ライフサイエンスコーパス: noncompaction

1 iomyopathy with features of left ventricular noncompaction.

2 omyopathy, and 23% for left ventricular (LV) noncompaction.

3 nt trabeculations to fulfill criteria for LV noncompaction.

4 oventricular block, and (3) left ventricular noncompaction.

5 ses to pregnancy and are not specific for LV noncompaction.

6 h may be compatible with the diagnosis of LV noncompaction.

7 e develop ventricular hypertrabeculation and noncompaction.

8 rtrophic cardiomyopathy and left ventricular noncompaction.

9 y and diagnosis of isolated left ventricular noncompaction.

10 lar layer in the ventricular wall, so called noncompaction, along with diverse cardiac anomalies, inc

11 ne (ZASP) in a patient with left ventricular noncompaction and conduction disturbances.

12 e cell cycle withdrawal leads to ventricular noncompaction and heart failure.

13 sed to define trabeculae in left ventricular noncompaction and to identify normal racial variations.

14 opment led to heart defect including cardiac noncompaction and ventricular septal defect, which pheno

15 ypertrophic cardiomyopathy, left ventricular noncompaction, and arrhythmogenic right ventricular dysp

16 myopathies are the most common; restrictive, noncompaction, and mixed cardiomyopathies occur infreque

17 ventricular septal defect (VSD), myocardium noncompaction, and ventricular hypertrabeculation.

18 ered cardiomyocyte cell cycling, ventricular noncompaction, and ventricular septal defects, while, in

19 may be the primary disease determinant, with noncompaction arising as a maladaptive remodelling respo

20 all children diagnosed with left ventricular noncompaction at Texas Children's Hospital from January

21 s hypertrophic, dilated and left ventricular noncompaction, but the molecular mechanisms involved in

22 ycardia in association with left ventricular noncompaction cardiomyopathy (LVNC), pointing to a share

23 eported for sinus node dysfunction (SND) and noncompaction cardiomyopathy (NCCM).

24 cycle reentry, with relevance to ventricular noncompaction cardiomyopathy and regenerative medicine.

25 Noncompaction cardiomyopathy is characterized by the pre

26 The human genetics of left ventricular noncompaction cardiomyopathy suggest that cardiomyocyte

27 In this review, left ventricular noncompaction cardiomyopathy, which is often caused by m

28 tures of autosomal dominant left ventricular noncompaction cardiomyopathy.

29 yonic day 10.5 leads to a severe ventricular noncompaction defect associated with reduced cardiomyocy

30 ical to understanding the pathophysiology of noncompaction disease.

31 tiple cardiac defects, including ventricular noncompaction, double outlet right ventricles and ventri

32 Left ventricular noncompaction has a heterogeneous clinical presentation

33 Left ventricular noncompaction has a high mortality rate and is strongly

34 , other genetic and metabolic syndromes with noncompaction have been described.

35 Isolated left ventricular noncompaction (ILVNC) is a cardiomyopathy caused by intr

36 Isolated left ventricular noncompaction (ILVNC) is a cardiomyopathy that was first

37 Left ventricular noncompaction is a cardiomyopathy characterized by exces

38 Left ventricular noncompaction is also observed in families with hypertro

39 onsiderable overlap between left ventricular noncompaction (LVNC) and other cardiomyopathies.

40 Left ventricular noncompaction (LVNC) can occur in isolation or can co-oc

41 linked to gene mutations is left ventricular noncompaction (LVNC) characterized by a typical diffuse

42 Left ventricular noncompaction (LVNC) describes a ventricular wall anatom

43 Whether left ventricular noncompaction (LVNC) is a distinct cardiomyopathy or a m

44 Left ventricular noncompaction (LVNC) is a genetically and phenotypically

45 Isolated left ventricular noncompaction (LVNC) is a myocardial disorder characteri

46 Left ventricular noncompaction (LVNC) is a reportedly uncommon genetic di

47 Left ventricular noncompaction (LVNC) is an autosomal-dominant, genetical

48 ion satisfying criteria for left ventricular noncompaction (LVNC) on routine cardiac magnetic resonan

49 crease our understanding of left ventricular noncompaction (LVNC), a cardiomyopathy characterized by

50 useful for the diagnosis of left ventricular noncompaction (LVNC).

51 ociated with a diagnosis of left ventricular noncompaction (LVNC).

52 ent cardiac MR criteria for left ventricular noncompaction may be necessary.

53 Left ventricular noncompaction may be sporadic or familial and is linked

54 of myocardial dysfunction, left ventricular noncompaction may represent a secondary consequence of a

55 ophic cardiomyopathy (n=2), left ventricular noncompaction (n=1), or long-QT syndrome (n=2).

56 ricular fibrillation (n=4), left ventricular noncompaction (n=2), hypertrophic cardiomyopathy (n=1),

57 lated the ventricular hypertrabeculation and noncompaction observed in Fkbp1a systemically deficient

58 Right ventricular noncompaction occurred in 12 subjects (22.2%).

59 hat mimic a human congenital heart disorder, noncompaction of left ventricular myocardium.

60 Noncompaction of the left ventricle is a descriptive ana

61 al relevance and management of patients with noncompaction of the left ventricle will remain elusive.

62 -linked cardiomyopathy described as isolated noncompaction of the left ventricular myocardium (INVM).

63 ody mutants including hypertrabeculation and noncompaction of the ventricle.

64 null mutation was cardiac failure because of noncompaction of the ventricular myocardium and resultan

65 ations, including ventricular septal defect, noncompaction of the ventricular wall, double-outlet rig

66 ac defects including hypertrabeculation with noncompaction of the ventricular wall.

67 ction, mimicking the pathological changes of noncompaction of ventricular myocardium.

68 of cardiomyopathy and 1 had left ventricular noncompaction on echocardiogram.

69 FG+/phenotype-negative relatives, and 9 with noncompaction or dilated cardiomyopathy.

70 ere diagnosed with isolated left ventricular noncompaction over the study period.

71 All individuals with a noncompaction ratio of >/=2 underwent short axis systoli

72 Long axis noncompaction ratios were the least specific, with curre

73 The left ventricular noncompaction-specific ZASP1 mutation can cause loss of

74 ric remodeling can occur in left ventricular noncompaction subject because of a direct effect of muta

75 yocyte proliferation resulted in ventricular noncompaction that was markedly rescued by heterozygous

76 sed LV trabeculations and the presence of LV noncompaction were based on established criteria.

77 Common sites of noncompaction were the apical (100%), midinferior (74.1%

78 tectural proteins can cause left ventricular noncompaction, which is often associated with conduction

79 other 14-3-3 isoforms but led to ventricular noncompaction, with features similar to LVNC, resulting