ライフサイエンスコーパス: mitochondrial protein

1 orts regarding REEP1 being either an ER or a mitochondrial protein.

2 ative, MPV17L2, which is also annotated as a mitochondrial protein.

3 cell size and lipid content and increases in mitochondrial proteins.

4 sult from mutations affecting many different mitochondrial proteins.

5 as binding nuclear-encoded mRNAs specifying mitochondrial proteins.

6 in (Dox)-cardiotoxicity via deacetylation of mitochondrial proteins.

7 ediators, specific transcription factors and mitochondrial proteins.

8 -3 arginine processing motif of a number of mitochondrial proteins.

9 = 6) (versus controls; n = 6), including two mitochondrial proteins.

10 DNA or mutations in nuclear genes coding for mitochondrial proteins.

11 pecifically binds a subset of mRNAs encoding mitochondrial proteins.

12 ecificity and includes nine newly discovered mitochondrial proteins.

13 logy by mediating the deglutathionylation of mitochondrial proteins.

14 nction may be the result of dysregulation of mitochondrial proteins.

15 and restored the expression and function of mitochondrial proteins.

16 Patients were deficient in lipoylation of mitochondrial proteins.

17 lates thousands of nuclear, cytoplasmic, and mitochondrial proteins.

18 by transient alterations in contractile and mitochondrial proteins.

19 tochondrial function through upregulation of mitochondrial proteins.

20 tochondrion-associated ER membrane (MAM) and mitochondrial proteins.

21 g in simultaneous rescue of the loss of both mitochondrial proteins.

22 s normal transcript levels at genes encoding mitochondrial proteins.

23 As in BJAB cells, mitochondrial proteins accumulated in BCR-stimulated cel

24 eeding, the rate of fatty acid oxidation and mitochondrial protein acetylation are invariably enhance

25 itochondrial function by not only repressing mitochondrial protein acetylation but also enhancing PPA

26 The therapeutic effects of normalizing mitochondrial protein acetylation by expanding the NAD(+

27 d AEC SIRT3 protein expression and increased mitochondrial protein acetylation, including MnSOD(K68)

28 (GCN5L1) protein has been shown to modulate mitochondrial protein acetylation, mitochondrial content

29 esponses whereas expression of RNAs encoding mitochondrial proteins after Ang II administration was m

30 emical uncoupling of mitochondria, increased mitochondrial-protein aging, and accumulation of p62/SQS

31 hondrial function, following deletion of the mitochondrial protein AIF, OPA1, or PINK1, as well as ch

32 d vesicles, which mediate the degradation of mitochondrial proteins and contribute to mitochondrial q

33 under heat shock contain both cytosolic and mitochondrial proteins and interact with the mitochondri

34 per-mitophagy, assessed as ubiquitination of mitochondrial proteins and mitochondrial association of

35 al proteins showed short half-lives, whereas mitochondrial proteins and other energy production enzym

36 tely 500 new or previously unconfirmed plant mitochondrial proteins and outlines a facile strategy fo

37 enzymes responsible for cycling O-GlcNAc on mitochondrial proteins and studied the mitochondrial tra

38 nal mechanisms controlling the expression of mitochondrial proteins and suggest novel strategies to t

39 biased, near-comprehensive identification of mitochondrial proteins and their modified forms.

40 CLUH is coregulated both with genes encoding mitochondrial proteins and with genes involved in riboso

41 or PTEN-induced putative kinase 1 (PINK1), a mitochondrial protein, and the cytosolic innate immune p

42 ase: Dld2, which, as its human homolog, is a mitochondrial protein, and the cytosolic protein Dld3.

43 nes (the chloroplast rubisco protein, mammal mitochondrial proteins, and an influenza virus polymeras

44 analysis and Western blot analysis for some mitochondrial proteins, and Parkin KO mice were protecte

45 phology, slow growth, reduced lipoylation of mitochondrial proteins, and the hyperaccumulation of pho

46 a cell death characterized by the release of mitochondrial proteins, apoptosis-inducing factor, and c

47 Mitochondrial proteins are coded by nuclear (nDNA) and m

48 Nearly all mitochondrial proteins are coded by the nuclear genome a

49 We have previously shown that heart mitochondrial proteins are hyperacetylated in OVE26 mice

50 Most mitochondrial proteins are imported through the TIM23 tr

51 Nearly all mitochondrial proteins are nuclear-encoded and are targe

52 Most mitochondrial proteins are nuclearly encoded and are imp

53 O-GlcNAcomic profiling finds that over 88 mitochondrial proteins are O-GlcNAcylated, with the oxid

54 e-third of the protein domains identified in mitochondrial proteins are only rarely found in bacteria

55 Most of the >1,000 different mitochondrial proteins are synthesized as precursors in

56 Mitochondrial proteins are synthesized on cytosolic ribo

57 The majority of mitochondrial proteins are synthesized with amino-termin

58 The majority of mitochondrial proteins are targeted to mitochondria by N

59 Mitochondrial proteins are targeted to the intermembrane

60 bly by temporarily limiting synthesis of new mitochondrial proteins as cells adapt to the stress.

61 t of structurally and functionally unrelated mitochondrial proteins as substrates of the SUMO pathway

62 ned the expression pattern of UCP1 and other mitochondrial proteins as well as analyzed mtDNA content

63 ced in high glucose-1 (IHG-1) is a conserved mitochondrial protein associated with diabetic nephropat

64 Tom22 forms a 500-kDa complex with mitochondrial proteins associated with 3betaHSD2.

65 o far no direct role for a specific lipid in mitochondrial protein biogenesis has been shown.

66 nce of aggregation-prone Abeta peptides with mitochondrial protein biogenesis represents a crucial as

67 anner, revealing an unexpected connection of mitochondrial protein biogenesis to metabolite transport

68 the synthesis of a subset of nuclear-encoded mitochondrial proteins by cytosolic ribosomes on the mit

69 ic modification of nuclear, cytoplasmic, and mitochondrial proteins by O-linked beta-N-acetyl-D-gluco

70 tidase55 (ICP55) plays a role in stabilizing mitochondrial proteins by the removal of single amino ac

71 man genetics, we have identified a conserved mitochondrial protein, C1orf31/COA6, and shown its requi

72 These data indicate that cardiac mitochondrial proteins can be target autoantigens in myo

73 ochondrial dysfunction and exhibit decreased mitochondrial protein carbonylation and UCP2-dependent r

74 al modification of nuclear, cytoplasmic, and mitochondrial proteins catalyzed exclusively by OGT.

75 es between hESCs and hiPSCs, we identified a mitochondrial protein, CHCHD2, whose expression seems to

76 ell, Cole and colleagues report a non-mutant mitochondrial protein (ClpP) that is overexpressed in a

77 We analyzed partial sequences of three mitochondrial protein-coding genes (COI, ND2 and CytB) a

78 A Bayesian dated phylogeny, based on the 13 mitochondrial protein-coding genes, supports a mid-Pleis

79 s and patterns of gene expression across key mitochondrial protein-coding genes.

80 tochondrial biogenesis and expression of the mitochondrial proteins Complex III and IV, consistent wi

81 r X1)-TUFM (Tu translation elongation factor mitochondrial) protein complex, promoting autophagic flu

82 ignificantly lower maximum aerobic capacity, mitochondrial protein content, respiratory complex prote

83 Three sperm mitochondrial proteins copurified with the recombinant,

84 l oxidation and, in particular, oxidation of mitochondrial protein cysteine residues.

85 insulin deficiency were related to increased mitochondrial protein degradation and decreased protein

86 Faster mitochondrial protein degradation rates not only for ICP

87 Import and assembly of mitochondrial proteins depend on a complex interplay of

88 We show that SUMO modification of mitochondrial proteins does not rely on mitochondrial ta

89 otic cell, we investigated the occurrence of mitochondrial protein domains in bacteria and eukaryotes

90 ght-responsive Bax results in the release of mitochondrial proteins, downstream caspase-3 cleavage, c

91 S proteasome and regulating the clearance of mitochondrial proteins during mitophagy.

92 Lineage-specific analysis of mitochondrial protein evolution revealed a significant e

93 to endoplasmic reticulum stress and aberrant mitochondrial protein expression in autophagy-deficient

94 teomics screen, we quantified the changes in mitochondrial protein expression in OGT- and OGA-overexp

95 es genomic and mitochondrial gene mutations, mitochondrial protein expression modifications and alter

96 clear base excision repair (BER) protein, in mitochondrial protein extracts derived from mammalian ti

97 TH1) was reported to accumulate in total and mitochondrial protein extracts during aging.

98 including cytosolic, nuclear, membrane, and mitochondrial protein extracts.

99 quencing (MPS) of 1,034 genes encoding known mitochondrial proteins failed to identify a likely candi

100 nutrient-sensing regulatory node controlling mitochondrial protein folding and metabolic function.

101 ase, we tested whether acetylation-dependent mitochondrial protein folding contributes to this regula

102 oxia and have found that manipulation of the mitochondrial protein folding environment is an effectiv

103 ivation caused reduced quiescence, increased mitochondrial protein folding stress (PFS(mt)), and comp

104 levels of reactive oxygen species (ROS), or mitochondrial protein folding stress, a percentage of AT

105 in response that is activated in response to mitochondrial protein folding stress, a response that is

106 to prolonged fasting, SIRT3 levels modulate mitochondrial protein folding.

107 nd transcription, and TRAP1, which regulates mitochondrial protein folding.

108 isease, promotes mitophagy by ubiquitinating mitochondrial proteins for efficient engagement of the a

109 Inherited deficiency in the mitochondrial protein frataxin (FXN) causes the rare dis

110 isease caused by inherited deficiency of the mitochondrial protein Frataxin (FXN), which has no appro

111 An inherited deficiency of the mitochondrial protein frataxin causes Friedreich's ataxi

112 gene, resulting in reduced expression of the mitochondrial protein frataxin.

113 the diversity displayed in 104 nuclear-coded mitochondrial proteins from 1,092 individuals from the 1

114 ine by pulsing dendritic cells with enriched mitochondrial proteins from RENCA cells.

115 onal interactions for further exploration of mitochondrial protein function.

116 ource should provide molecular insights into mitochondrial protein functions.

117 In addition, all Viscum mitochondrial protein genes have experienced a dramatic

118 to the mitochondria and its interaction with mitochondrial proteins has not been explored.

119 teomics and large scale studies of potential mitochondrial proteins have led to the identification of

120 We found mitochondrial proteins highly involved in HCV infection

121 quality control (IMQC) system is central to mitochondrial protein homeostasis and cellular health.

122 overed a conserved, robust mechanism linking mitochondrial protein homeostasis and the cytosolic fold

123 (UPR(mt)), which includes genes that promote mitochondrial protein homeostasis and the recovery of de

124 ealed roles in the electron transport chain, mitochondrial protein homeostasis, mitophagy, and the fu

125 n its binding partner, Cdc48, contributes to mitochondrial protein homeostasis.

126 terol receptor that recruits Vms1 to support mitochondrial protein homeostasis.

127 lating the NAD(+) salvage pathway suppressed mitochondrial protein hyperacetylation and cardiac hyper

128 We show that mitochondrial protein hyperacetylation due to NAD(+) red

129 Among the mitochondrial proteins identified by gene ontology analy

130 , these results identify NLRX1 as a critical mitochondrial protein implicated in the regulation of ap

131 In particular, mitochondrial proteins implicated in H2S detoxification

132 the connection between Erv1/Mia40-dependent mitochondrial protein import and cytosolic Fe-S cluster

133 e isoforms for many of the components of the mitochondrial protein import apparatus.

134 mplex subunits, demonstrating that deficient mitochondrial protein import causes mutant Htt-induced n

135 interaction between mutant Htt and the TIM23 mitochondrial protein import complex.

136 otects cells from the reduced proliferation, mitochondrial protein import defects, lower mitochondria

137 hondrial function is evaluated by monitoring mitochondrial protein import efficiency of the transcrip

138 dentifies conserved and modified features of mitochondrial protein import in apicomplexan parasites.

139 y, recombinant mutant Htt directly inhibited mitochondrial protein import in vitro.

140 versatility and dynamic organization of the mitochondrial protein import machineries.

141 a central, membrane-embedded subunit of the mitochondrial protein import machinery.

142 can trypanosomiasis, possesses non-canonical mitochondrial protein import machinery.

143 , pATOM36 has a dual function and integrates mitochondrial protein import with mitochondrial DNA inhe

144 complex, is essential for parasite survival, mitochondrial protein import, and assembly of the TOM co

145 nd neuronal pathology, with implications for mitochondrial protein import-based therapies in HD.

146 have identified small molecules that inhibit mitochondrial protein import.

147 that is important for parasite survival and mitochondrial protein import.

148 r results demonstrate that TbTim62, a unique mitochondrial protein in T. brucei, is required for the

149 Expression of selected nuclear-encoded mitochondrial proteins in 2- and 10-month-old YAC128 and

150 usly unknown pathway can selectively degrade mitochondrial proteins in aged and stressed cells withou

151 n-2 (Grx2) modulates the activity of several mitochondrial proteins in cardiac tissue by catalyzing d

152 nges in expression of nuclear genes encoding mitochondrial proteins in human skeletal muscle cells fo

153 d immunofluorescent labelling of neurons and mitochondrial proteins in mouse and human brain tissues

154 have led to the identification of many novel mitochondrial proteins in need of further characterizati

155 ial bioenergetics as well as the increase in mitochondrial proteins in Nox4-deficient lung fibroblast

156 large structures, we were able to visualise mitochondrial proteins in passively cleared tissues to r

157 onstruction microscopy) to visualize several mitochondrial proteins in primary mouse neurons and test

158 -Man glycosites on nuclear, cytoplasmic, and mitochondrial proteins in S. cerevisiae and S. pombe.

159 e of phosphatidic acid (PA) in biogenesis of mitochondrial proteins in Saccharomyces cerevisiae.

160 In particular, damage to mitochondrial proteins in skeletal muscle, which is a lo

161 fy 2,427 cross-linked peptide pairs from 327 mitochondrial proteins in whole, respiring murine mitoch

162 the model detected lowered expression of 80 mitochondrial proteins including subunits of respiratory

163 intracellular domain interacts with multiple mitochondrial proteins, including critical factors assoc

164 1, conserved in the mDRM-targeting region of mitochondrial proteins, including PTEN-induced putative

165 mitochondria and phosphorylates a cluster of mitochondrial proteins, including the complex I (CI) sub

166 ficient cells exhibited decreased GFP-tagged mitochondrial proteins inside the vacuole and decreased

167 Mitochondrial protein interactions and complexes facilit

168 SURF1 encodes an inner membrane mitochondrial protein involved in COX assembly.

169 duced levels of frataxin (FXN), an essential mitochondrial protein involved in the biosynthesis of ir

170 me analyses, we show that the translation of mitochondrial proteins is highly down-regulated in yeast

171 ROS induction by the MPZL3 and FDXR mitochondrial proteins is therefore essential for epider

172 ICP55 also removed single amino acids from mitochondrial proteins known to be cleaved at nonconserv

173 in vivo studies in mice and humans, that the mitochondrial protein LACTB potently inhibits the prolif

174 We show how impaired turnover of de novo mitochondrial proteins leads to aberrant protein accumul

175 nts of DNA repair, anti-oxidant capacity and mitochondrial protein levels (complexes I-V).

176 To enable the assessment of mitochondrial protein levels, we have developed a quadru

177 ased ROS would result in oxidative damage to mitochondrial proteins, lipids, and DNA.

178 a comprehensive central resource for data on mitochondrial protein localisation.

179 We show that CHCHD10 is a mitochondrial protein located in the intermembrane space

180 lated with hyperacetylation of IDH2 and SOD2 mitochondrial proteins, lowered enzymatic activities, an

181 transition from cold to warmth, and no other mitochondrial proteins matched UCP1.

182 with specialized/enriched functions, such as mitochondrial protein maturation, thermotolerance, senes

183 al protein Vps13 or by overexpression of the mitochondrial protein Mcp1.

184 These largely consisted of mitochondrial proteins, metabolic regulators, and sarcom

185 iptional modification, and the extent of the mitochondrial protein methylome, the modifying methyltra

186 ity in a manner that is synergistic with the mitochondrial protein Mff, suggesting a role for direct

187 Here we report that human mitochondrial protein Miner2 [2Fe-2S] clusters can bind

188 oxide in the CDGSH-type [2Fe-2S] clusters in mitochondrial protein Miner2 may represent a new nitric

189 us hypoxic injury, we have found evidence of mitochondrial protein misfolding post-hypoxia and have f

190 s of the role of parkin in ubiquitination of mitochondrial proteins, mitochondrial ubiquitination was

191 Titrating expression levels of the mitochondrial protein mitoNEET is a powerful approach to

192 ed large scale loss of the oxidant-sensitive mitochondrial protein Mpv17L.

193 These mtROS damage mitochondrial proteins, mtDNA, and membrane lipids and r

194 mologue (CLUH) regulates the expression of a mitochondrial protein network supporting key metabolic p

195 rameshift mutation in NNT, a nuclear-encoded mitochondrial protein, not implicated previously in huma

196 Herein, we define that the host mitochondrial protein nucleotide-binding oligomerization

197 However, mitochondrial protein O-GlcNAcylation and its effects on

198 Our data reveal widespread and dynamic mitochondrial protein O-GlcNAcylation, serving as a regu

199 MPV17 is a mitochondrial protein of unknown function, and mutations

200 A mitochondrial protein of unknown function, encoded by th

201 ect, it differs from all other characterized mitochondrial proteins of baker's yeast.

202 tent, judged by increased levels of numerous mitochondrial proteins, of the mitochondrial structural

203 onsequences of stress-induced acetylation of mitochondrial proteins on the organelle morphology remai

204 We identified a so far uncharacterized mitochondrial protein (open reading frame YDR381C-A) as

205 ges in mass-specific respiratory capacities, mitochondrial protein or antioxidant content were found.

206 The resulting altered mitochondrial proteins or tumor-associated mitochondrial

207 Reduced mitochondrial protein oxidation in FABP4/aP2(-/-) macrop

208 alpha and uncoupling protein 3, increases in mitochondrial protein oxidation, and hypertrophy decompe

209 ptosis, possibly by binding to the host cell mitochondrial protein p32 (gC1qR).

210 Moreover, SUMOylated forms of mitochondrial proteins particularly accumulate in HSP70-

211 Remarkably, the majority of cycling mitochondrial proteins peaked during the early light pha

212 Here we report that mice deficient for the mitochondrial protein, phosphoglycerate mutase family me

213 had therapeutic properties similar to RENCA mitochondrial protein preparation.

214 volves binding of the ER protein VAPB to the mitochondrial protein PTPIP51, which act as scaffolds to

215 mammalian ATAD1 are conserved members of the mitochondrial protein quality control system that might

216 ther resolubilization nor degradation by the mitochondrial protein quality control system were observ

217 ring stability to the NEFs, helped fine-tune mitochondrial protein quality control, and regulated cru

218 in 70 (mtHsp70), a chaperone contributing to mitochondrial protein quality control.

219 drial DNA (mtDNA) mutations and oxidation of mitochondrial proteins, reactive oxygen species (ROS) le

220 nic deletion in the SLC25A46 gene encoding a mitochondrial protein recently implicated in optic atrop

221 ally TUFM (p = 3.0 x 10(-40)) that encodes a mitochondrial protein regulator of energy balance and in

222 Mitochondrial proteins remain the subject of intense res

223 Mitochondrial proteins require protein machineries calle

224 (OR) = 0.78, P = 4.05 x 10(-11)) encoding a mitochondrial protein required for redox homeostasis; rs

225 , the expression patterns for UCP1 and other mitochondrial proteins resembled each other, whereas in

226 Our study establishes mitochondrial protein sorting as an intervention point f

227 at nonconserved arginine sites, a subset of mitochondrial proteins specific to plants.

228 In vitro, the mitochondrial protein SQR was required for H2S-mediated

229 possibly, other mitochondrial proteins such as ADP/ATP carrier proteins.

230 [4Fe-4S] cluster insertion into a subset of mitochondrial proteins such as lipoate synthase and succ

231 hese changes reflect selective inhibition of mitochondrial protein synthesis (probably translation) w

232 port basic amino acids into mitochondria for mitochondrial protein synthesis and amino acid degradati

233 ial membrane potential, which in turn stalls mitochondrial protein synthesis and fragments the mitoch

234 We previously identified inhibition of mitochondrial protein synthesis as a novel mechanism for

235 ass, ATP production, oxygen consumption, and mitochondrial protein synthesis but did not alter mitoch

236 hich do not display an overall inhibition in mitochondrial protein synthesis but rather have a proble

237 an essential role in determining the rate of mitochondrial protein synthesis by regulating the level

238 e functional rescue of mt-RNA processing and mitochondrial protein synthesis defects after lentiviral

239 nthesis, iron-sulfur cluster biogenesis, and mitochondrial protein synthesis have previously been imp

240 We show that AGs inhibit mitochondrial protein synthesis in mammalian cells and p

241 protein synthesis products revealed impaired mitochondrial protein synthesis in patient fibroblasts.

242 nation and regulation, so quality control of mitochondrial protein synthesis is paramount to maintain

243 Pulse labeling of mitochondrial protein synthesis products revealed impair

244 and consequently, maintenance of the overall mitochondrial protein synthesis rate.

245 ctron transport, mitochondrial dynamics, and mitochondrial protein synthesis were dysregulated.

246 rs metabolic changes in protein translation, mitochondrial protein synthesis, and posttranslational r

247 of impaired mt-RNA processing and defective mitochondrial protein synthesis.

248 (Hyg) inhibits prokaryotic, chloroplast and mitochondrial protein synthesis.

249 ELP3 or NCS6 deletants had impaired mitochondrial protein synthesis.

250 plexes I and IV, and perturbation of de novo mitochondrial protein synthesis.

251 of the S209L mutant to support low levels of mitochondrial protein synthesis.

252 s was selective and did not adversely affect mitochondrial protein synthesis.

253 Overexpression of ABCB8, a mitochondrial protein that facilitates iron export, in v

254 nt optic atrophy (ADOA) are caused by mutant mitochondrial proteins that lead to defects in mitochond

255 inducing post-translational modifications of mitochondrial proteins that regulate mitochondrial dynam

256 25--represent a family of EF-hand-containing mitochondrial proteins that transport Mg-ATP/Pi across t

257 ylome analysis identified a subpopulation of mitochondrial proteins that was sensitive to changes in

258 -dead donors revealed large-scale changes in mitochondrial proteins that were associated with altered

259 sulfur protein family that also includes two mitochondrial proteins: the type II diabetes-related mit

260 Several mitochondrial protein thiols exposed to the mitochondria

261 PfLipL2) that are responsible for activating mitochondrial proteins through the covalent attachment o

262 However, it did delay the clearance of mitochondrial proteins (TIM23, TIM44, and TOM20) and enh

263 in 3 (SIRT3) deacetylates and regulates many mitochondrial proteins to maintain health, but its funct

264 tion and presentation of ubiquitinated sperm mitochondrial proteins to the 26S proteasome, explaining

265 In the MAM, StAR interacts with mitochondrial proteins Tom22 and VDAC2.

266 Most nuclear-encoded mitochondrial proteins traffic from the cytosol to mitoc

267 cles, including decreased levels of specific mitochondrial protein transcripts (RNA) and progressive

268 ent tumors showed elevated expression of the mitochondrial protein translation (MPT) gene pathway rel

269 mal proteins or mitoribosome assembly impair mitochondrial protein translation, causing combined OXPH

270 and tigecycline, an antibiotic that inhibits mitochondrial protein translation, selectively eradicate

271 modifies ribosomal rRNA and is required for mitochondrial protein translation, was markedly reduced

272 Elucidating the molecular mechanisms of mitochondrial protein translocation is crucial for under

273 rs homologues of proteins from all the major mitochondrial protein translocons present in yeast, sugg

274 ally affect the TIM22 and TIM23 complexes in mitochondrial protein transport.

275 The mitochondrial proteins TRAP1 and HTRA2 have previously b

276 A large fraction of mitochondrial proteins typically has detectable homologs

277 ER-resident protein VAPB interacts with the mitochondrial protein tyrosine phosphatase-interacting p

278 ouse livers after APAP treatment followed by mitochondrial protein ubiquitination and mitophagy induc

279 m implicates a role for calcium signaling in mitochondrial protein ubiquitylation, protein turnover,

280 s an important role in clearing mislocalized mitochondrial proteins upon cell stimulation, and its ab

281 The majority of mitochondrial proteins use N-terminal presequences for t

282 of a custom panel including genes coding for mitochondrial proteins was performed in patients with co

283 Mitofusin 2 (Mfn2), a mitochondrial protein, was shown to have antiproliferati

284 83 nuclear mRNAs encoding mitochondrial proteins were changed following 1alpha,25(

285 Expression levels of representative mitochondrial proteins were compared from harvested tiss

286 Interestingly, these mitochondrial proteins were down-regulated in the CTX mo

287 UBQLN1 expression was acutely inhibited, 120 mitochondrial proteins were enriched in the cytoplasm, s

288 BAT both mtDNA content and the expression of mitochondrial proteins were stable and expressed at simi

289 ADCK3 encodes a mitochondrial protein which functions as an electron-tra

290 tion of the vast majority of nuclear-encoded mitochondrial proteins, which is necessary for life at t

291 that SUMO serves as a mark for nonfunctional mitochondrial proteins, which only sporadically arise in

292 SCO1 is a ubiquitously expressed, mitochondrial protein with essential roles in cytochrome

293 A second mitochondrial protein with homology to lipoate ligases,

294 Here, we identified NaSIPP, a mitochondrial protein with phosphate transporter activit

295 TRMT5 encodes a mitochondrial protein with strong homology to members of

296 While FAM136A encodes a mitochondrial protein with unknown function, DTNA encode

297 dampens the transcription of genes encoding mitochondrial proteins with no change to transcript half

298 acts as a sensor to couple the synthesis of mitochondrial proteins with organelle fitness, thus ensu

299 ase that provides an inventory of Drosophila mitochondrial proteins with subcompartmental annotation.

300 s MitoMiner a unique platform to investigate mitochondrial proteins, with application in mitochondria