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1 microtubule cytoskeletons, leading to motor neuron degeneration.
2 tanding of the complex pathogenesis of motor neuron degeneration.
3 uscular junctions, muscle atrophy, and motor neuron degeneration.
4 optotic pathway, would protect against motor neuron degeneration.
5 ALS and an early disease indicator of motor neuron degeneration.
6 roinflammation as an initiation factor of DA neuron degeneration.
7 ular homeostasis that ultimately cause motor neuron degeneration.
8 neurological disorder characterized by motor neuron degeneration.
9 mic inclusions and predominantly lower motor neuron degeneration.
10 the contiguously progressive nature of motor neuron degeneration.
11 , we show exacerbation of selective striatal neuron degeneration.
12 s that a common mechanism may underlie motor neuron degeneration.
13 be manipulated genetically to suppress motor neuron degeneration.
14 ce, the mouse model of SMARD1, lead to motor neuron degeneration.
15 tical and striatal atrophy and striatal dark neuron degeneration.
16 a central contributor to initiation of motor neuron degeneration.
17 2O2, agents that are known to be involved in neuron degeneration.
18 and are a potential target to prevent motor neuron degeneration.
19 logy for identifying genes relevant to motor neuron degeneration.
20 spinal motor neurons does not provoke motor neuron degeneration.
21 associated with increased olfactory sensory neuron degeneration.
22 unction of p150(glued) and accelerates motor neuron degeneration.
23 on is a potential mechanism for dopaminergic neuron degeneration.
24 in the physiopathological continuum of motor neuron degeneration.
25 a fatal adult human disease caused by motor neuron degeneration.
26 erative disease characterized by lower motor neuron degeneration.
27 ecular-weight heat shock proteins, and focal neuron degeneration.
28 d is implicated in the pathogenesis of motor neuron degeneration.
29 scular disorder characterized by lower motor neuron degeneration.
30 is colocalized with markers of astrocyte and neuron degeneration.
31 t symptoms; none halt or retard dopaminergic neuron degeneration.
32 ibits both adult lethality and photoreceptor neuron degeneration.
33 binding factors in the pathogenesis of motor neuron degeneration.
34 of PEDF as a neuroprotectant in human motor neuron degeneration.
35 r, suggesting a decrease in the extent of DA neuron degeneration.
36 an spastic paraplegia characterized by motor neuron degeneration.
37 nities for understanding mechanisms of motor neuron degeneration.
38 This increase precedes motor neuron degeneration.
39 l Muscular Atrophy (SMA), a disease of motor neuron degeneration.
40 onal excitability were associated with motor neuron degeneration.
41 S inclusions in the cytoplasm triggers motor neuron degeneration.
42 adult-onset muscle weakness and lower motor neuron degeneration.
43 the role of aberrant RNA processing in motor neuron degeneration.
44 , higher numbers of astrocytes, and Purkinje neuron degeneration.
45 triggered chronic ER stress and dopaminergic neuron degeneration.
46 ad to neuronal dysfunction and ultimately to neuron degeneration.
47 ignificant denervation occurs prior to motor neuron degeneration.
48 ed in disease, which contributes to striatal neuron degeneration.
49 S, disrupt RNA processing and initiate motor neuron degeneration.
50 urodegenerative disease resulting from motor neuron degeneration.
51 cated pathological immune responses in motor neuron degeneration.
52 pinal tract degeneration without lower motor neuron degeneration.
53 ing important biochemical processes, such as neuron degeneration.
54 cs, loss of functional motor units and motor neuron degeneration.
55 ubiquitous SMN decrease but selective motor neuron degeneration.
56 ned if 6-hydroxydopamine SN lesions cause PF neuron degeneration.
57 /VCP and genetically distinct forms of motor neuron degeneration.
58 r of alpha-syn accumulation and dopaminergic neuron degeneration.
59 t a necessary step in the emergence of motor neuron degeneration.
60 ction mechanisms, leading to selective motor neuron degeneration.
61 target for therapeutic manipulation in motor neuron degeneration.
62 ir results may help uncover a cause of motor neuron degeneration.
63 damage response, innate immune response and neuron degeneration.
64 ha-syn in vitro, and caused primary cortical neuron degeneration.
65 ination/protein degradation pathway in motor neuron degeneration.
66 sclerosis (ALS) is a fatal disorder of motor neuron degeneration.
67 t observed in a cell line derived from motor neuron degeneration 2 mice that carry a mutated form of
69 the affected males suffer progressive motor neuron degeneration accompanied by signs of androgen ins
70 E is efficacious for thwarting glutamatergic neuron degeneration, alleviating interneuron loss and ab
72 animals also developed age-dependent sensory neuron degeneration, an accumulation of NF subunits in c
73 136 to alanine substitution rescues dopamine neuron degeneration and age-related locomotor deficits i
74 An autopsy study of one patient showed motor neuron degeneration and axonal loss in the ventral horn
78 mB, and to a lesser extent DeltaDomA, caused neuron degeneration and demyelination in mice infected i
79 complete loss of eEF1A2 in mice causes motor neuron degeneration and early death; on the other hand h
80 enes implicated in the pathogenesis of motor neuron degeneration and how this new information is chan
81 l discharges always produced extensive hilar neuron degeneration and immediate granule cell disinhibi
83 d by decreased strength and endurance, motor neuron degeneration and loss, and denervation of muscle.
84 disease phenotype, with spontaneous striatal neuron degeneration and motor deficits, as assessed by r
89 neurological disorder characterized by motor neuron degeneration and progressive muscle paralysis.
90 s extends the VCP phenotype to include motor neuron degeneration and provides another molecular tool
92 termini is a key factor in preventing motor neuron degeneration and that Bchs reveals a functional l
93 endothelial damage accumulated before motor neuron degeneration and the neurovascular inflammatory r
94 peripherin appear to play some part in motor neuron degeneration, and amyotrophic lateral sclerosis i
95 te that neuronal VEGF protects against motor neuron degeneration, and may have therapeutic implicatio
96 Parkinson's disease, including dopaminergic neuron degeneration, and provides a useful model to stud
98 n (alsin) may indicate a mechanism for motor-neuron degeneration, as it may include several cell-sign
100 used in models of ischaemic injury and motor neuron degeneration, both based in part on glutamate tox
101 exhibiting adult-onset upper and lower motor neuron degeneration, but closer examination revealed ear
102 sed to explain how mutant FUS leads to motor neuron degeneration, but neither has been firmly establi
104 microglia and oligodendrocytes promote motor neuron degeneration by inducing inflammation and necropt
105 disorder characterised by progressive motor neuron degeneration) cases are due to mutations in the g
107 (123)I]beta-CIT uptake, a marker of dopamine neuron degeneration, compared with those initially treat
108 reduced body weight but did not induce motor neuron degeneration, defects in motor function, or alter
110 e levels but did not exacerbate dopaminergic neuron degeneration, findings suggesting that basal leve
111 eficiency manifests predominantly with motor neuron degeneration; however, a wealth of emerging data
112 y protected against H(2)O(2)-induced retinal neuron degeneration; however, progesterone had no effect
113 ar mechanisms of TAU- and SOD1-induced motor neuron degeneration identified several new SALS-relevant
114 cient to cause major motor deficits or motor neuron degeneration in a mouse model but predisposes neu
117 at BSCB breakdown contributes to early motor-neuron degeneration in ALS mice and that restoring BSCB
119 s, the pathogenic mechanism underlying motor-neuron degeneration in ALS remains largely obscure.
120 naling pathways that may contribute to motor neuron degeneration in ALS, among which are TGF-beta sig
128 The mechanisms involved in selective motor neuron degeneration in amyotrophic lateral sclerosis rem
129 impair axonal transport and accelerate motor neuron degeneration in amyotrophic lateral sclerosis.
130 esembling apoptosis is responsible for motor-neuron degeneration in amyotrophic lateral sclerosis.
131 cytes have been shown to contribute to motor neuron degeneration in amyotrophic lateral sclerosis.
132 to excitotoxicity that participates in motor neuron degeneration in amyotrophic lateral sclerosis.
133 tochondria macroautophagy impairments and DA neuron degeneration in an in vivo model based on known P
137 de dismutase (SOD1) cause preferential motor neuron degeneration in familial amyotrophic lateral scle
138 oxide dismutase (SOD1) mutants lead to motor neuron degeneration in familial amyotrophic lateral scle
139 superoxide dismutase (SOD1) gene cause motor neuron degeneration in familial amyotrophic lateral scle
140 f BBB and BSCB was evident in areas of motor neuron degeneration in G93A mice at both early and late
141 nein heavy chain result in progressive motor neuron degeneration in heterozygous mice, and in homozyg
142 0(glued) subunit of dynactin can cause motor neuron degeneration in humans and mice, which resembles
145 ated MPTP-induced nigrostriatal dopaminergic neuron degeneration in mice, as well as MPTP-induced JNK
146 ological processes involved in dopamine (DA) neuron degeneration in Parkinson's disease (PD) are not
151 f SBMA using mouse models, the role of motor neuron degeneration in SBMA has not been rigorously inve
153 iron in the spinal cord leads to early motor-neuron degeneration in SOD1(G93A) mice at least in part
154 es indicated a similar extent of lower motor neuron degeneration in SODMutM maintained on DR or ad li
155 hat the mutant mice develop age-dependent DA neuron degeneration in substantia nigra accompanied by a
156 nal consequences of this pathology including neuron degeneration in the absence of neuronal tau inclu
157 (ALS) causes adult-onset, progressive motor neuron degeneration in the brain and spinal cord, result
161 day (E) 6 and E12; whereas, a peak of motor neuron degeneration in the human spinal cord occurs betw
164 light neurofilament (NF-L) RNA causes motor neuron degeneration in transgenic mice, leads to accumul
165 hydrogen peroxide (H(2)O(2))-induced retinal neuron degeneration in vitro, and 2) light-induced photo
166 neurons substantially delayed onset of motor neuron degeneration, increasing disease-free life by 50%
167 neuromuscular phenotype accompanied by motor neuron degeneration, indicating striking recapitulation
168 kout (KO) mice protects against dopaminergic neuron degeneration induced by a mutant human alpha-synu
169 PX4 as a ferroptosis inhibitor, spinal motor neuron degeneration induced by Gpx4 ablation exhibited f
170 e the relationship between RNA oxidation and neuron degeneration induced by various insults, includin
171 le electromyographic evidence of lower motor neuron degeneration into diagnostic criteria has undoubt
172 determine whether nigrostriatal dopaminergic neuron degeneration is associated with changes in PPN me
173 results indicate that the mechanism of GABA neuron degeneration is calcium-dependent and requires ac
175 onset and progression of ALS and that motor neuron degeneration is partially reversible, at least in
177 ular atrophy (SMA) is characterized by motor neuron degeneration, it is unclear whether and how much
178 cular atrophy (SBMA) is a rare form of motor neuron degeneration linked to a CAG repeat expansion in
179 (tg) plus tottering-leaner (tgla), and motor neuron degeneration (mnd) by Northern blot analysis of b
184 similar mechanism has been reported in motor neuron degeneration of amyotrophic lateral sclerosis, ab
186 is a primary cause in the cascade leading to neuron degeneration or a secondary event to cell death.
187 tion of the motor cortex without lower motor neuron degeneration or involvement of other brainstem tr
189 resulting founder (F0) mice developed motor neuron degeneration, others displayed phenotypes consist
190 strating a role of SCYL1 in preventing motor neuron degeneration, our findings clearly establish the
194 manifest progressive, mutant-dependent motor neuron degeneration preceded by early, structural and fu
196 anisms of apoptosis may participate in motor neuron degeneration produced by mutant copper/zinc super
197 anisms of apoptosis may participate in motor neuron degeneration produced by mutant superoxide dismut
198 fatal neurological disease that causes motor neuron degeneration, progressive motor dysfunction, para
202 s also consistent with our finding that GABA neuron degeneration requires the mitochondrial fission g
203 ding mechanisms that lead to selective motor neuron degeneration requires visualization and cellular
205 teral sclerosis (ALS) is a progressive motor neuron degeneration resulting in paralysis and death, us
206 We provide evidence that the photoreceptor neuron degeneration seen in flies expressing mutant huma
207 and hindlimb paralysis associated with motor neuron degeneration, severe muscle wasting, and prematur
208 ophic lateral sclerosis (ALS) involves motor neuron degeneration, skeletal muscle atrophy, paralysis,
210 xonal transport is sufficient to cause motor neuron degeneration such as that observed in amyotrophic
211 den the phenotype of IBMPFD to include motor neuron degeneration, suggest that VCP mutations may acco
212 genic link between ALS2-deficiency and motor neuron degeneration, suggesting a protective role of als
213 ed protein, causes a unique pattern of motor neuron degeneration that is associated with the accumula
215 een independently linked to the dopaminergic neuron degeneration that underlies Parkinson's disease (
217 2O2 rapidly induces DNA-SSB and causes motor neuron degeneration, the occurrence of which is dose and
218 acterized by selective upper and lower motor neuron degeneration, the pathogenesis of which is unknow
219 6-OHDA) is often used in animal models of DA neuron degeneration, there have been relatively few stud
220 and dysfunction of a single U2 snRNA causes neuron degeneration through distortion of pre-mRNA splic
222 euronal connectivity that occur during motor neuron degeneration, we characterized the function and s
223 in/dynactin complex and contributes to motor neuron degeneration, we generated p150(glued) G59S knock
224 ore the link between bioenergetics and motor neuron degeneration, we used a computational model in wh
226 at Zfp106 knockout mice develop severe motor neuron degeneration, which can be suppressed by transgen
227 (ALS) is characterized by progressive motor neuron degeneration, which ultimately leads to paralysis
228 of the Ighmbp2 cDNA prevented primary motor neuron degeneration, while restoring the normal axonal m
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