ライフサイエンスコーパス: lymphohistiocytosis

1 mining patients with familial hemophagocytic lymphohistiocytosis.

2 erhans cell histiocytosis and hemophagocytic lymphohistiocytosis.

3 veral human diseases, such as hemophagocytic lymphohistiocytosis.

4 phoproliferative disease, and hemophagocytic lymphohistiocytosis.

5 nc13-4 as a cause of familial hemophagocytic lymphohistiocytosis.

6 and virus-associated reactive hemophagocytic lymphohistiocytosis.

7 ied in humans with familial hematophagocytic lymphohistiocytosis.

8 with some cases of CAEBV with hemophagocytic lymphohistiocytosis.

9 ferative disease and familial hemophagocytic lymphohistiocytosis.

10 sing a specific treatment for hemophagocytic lymphohistiocytosis.

11 ficiencies including familial hemophagocytic lymphohistiocytosis.

12 in the development of lethal hemophagocytic lymphohistiocytosis.

13 ted in the setting of primary hemophagocytic lymphohistiocytosis.

14 assified as X-linked familial hemophagocytic lymphohistiocytosis.

15 ce disease in mouse models of hemophagocytic lymphohistiocytosis.

16 a protein mutated in familial hemophagocytic lymphohistiocytosis 3, as a WPB-tethering factor.

17 nt for 20% to 40% of familial hemophagocytic lymphohistiocytosis, a fatal disease of early childhood

18 these genes develop familial hemophagocytic lymphohistiocytosis, a primary immunodeficiency characte

19 mes in childhood survivors of hemophagocytic lymphohistiocytosis after hematopoietic stem cell transp

20 ically suspected diagnosis of hemophagocytic lymphohistiocytosis and found 28 patients with single he

21 AKI is frequent in severe hemophagocytic lymphohistiocytosis and has been attributed to multiorga

22 as been proposed that in both hemophagocytic lymphohistiocytosis and macrophage activation syndrome,

23 Rosai-Dorfman disease and (5) hemophagocytic lymphohistiocytosis and macrophage activation syndrome.

24 preclinical disease models of hemophagocytic lymphohistiocytosis and multiple sclerosis, which are dr

25 ages, is seen in the disorder hemophagocytic lymphohistiocytosis and other inflammatory contexts.

26 y syndromes, however, such as hemophagocytic lymphohistiocytosis and the newly classified proteasome

27 cciniforme-like lymphoma with hemophagocytic lymphohistiocytosis, and 2 had EBV-positive smooth muscl

28 fy the frequency of secondary hemophagocytic lymphohistiocytosis, and the main prognostic factors for

29 mmary, childhood survivors of hemophagocytic lymphohistiocytosis are at risk of long-term cognitive a

30 ies in patients with familial hemophagocytic lymphohistiocytosis are decreased natural killer and cyt

31 some cases of type 2 familial hemophagocytic lymphohistiocytosis, based on the pharmacologic inhibiti

32 d with suspected or diagnosed hemophagocytic lymphohistiocytosis, between January 1, 2000, and August

33 immunodeficiency and a fatal hemophagocytic lymphohistiocytosis caused by impaired function of cytot

34 XBP2 associated with familial hemophagocytic lymphohistiocytosis, CTL and NK cell degranulation were

35 Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis (EBV-HLH).

36 Familial hemophagocytic lymphohistiocytosis (F-HLH) and Griscelli syndrome type

37 as both acquired and familial hemophagocytic lymphohistiocytosis (FHL) forms.

38 Familial hemophagocytic lymphohistiocytosis (FHL) is a genetically determined hy

39 Familial hemophagocytic lymphohistiocytosis (FHL) is a life-threatening disorder

40 Familial hemophagocytic lymphohistiocytosis (FHL) is a rare and often fatal diso

41 Familial hemophagocytic lymphohistiocytosis (FHL) is a rare, genetically heterog

42 Familial hemophagocytic lymphohistiocytosis (FHL) is a rare, rapidly fatal, auto

43 Familial hemophagocytic lymphohistiocytosis (FHL) is an inherited, fatal disorde

44 Familial hemophagocytic lymphohistiocytosis (FHL) is caused by genetic defects i

45 d from patients with familial hemophagocytic lymphohistiocytosis (FHL) to screen for biologic correla

46 m syndromes, such as familial hemophagocytic lymphohistiocytosis (FHL), are lethal disorders caused b

47 eferred to as having familial hemophagocytic lymphohistiocytosis (FHL), have various underlying genet

48 result in a form of familial hemophagocytic lymphohistiocytosis (FHL).

49 been associated with familial hemophagocytic lymphohistiocytosis (FHL).

50 tations cause type 3 familial hemophagocytic lymphohistiocytosis (FHL3), a fatal disease marked by ma

51 ty, and give rise to familial hemophagocytic lymphohistiocytosis (FHL4 or FHL5, respectively).

52 ollectively known as familial hemophagocytic lymphohistiocytosis (FHLH), all associated with various

53 patients with severe forms of hemophagocytic lymphohistiocytosis have been developed.

54 Haemophagocytic syndromes (haemophagocytic lymphohistiocytosis) have a wide range of causes, sympto

55 oped all clinical symptoms of hemophagocytic lymphohistiocytosis (HLH) after infection with lymphocyt

56 vation and the fatal disorder hemophagocytic lymphohistiocytosis (HLH) after infection.

57 ated with a high incidence of hemophagocytic lymphohistiocytosis (HLH) and a lack of lymphoma, sugges

58 atory state characteristic of hemophagocytic lymphohistiocytosis (HLH) and macrophage activation synd

59 Hemophagocytic lymphohistiocytosis (HLH) and macrophage activation synd

60 The clinical syndromes of hemophagocytic lymphohistiocytosis (HLH) and macrophage activation synd

61 ll transplantation (HSCT) for hemophagocytic lymphohistiocytosis (HLH) at the cost of more frequent m

62 Primary hemophagocytic lymphohistiocytosis (HLH) can be caused by biallelic mut

63 Hemophagocytic lymphohistiocytosis (HLH) comprises an emerging spectrum

64 Hemophagocytic lymphohistiocytosis (HLH) is a devastating disorder of u

65 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening disorder

66 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening hyperinf

67 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening immunolo

68 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening syndrome

69 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening syndrome

70 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening syndrome

71 Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening, heterog

72 Hemophagocytic lymphohistiocytosis (HLH) is a rare disorder of immune d

73 Hemophagocytic lymphohistiocytosis (HLH) is a rare disorder with famili

74 Hemophagocytic lymphohistiocytosis (HLH) is a rare inflammatory disorde

75 Hemophagocytic lymphohistiocytosis (HLH) is a rare life-threatening dis

76 Familial hemophagocytic lymphohistiocytosis (HLH) is a rare primary immunodefici

77 Hemophagocytic lymphohistiocytosis (HLH) is a rare syndrome of uncontro

78 Hemophagocytic lymphohistiocytosis (HLH) is a severe inflammatory condi

79 Hemophagocytic lymphohistiocytosis (HLH) is a syndrome of pathologic im

80 Hemophagocytic lymphohistiocytosis (HLH) is an immune dysregulatory syn

81 Hemophagocytic lymphohistiocytosis (HLH) is an inborn disorder of immun

82 forms from secondary forms of hemophagocytic lymphohistiocytosis (HLH) is crucial for treatment decis

83 Frequently fatal, primary hemophagocytic lymphohistiocytosis (HLH) occurs in infancy resulting fr

84 consequences, including fatal hemophagocytic lymphohistiocytosis (HLH) triggered predominantly by Eps

85 the outcomes of patients with hemophagocytic lymphohistiocytosis (HLH) undergoing allogeneic hematopo

86 AS bears strong similarity to hemophagocytic lymphohistiocytosis (HLH), and some authors prefer the t

87 xolitinib in murine models of hemophagocytic lymphohistiocytosis (HLH), and the HLH-sibling macrophag

88 develop clinical features of hemophagocytic lymphohistiocytosis (HLH), but do so when infected with

89 scribed in some patients with hemophagocytic lymphohistiocytosis (HLH), but the role of perforin defe

90 e-threatening immune disorder hemophagocytic lymphohistiocytosis (HLH), characterized by uncontrolled

91 It is clinically similar to hemophagocytic lymphohistiocytosis (HLH), which is caused by viral infe

92 mmune regulation and underlie hemophagocytic lymphohistiocytosis (HLH), which requires hematopoietic

93 racterize 2 novel monoallelic hemophagocytic lymphohistiocytosis (HLH)-associated mutations affecting

94 ferative disorders, including hemophagocytic lymphohistiocytosis (HLH).

95 can have features of reactive hemophagocytic lymphohistiocytosis (HLH).

96 xicity predispose patients to hemophagocytic lymphohistiocytosis (HLH).

97 iTE antibodies and leading to hemophagocytic lymphohistiocytosis (HLH).

98 r earlier reports of familial hemophagocytic lymphohistiocytosis (HLH).

99 inflammatory disorder called hemophagocytic lymphohistiocytosis (HLH).

100 ns of hemophagocytic syndrome/hemophagocytic lymphohistiocytosis (HLH).

101 ence of reversible AKI due to hemophagocytic lymphohistiocytosis-induced activated macrophage infiltr

102 he better understood familial hemophagocytic lymphohistiocytosis is a constellation of rare, autosoma

103 Hemophagocytic lymphohistiocytosis is a disease of abnormally activated

104 Hemophagocytic lymphohistiocytosis is a hyperinflammatory disorder resu

105 Hemophagocytic lymphohistiocytosis is a life-threatening disorder chara

106 The hemophagocytic lymphohistiocytosis is probably underdiagnosed in the IC

107 ant infectious mononucleosis, hemophagocytic lymphohistiocytosis, lymphoproliferative disease, organo

108 imately one third of familial hemophagocytic lymphohistiocytosis patients, these immunologic abnormal

109 asma cell hepatitis, familial hemophagocytic lymphohistiocytosis, pediatric nonalcoholic fatty liver

110 In familial hemophagocytic lymphohistiocytosis, Prf-deficient infants suffer a fata

111 included in a postinfectious hemophagocytic lymphohistiocytosis setting.

112 ymphoproliferative disorders, hemophagocytic lymphohistiocytosis, solid tumors, and other diseases.

113 phage activation syndrome and hemophagocytic lymphohistiocytosis still remain to be determined.

114 acrophage activation syndrome/hemophagocytic lymphohistiocytosis, such as interleukin (IL)-10 and IL-

115 sms, possibly integrated into hemophagocytic lymphohistiocytosis syndrome, of infectious origin in th

116 ll dysfunction leading to the hemophagocytic lymphohistiocytosis syndromes.

117 um of diseases, from familial hemophagocytic lymphohistiocytosis to an increased risk of tumorigenesi

118 are associated with familial hemophagocytic lymphohistiocytosis type 3 (FHL3).

119 mutation of which in familial hemophagocytic lymphohistiocytosis type 3 results in a profound defect

120 escribe a child with familial hemophagocytic lymphohistiocytosis type 3 who developed AKI requiring p

121 man immunodeficiency familial hemophagocytic lymphohistiocytosis type 3.

122 e strains and from a Familial Hemophagocytic Lymphohistiocytosis type 4 (FHL4) patient.

123 1 deficiency develop familial hemophagocytic lymphohistiocytosis type 4 (FHL4), a life-threatening di

124 Familial hemophagocytic lymphohistiocytosis type 5 (FHL5) is caused by defects i

125 sis of patients with familial hemophagocytic lymphohistiocytosis type 5 has identified the E132A muta

126 regulation disorder, familial hemophagocytic lymphohistiocytosis (type 2 FHL, FHL2).

127 eating children with familial hemophagocytic lymphohistiocytosis using reduced intensity conditioning

128 e have been found in familial hemophagocytic lymphohistiocytosis, which shares some features with CAE

129 A liver biopsy showed hemophagocytic lymphohistiocytosis with exuberant infiltrates of CD8+ T