataxia and myopathy.
126 lying neuropathological entities lead to the frontotemporal dementia clinical phenotype, all of which
127 avioural profile than in behavioural variant frontotemporal dementia, co-occurrence of memory dysfunc
128 observational study, 90 patients meeting the Frontotemporal Dementia Consortium consensus criteria fo
129 ed resting heart rate in behavioural variant frontotemporal dementia correlated with atrophy involvin
130 , such as Alzheimer's disease, some cases of frontotemporal dementia, corticobasal degeneration and p
132 racterisation have increased the accuracy of frontotemporal dementia diagnosis, thus allowing for the
133 Though patients with behavioural variant frontotemporal dementia display changes in their pursuit
134 ncluding stroke, traumatic brain injury, and frontotemporal dementia, disrupt emotional empathy-the a
136 , we describe two illuminating patients with frontotemporal dementia due to the C9orf72 repeat expans
137 -like phenotypes and a behavioral variant of frontotemporal dementia, especially when a familial hist
138 me C9orf72 carriers with behavioural variant frontotemporal dementia exhibit distinctive atrophy patt
141 n Alzheimer's disease and behavioral variant frontotemporal dementia, focusing on the divergent impac
142 luding C9ORF72 amyotrophic lateral sclerosis/frontotemporal dementia, fragile X tremor ataxia syndrom
143 s of amyotrophic lateral sclerosis (ALS) and frontotemporal dementia-frontotemporal lobar degeneratio
144 ]; median age, 62.5 years), 20 patients with frontotemporal dementia (FTD) (8 men [4.5%] and 12 women
146 ns in C9ORF72, are abundant in patients with frontotemporal dementia (FTD) and amyotrophic lateral sc
147 72) gene is the most common genetic cause of frontotemporal dementia (FTD) and amyotrophic lateral sc
148 protein homeostasis have been identified in frontotemporal dementia (FTD) and amyotrophic lateral sc
149 nsions are the most common cause of familial frontotemporal dementia (FTD) and amyotrophic lateral sc
151 ial function has been found in patients with frontotemporal dementia (FTD) and amyotrophic lateral sc
152 ), yet their occurrence in other subtypes of frontotemporal dementia (FTD) and effect on metabolic he
153 er's disease (AD), Lewy body dementia (LBD), frontotemporal dementia (FTD) and Huntington's disease (
154 of patients with Alzheimer's disease (AD) or frontotemporal dementia (FTD) and matched cognitively no
155 tations in C9ORF72 are an important cause of frontotemporal dementia (FTD) and motor neuron disease.
156 Amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD) are age-related neurodegen
157 Amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD) are overlapping neurodegen
158 Amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD) are overlapping, fatal neu
159 Amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD) are progressive neurodegen
160 Amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD) are related neurodegenerat
161 viewed all neuroimaging studies of apathy in frontotemporal dementia (FTD) attempting to refine a neu
162 are similar to Alzheimer's disease (AD) and frontotemporal dementia (FTD) cases, and LSD1 is specifi
165 profiling to demonstrate that deficiency in frontotemporal dementia (FTD) gene progranulin (Grn) lea
172 ing PGRN levels in iPSC neurons derived from frontotemporal dementia (FTD) patients with PGRN deficie
173 e in amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD) presents a significant res
175 ese features in Alzheimer's disease (AD) and frontotemporal dementia (FTD) spectrum disorders, at fir
176 ations in MAPT that alter tau splicing cause frontotemporal dementia (FTD) with tau pathology, provid
178 s having ALS with normal cognition, ALS with frontotemporal dementia (FTD), ALS with executive or non
179 logical and genetic overlap between sporadic frontotemporal dementia (FTD), Alzheimer's disease (AD)
180 disease (PD) and Huntington's disease (HD), frontotemporal dementia (FTD), amyotrophic lateral scler
181 ations in GRN, the gene encoding PGRN, cause frontotemporal dementia (FTD), and a GRN SNP confers sig
182 h AD, 20 patients with DM2, 16 patients with frontotemporal dementia (FTD), and matched case control
183 ive diseases such as Alzheimer disease (AD), frontotemporal dementia (FTD), and progressive supranucl
185 d in amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD), as it was demonstrated th
186 LS) exhibit cognitive deficits indicative of frontotemporal dementia (FTD), suggesting a common patho
188 from amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD), two diseases commonly see
189 various neurodegenerative diseases including frontotemporal dementia (FTD), which can be caused by mu
190 eating behaviors are common in patients with frontotemporal dementia (FTD), yet their exact prevalenc
217 al ALS (fALS), sporadic ALS (sALS), ALS with frontotemporal dementia (FTD-ALS), and Alzheimer's disea
219 Other neurodegenerative diseases, such as frontotemporal dementia (FTD; n = 30), Parkinson's disea
220 that is associated with a hereditary form of frontotemporal dementia (FTD3) disrupts the endosomal-ly
221 In addition, CNVs encompassing two known frontotemporal dementia genes, CHMP2B and MAPT were foun
223 generation of human neuron models of AD and frontotemporal dementia have pointed to pathologic pathw
224 disease, amyotrophic lateral sclerosis, and frontotemporal dementia have several important features
225 ss) can be maintained in behavioural variant frontotemporal dementia; however, more complex normative
226 inclusion body myopathy, Paget disease with frontotemporal dementia (IBMPFD) and other neurodegenera
228 the understanding of the molecular basis for frontotemporal dementia improves, rational therapies are
229 e 9-linked amyotrophic lateral sclerosis and frontotemporal dementia in 2011, a plethora of studies h
230 body myopathy, Paget's disease of bone, and frontotemporal dementia in humans unfolds substrate fast
231 symptomatic treatment of behavioural variant frontotemporal dementia including serotonergic strategie
232 E-locus association with behavioural variant frontotemporal dementia indicates its potential risk-inc
237 ly been established that behavioural variant frontotemporal dementia is associated with abnormal eati
240 4 we described an Irish-American family with frontotemporal dementia linked to chromosome 17 associat
241 A>C variant is a mutation and that it causes frontotemporal dementia linked to chromosome 17 in this
242 at in some patients with behavioural variant frontotemporal dementia, low volume of subcortical rewar
244 it was hypothesized that behavioural variant frontotemporal dementia might also be associated with al
245 ase 2 was a 74-year-old female with atypical frontotemporal dementia-motor neuron disease who underwe
246 atrophy in presymptomatic carriers of common frontotemporal dementia mutations is affected by both ge
247 sease biomarker-negative behavioural variant frontotemporal dementia (n = 59), and controls (n = 61).
249 gative cases were most often reclassified as frontotemporal dementia, non-amnestic as frontotemporal
250 as frontotemporal dementia, non-amnestic as frontotemporal dementia or corticobasal degeneration, an
251 e the role of p25/Cdk5 in tauopathy, we used frontotemporal dementia patient-derived induced pluripot
253 be a modifier of the age at disease onset in frontotemporal dementia patients with TDP-43 pathology.
254 ehavioural symptoms span a range from ALS to frontotemporal dementia, present an opportunity to evalu
255 rdinal feature of the behavioural variant of frontotemporal dementia, presenting as impulsive and imp
256 t spans behavioural and language variants of frontotemporal dementia, progressive supranuclear palsy
257 r treating or preventing such tauopathies as frontotemporal dementia, progressive supranuclear palsy,
258 n to cause amyotrophic lateral sclerosis and frontotemporal dementia, providing the first suggestion
259 ealed that patients with behavioural variant frontotemporal dementia rated unpleasant odours as less
260 f neuronal progranulin in the development of frontotemporal dementia-related deficits, we generated t
261 ge cohort of presymptomatic subjects bearing frontotemporal dementia-related pathogenic mutations.
263 hometry of patients with behavioural variant frontotemporal dementia revealed that the inability to s
264 ing Alzheimer's disease, behavioural variant frontotemporal dementia, right-temporal frontotemporal d
265 dementia (bvFTD), (2) right temporal variant frontotemporal dementia (rtFTD), (3) semantic variant of
266 iant frontotemporal dementia, right-temporal frontotemporal dementia, semantic variant and non-fluent
267 s or patients with the behavioral variant of frontotemporal dementia share social cognition impairmen
269 s disease, patients with behavioural variant frontotemporal dementia showed more frontal atrophy and
270 entia diagnoses with Alzheimer's disease and frontotemporal dementia showing the greatest difference
271 nt p.A152T was reported as a risk factor for frontotemporal dementia spectrum and Alzheimer's disease
275 the network involved in eating behaviour in frontotemporal dementia, suggesting a complex interactio
278 on may contribute to the behavioural variant frontotemporal dementia syndrome in C9orf72 carriers by
281 models of amyotrophic lateral sclerosis and frontotemporal dementia, that TDP-43 impairs the inducti
282 ), and two mutant forms linked with familial frontotemporal dementia, the deletion mutant DeltaK280 a
283 e of amyotrophic lateral sclerosis (ALS) and frontotemporal dementia, though the mechanisms by which
285 lthcare providers who care for patients with frontotemporal dementia to recognize the unique needs of
289 ion score, patients with behavioural variant frontotemporal dementia were less averse to losses than
290 stimulus, patients with behavioural variant frontotemporal dementia were less motivated, and therefo
291 ggest that patients with behavioural variant frontotemporal dementia with or without the C9orf72 expa
292 antic dementia) are two clinical variants of frontotemporal dementia with overlapping but distinct an
293 ranuclear palsy, eight Pick's disease, three frontotemporal dementia with parkinsonism associated wit
294 el expresses a human tau protein bearing two frontotemporal dementia with Parkinsonism linked to chro
297 Double-transgenic mice expressing TTBK1 and frontotemporal dementia with parkinsonism-17-linked P301
300 TB is significantly altered in patients with frontotemporal dementia with TDP-43-positive inclusions
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