ライフサイエンスコーパス: pulmonary atresia

1 ogenitors, and embryos predominantly develop pulmonary atresia.

2 r airway was not sufficient for diagnosis of pulmonary atresia.

3 onduit replacement in patients with TOF with pulmonary atresia.

4 nging from mild pulmonary stenosis to severe pulmonary atresia.

5 diac diagnoses were Ebstein's anomaly (40%), pulmonary atresia (11%), and tetralogy of Fallot (8%).

6 Among TOF, 35 (9%) had pulmonary atresia, 98 (26%) had a palliative procedure b

7 patients with cases of TOF, including 3 with pulmonary atresia and 5 with right aortic arch; none had

8 d with the Fontan procedure in patients with pulmonary atresia and an intact ventricular septum and t

9 that occurs in response to Shh knockdown is pulmonary atresia and is directly related to the abnorma

10 on can be performed in >90% of patients with pulmonary atresia and MAPCAs, even those with absent tru

11 It was associated with pulmonary atresia and moderate or severe aortic regurgit

12 rome suffering from tetralogy of Fallot with pulmonary atresia and multiple aortopulmonary collateral

13 ypoplastic left heart (HLH) syndrome, 10 had pulmonary atresia, and 1 had tricuspid atresia.

14 patients (48%) with tetralogy of Fallot and pulmonary atresia, and 4 of 54 (8%) with prosthetic valv

15 TOF with pulmonary stenosis, 24 had TOF with pulmonary atresia, and 6 had TOF with nonconfluent pulmo

16 Male sex, pulmonary atresia, and previous palliations emerged as p

17 In hearts with pulmonary atresia, cardiac neural crest-derived cells, w

18 n=44), primary repair (aged <3 months) with pulmonary atresia (early-PA group; n=49), and primary re

19 onary trunk formation, and that embryos with pulmonary atresia have an outflow tract septum.

20 phenotypic mimic of Tetralogy of Fallot with pulmonary atresia; however, subsequent reports describe

21 resent in 23 subjects and was accompanied by pulmonary atresia in 8.

22 .1% (95% confidence interval, 49.9 to 61.7); pulmonary atresia intact ventricular septum, 55.7% (95%

23 tients with hypoplastic left heart syndrome, pulmonary atresia intact ventricular septum, single vent

24 noses included pulmonary stenosis (n = 433), pulmonary atresia (n = 121), common atrioventricular can

25 rtery stenosis (n = 94), tetralogy of Fallot/pulmonary atresia (n = 72), congenital branch pulmonary

26 oses included tetralogy of Fallot (TOF) with pulmonary atresia (n=13), TOF with pulmonary stenosis (n

27 tresia (n=103), tetralogy of Fallot (n=127), pulmonary atresia (n=177), heterotaxy syndrome (n=38), a

28 ependent risk factors for mortality, whereas pulmonary atresia or stenosis and pulmonary artery bandi

29 In TOF, pulmonary atresia (P=0.003), male sex (P=0.01) and previ

30 OF) patients with pulmonary stenosis (PS) or pulmonary atresia (PA).

31 crest, and compared these phenotypes to the pulmonary atresia phenotype observed following the syste

32 , embryos treated with cyclopamine exhibited pulmonary atresia, pulmonary stenosis, and persistent tr

33 ructive lesions, including nine fetuses with pulmonary atresia, six with severe obstructive tricuspid

34 and more common in tetralogy of Fallot with pulmonary atresia than tetralogy of Fallot alone.

35 rare and resembles tetralogy of Fallot with pulmonary atresia: There is a high incidence of aortopul

36 120 infants (7.5% [95% CI, 3.5%-13.8%]) with pulmonary atresia to 497 of 801 (62.0% [58.7%-65.4%]) wi

37 PCs) in infants with tetralogy of Fallot and pulmonary atresia (TOF/PA) and to prospectively validate

38 with TOF pulmonary stenosis (TOF/PS) or TOF pulmonary atresia (TOF/PA) who were <90 days of age unde

39 Twenty-three children with pulmonary atresia underwent 48 cardiac-triggered dynamic

40 Since 1992, 85 patients with pulmonary atresia, VSD, and MAPCAs have undergone unifoc

41 rdiac defects including overriding aorta and pulmonary atresia, while none of the sham-operated contr

42 ete atrioventricular septal defect, 5.3% for pulmonary atresia with an intact ventricular septum, and

43 sociated with higher risk of thrombosis were pulmonary atresia with intact ventricular septum (hazard

44 Pulmonary atresia with intact ventricular septum (PA/IVS

45 ts undergoing catheter valve perforation for pulmonary atresia with intact ventricular septum (PAIVS)

46 way in a longitudinal series of fetuses with pulmonary atresia with intact ventricular septum (PAIVS)

47 We describe the morphologic variability in pulmonary atresia with intact ventricular septum (PAIVS)

48 ased study was to determine the incidence of pulmonary atresia with intact ventricular septum (PAIVS)

49 Ninety-nine patients (71 with pulmonary atresia with intact ventricular septum and 28

50 Patients with pulmonary atresia with intact ventricular septum deemed

51 Pulmonary atresia with intact ventricular septum is rare

52 ventricle (RV) decompression in infants with pulmonary atresia with intact ventricular septum vary wi

53 AND Neonates undergoing RV decompression for pulmonary atresia with intact ventricular septum were in

54 tions, and mice lacking connexin43 developed pulmonary atresia with intact ventricular septum.

55 Pulmonary atresia with ventricular septal defect (VSD) a

56 h an intact ventricular septum, and 6.4% for pulmonary atresia with ventricular septal defect.

57 h surgically repaired tetralogy of Fallot or pulmonary atresia with ventricular septal defect.