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1 last 20 years that a substantial portion of nephrotic adults with primary FSGS do respond to treatme
4 modified at a key LPL interacting site into nephrotic Buffalo Mna and Zucker Diabetic Fatty rats red
5 ed ferritin permeability was not observed in nephrotic CD2-associated protein-null (Cd2ap-/-) mice, w
8 xt, the effects of plasma from patients with nephrotic conditions to non-nephrotic conditions were co
11 t, it is in patients who remain persistently nephrotic despite conservative therapy that a more aggre
12 hypercoagulopathy is highly correlated with nephrotic disease severity, but overt thrombosis may req
16 st was shown that exposure to normal and non-nephrotic human plasma leads to a concentration of nephr
19 s over the course of 5-10 years, whereas non-nephrotic patients and those entering a remission have a
20 tium (edema) and the peritoneum (ascites) of nephrotic patients is classically thought to stem from t
24 ed, and the relocation of nephrin induced by nephrotic plasma could be rescued back to the plasma mem
28 tracellular calcium signaling was altered by nephrotic plasma, which was mediated by tyrosine kinase
31 ental glomerulosclerosis (FSGS) often causes nephrotic proteinuria and frequently results in end-stag
34 Rats with puromycin-aminonucleoside-induced nephrotic proteinuria displayed higher renal protein exp
35 e common morphologic feature associated with nephrotic proteinuria was diffuse visceral epithelial ce
38 ed activity were younger (P=0.008), had less nephrotic range proteinuria (P=0.02), and exhibited a hi
39 rrence of FSGS was defined as development of nephrotic range proteinuria between days 3 and 30 posttr
40 hematuria and proteinuria (sometimes in the nephrotic range), and develop chronic kidney disease wit
42 psies were studied, eight from patients with nephrotic-range proteinuria (>/=3 g/d) and 10 from patie
43 improved understanding of the threshold for nephrotic-range proteinuria and the pathogenesis of hype
46 At diagnosis, renal disease was severe, with nephrotic-range proteinuria in 20/46 (43%) patients and
47 ng adolescence (median age, 14.1 years) with nephrotic-range proteinuria in 44% of patients and advan
48 min purified from the urine of patients with nephrotic-range proteinuria inhibits Ca(2+) uptake in TR
51 reases in circulating Angptl4 in response to nephrotic-range proteinuria reduces the degree of this p
52 re confirmed in transgenic mice that develop nephrotic-range proteinuria resulting from podocyte depl
53 s with idiopathic membranous nephropathy and nephrotic-range proteinuria using both indirect immunofl
55 of consanguineous parents with intermittent nephrotic-range proteinuria, we identified a homozygous
57 n of Angptl4 (NPHS2-Angptl4) in rats induced nephrotic-range, and selective, proteinuria (over 500-fo
62 5.7% vs 2.6%; aHR, 2.27; 95% CI, 1.32-3.89), nephrotic syndrome (1.3% vs 0.1%; aHR, 15.7; 95% CI, 2.9
63 logy Damage Index, the greatest frequency of nephrotic syndrome (8.9%) was observed in patients in cl
64 the underlying disease, the severity of the nephrotic syndrome (as assessed by serum albumin concent
68 of podocyte disorders in cases of idiopathic nephrotic syndrome (INS) are complex and remain incomple
69 ritis, type I membranoproliferative GN), and nephrotic syndrome (minimal change/FSGS, membranous neph
71 mutations profile in Brazilian children with nephrotic syndrome (NS) and to determine a genotype-phen
76 nefits of genetic screening of patients with nephrotic syndrome (NS) to diagnose monogenic causes, re
77 Glucocorticoids are the primary therapy for nephrotic syndrome (NS), but have serious side effects a
78 have been identified as monogenic causes of nephrotic syndrome (NS), but important knowledge gaps ex
81 relative risk 4.79; 95% CI 2.71 to 8.46) and nephrotic syndrome (relative risk 7.78; 95% CI 1.80 to 3
83 racterized by the combination of early-onset nephrotic syndrome (SRNS) and microcephaly with brain an
84 yme Q10 biosynthesis cause steroid-resistant nephrotic syndrome (SRNS) as part of multiorgan involvem
87 s reduced in patients with steroid-resistant nephrotic syndrome (SRNS) due to monogenic disorders.
88 n of single-gene causes of steroid-resistant nephrotic syndrome (SRNS) has furthered the understandin
96 ed protein (CD2AP) develop renal failure and nephrotic syndrome about 4 weeks after birth and die aro
97 hallmarks of Pierson syndrome are congenital nephrotic syndrome accompanied by ocular abnormalities,
100 ldren affected by sporadic steroid-resistant nephrotic syndrome and 38 patients who exhibited a simil
101 obtained from (1) the urine of children with nephrotic syndrome and carrying potentially pathogenic m
102 merulosclerosis (FSGS) is a leading cause of nephrotic syndrome and end-stage renal disease worldwide
105 ilial nephropathy in which steroid-sensitive nephrotic syndrome and glomerular deposits of fibrillar
106 erular disorder, manifests clinically with a nephrotic syndrome and has a high propensity for recurre
107 tified in a child with encephalomyopathy and nephrotic syndrome and in a younger sibling with only ne
108 on bilateral transperitoneal nephrectomy for nephrotic syndrome and laparoscopic nephrectomy for Wilm
110 phila orthologs of human monogenic causes of nephrotic syndrome and observed conservation of the cent
113 ng anti-PLA2R antibody levels associate with nephrotic syndrome and progressive loss of kidney functi
117 terations in children with sporadic forms of nephrotic syndrome associate with resistance to steroids
119 hypercoagulopathy to identify patients with nephrotic syndrome at highest risk for thrombotic diseas
120 -LAMB2 missense mutation leads to congenital nephrotic syndrome but only mild extrarenal symptoms; th
121 e to FFAs may function in the development of nephrotic syndrome by amplifying the effects of proteinu
122 sults suggest that the R246Q mutation causes nephrotic syndrome by impairing secretion of laminin-521
125 patients with congenital red hair color and nephrotic syndrome caused by idiopathic membranous nephr
126 insufficiency syndrome and steroid-resistant nephrotic syndrome caused by loss-of-function mutations
128 These data show that diseases that cause nephrotic syndrome change glomerular protein permeabilit
129 erosis (FSGS) is a common form of idiopathic nephrotic syndrome defined by the characteristic lesions
131 , together with the zebrafish model of human nephrotic syndrome generated by plce1 knockdown, open ne
136 eral nephrectomy in patients with congenital nephrotic syndrome have permitted transplantation to be
137 anous nephropathy (MN) is a leading cause of nephrotic syndrome in adults and a significant cause of
138 Membranous nephropathy is a common cause of nephrotic syndrome in adults and can be primary or secon
139 nephropathy (MN) is the most common cause of nephrotic syndrome in adults, and one-third of patients
140 d as one of the leading causes of idiopathic nephrotic syndrome in adults, particularly among African
141 phropathy (MN), a relatively common cause of nephrotic syndrome in adults, were considered idiopathic
142 nephropathy (MN) is the most common cause of nephrotic syndrome in adults, with an uncertain clinical
152 ievable, would likely lessen the severity of nephrotic syndrome in patients carrying LAMB2 mutations.
153 glomerular diseases and induces remission of nephrotic syndrome in patients with diverse glomerulopat
154 tients, and immune-mediated pancytopenia and nephrotic syndrome in the recipient of a double UCB tran
163 e type of glomerular disease that causes the nephrotic syndrome is necessary for appropriate treatmen
169 is dissociation, wild-type mice with induced nephrotic syndrome maintained an intact blood-brain barr
170 that leak through the abnormal glomerulus in nephrotic syndrome may affect tubular transport by inter
171 eatment for the initial episode of childhood nephrotic syndrome may reduce relapse rate, but whether
172 ducing remissions of proteinuria, relapse of nephrotic syndrome occurred significantly more often aft
173 of steroid-dependent or frequently relapsing nephrotic syndrome of minimal change disease (MCD), mesa
174 ce of either nephrin (as in human congenital nephrotic syndrome of the Finnish type, NPHS1) or NEPH1.
175 as either primary or adjunctive therapy for nephrotic syndrome or other diseases treated with glucoc
176 PCSK9 and plasma lipids were studied in nephrotic syndrome patients before and after remission o
177 ckdown of kank2 in zebrafish recapitulated a nephrotic syndrome phenotype, resulting in proteinuria a
179 athogenic circulating permeability factor in nephrotic syndrome remains to be confirmed, we propose i
180 boembolic events with oral anticoagulants in nephrotic syndrome requires a careful case-by-case analy
182 months later, the patient suddenly developed nephrotic syndrome resistant to steroid therapy 1 week a
183 D in relapse and in remission, patients with nephrotic syndrome resulting from other glomerular disea
185 odels of glomerular injury and patients with nephrotic syndrome revealed that calpain-induced talin1
187 tasets derived from 90 black subjects in the Nephrotic Syndrome Study Network (NEPTUNE), stratified b
188 ogenic NS genes in 312 participants from the Nephrotic Syndrome Study Network and 61 putative control
189 f rituximab, a B cell-depleting antibody, in nephrotic syndrome suggests a pathogenic role of B cells
191 ldren (9 months to 17 years) presenting with nephrotic syndrome to either 3 months of prednisolone fo
192 trolled trial in 31 children with idiopathic nephrotic syndrome unresponsive to the combination of ca
193 relationships among different components of nephrotic syndrome use naturally occurring pathways and
198 ients with first manifestation of idiopathic nephrotic syndrome with no immune complexes can improve
199 cause Pierson syndrome, a severe congenital nephrotic syndrome with ocular and neurologic defects.
200 cause Pierson syndrome, a severe congenital nephrotic syndrome with ocular and neurologic defects.
202 THSD7A antibodies into mice induced a severe nephrotic syndrome with proteinuria, weight gain, and hy
205 hose patients with available data, 92% had a nephrotic syndrome, 64% had AKI, and 67% had a documente
209 scribe an infant with severe Leigh syndrome, nephrotic syndrome, and CoQ(10) deficiency in muscle and
210 in steroid-dependent or frequently relapsing nephrotic syndrome, and halted disease-associated growth
211 ry diseases; 2.77 (1.49-5.15) for nephritis, nephrotic syndrome, and nephrosis; 4.08 (1.38-12.08) for
213 odel with which to study the pathogenesis of nephrotic syndrome, and ROS formation may be a pathomech
214 ers, previous immobility, surgery or trauma, nephrotic syndrome, associated tumor, inflammatory disea
215 subset of CD2AP(-/-) mice exhibiting severe nephrotic syndrome, associated with systemic illness.
216 ) collagen developed massive albuminuria and nephrotic syndrome, because of subepithelial deposits of
218 Lamb2(-/-) mice abrogates the development of nephrotic syndrome, correlating with a greatly extended
220 ding patients with congestive heart failure, nephrotic syndrome, diuretic resistance, or generalized
222 were similar to those reported in congenital nephrotic syndrome, Finnish type, that is caused by muta
223 se, a major life-threatening complication of nephrotic syndrome, has been associated with proteinuria
224 target genes, reported as possible causes of nephrotic syndrome, in a cohort of 31 children affected
225 in the epidemiology of steroid-unresponsive nephrotic syndrome, in particular focal segmental glomer
227 g nephrin lead to proteinuria and congenital nephrotic syndrome, indicating that nephrin is essential
228 -brain barrier integrity was correlated with nephrotic syndrome, indicating that these effects are di
229 multiorgan disorder that included congenital nephrotic syndrome, interstitial lung disease, and epide
230 membranous nephropathy, a common form of the nephrotic syndrome, is an antibody-mediated autoimmune g
231 cation of patients with steroid-unresponsive nephrotic syndrome, severity of disease, progression and
232 s central to proteinuric states, such as the nephrotic syndrome, the murine adriamycin nephrosis mode
233 ong the glomerular basement membranes, and a nephrotic syndrome, two additional immunizations were ne
234 CD2AP(-/-) mice normally die by 6 weeks from nephrotic syndrome, we used mice that also express a CD2
235 n during organogenesis results in congenital nephrotic syndrome, whereas VEGF164 overexpression after
236 be single-gene defects-eg, steroid-resistant nephrotic syndrome, which is caused by podocin mutations
237 anous nephropathy is a common cause of adult nephrotic syndrome, with recent evidence suggesting that
238 nhibitors may be beneficial in patients with nephrotic syndrome-associated hypercholesterolemia.
240 nucleoside-induced injury (designed to mimic nephrotic syndrome-related injury), as determined by bot
297 o heart disease, cancer, diabetes, nephritis/nephrotic syndrome/nephrosis, chronic lower respiratory
298 vents; partial and complete remission of the nephrotic syndrome; and a composite of doubling of serum
301 diseases and in other human pathologies with nephrotic syndromes such as HIV and Hantavirus infection
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