1                                              Pleuropulmonary blastoma (PPB) is a rare pediatric lung

2                                       Type I pleuropulmonary blastoma (PPB) is a rare, cystic lung ne

3          There was systemic association with pleuropulmonary blastoma in 2 cases (5%).

4                                              Pleuropulmonary blastoma is a rare childhood malignancy

5                    Systemic association with pleuropulmonary blastoma rarely is found.

6 NAs, have been observed in families with the pleuropulmonary blastoma-family tumor and dysplasia synd

7 ed diseases due to possible evolution toward pleuropulmonary fibrosis and respiratory failure.

8 ay mortality but was associated with reduced pleuropulmonary morbidity (odds ratio (OR) 0.73, P = 0.0

9 ic findings support the concept that classic pleuropulmonary SFT and deep-seated HPC are separate ent

10  NAB2ex4-STAT6ex2/3, corresponded to classic pleuropulmonary SFTs with diffuse fibrosis and mostly be