ライフサイエンスコーパス: transmembrane conductance

1 stance arteries ex vivo, the cystic fibrosis transmembrane conductance regulator (1) is critical for

2 nger regulatory factor-1 and cystic fibrosis transmembrane conductance regulator (a key player in the

3 Because the cystic fibrosis transmembrane conductance regulator (ABCC7) is closely r

4 s to the gating mutations of cystic fibrosis transmembrane conductance regulator (CFTR or ABCC7; i.e.

5 Cystic fibrosis transmembrane conductance regulator (CFTR) (ABCC7), uniq

6 ol of cell proliferation and cystic fibrosis transmembrane conductance regulator (CFTR) -driven fluid

7 coid dexamethasone increases cystic fibrosis transmembrane conductance regulator (CFTR) abundance in

8 linone CFTRact-J027 (4) as a cystic fibrosis transmembrane conductance regulator (CFTR) activator wit

9 ates that ivacaftor improves cystic fibrosis transmembrane conductance regulator (CFTR) activity and

10 The cystic fibrosis transmembrane conductance regulator (CFTR) acts as a cha

11 ons to the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) also cause pa

12 membrane, which include the cystic fibrosis transmembrane conductance regulator (CFTR) and Ca(2+)-ac

13 association between lack of cystic fibrosis transmembrane conductance regulator (CFTR) and ceramide

14 ainst other proteins such as cystic fibrosis transmembrane conductance regulator (CFTR) and dystrophi

15 ulated by apically expressed cystic fibrosis transmembrane conductance regulator (CFTR) and large-con

16 nal HCO3(-) exit mediated by cystic fibrosis transmembrane conductance regulator (CFTR) and solute ca

17 alveolar fluid balance: the cystic fibrosis transmembrane conductance regulator (CFTR) and the amilo

18 l permeability and decreased cystic fibrosis transmembrane conductance regulator (Cftr) and the Na-K-

19 /H(+) antiporter, CLC-5, the cystic fibrosis transmembrane conductance regulator (CFTR) and the sodiu

20 g cassette (ABC) transporter cystic fibrosis transmembrane conductance regulator (CFTR) and two other

21 and secrete Cl- through the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

22 alanine 508 (F508del) in the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

23 Loss of cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

24 on special properties of the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

25 in the gene that encodes the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

26 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

27 loride permeation pathway in cystic fibrosis transmembrane conductance regulator (CFTR) as a short na

28 ts in functional expression defect of the CF transmembrane conductance regulator (CFTR) at the apical

29 Mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) cause recurri

30 inclusion of the full-length cystic fibrosis transmembrane conductance regulator (CFTR) cDNA together

31 espite the importance of the cystic fibrosis transmembrane conductance regulator (CFTR) channel for e

32 The cystic fibrosis transmembrane conductance regulator (CFTR) channel is ac

33 F) mice with a nonfunctional cystic fibrosis transmembrane conductance regulator (CFTR) channel was r

34 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) channel, whic

35 functionally interacts with cystic fibrosis transmembrane conductance regulator (CFTR) channel.

36 lands are important sites of cystic fibrosis transmembrane conductance regulator (CFTR) chloride (Cl(

37 used by loss of a functional cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

38 e: functional defects of the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

39 eine scanning studies of the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

40 y the functional expression defect of the CF transmembrane conductance regulator (CFTR) chloride chan

41 The cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

42 regulatory (R) domain of the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

43 s caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

44 all-molecule blockers of the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

45 ystic fibrosis (CF), a lack of functional CF transmembrane conductance regulator (CFTR) chloride chan

46 pus oocytes coexpressing the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

47 ppropriate activation of the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

48 esults from mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

49 eads to an inhibition of the cystic fibrosis transmembrane conductance regulator (CFTR) Cl(-) channel

50 ability, and function of the cystic fibrosis transmembrane conductance regulator (CFTR) Cl(-) channel

51 Cystic fibrosis transmembrane conductance regulator (CFTR) Cl(-) channel

52 the loss of function of the cystic fibrosis transmembrane conductance regulator (CFTR) combined with

53 We evaluated the effects of cystic fibrosis transmembrane conductance regulator (CFTR) deficiency on

54 Smoking is reported to cause cystic fibrosis transmembrane conductance regulator (CFTR) dysfunction i

55 The cystic fibrosis transmembrane conductance regulator (CFTR) epithelial an

56 um (OE) of mice deficient in cystic fibrosis transmembrane conductance regulator (CFTR) exhibits ion

57 n epithelial cells decreases cystic fibrosis transmembrane conductance regulator (CFTR) expression an

58 Here we show that the cystic fibrosis transmembrane conductance regulator (CFTR) facilitates L

59 main interaction between the cystic fibrosis transmembrane conductance regulator (CFTR) first cytosol

60 as correctors of the F508del-cystic fibrosis transmembrane conductance regulator (CFTR) folding defec

61 e findings are directly caused by loss of CF transmembrane conductance regulator (CFTR) function or s

62 Cystic fibrosis transmembrane conductance regulator (CFTR) functions as

63 Mutations in the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) gene affect C

64 covery that mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene cause cy

65 Mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene cause cy

66 hesis that disruption of the cystic fibrosis transmembrane conductance regulator (CFTR) gene directly

67 of-function mutations of the cystic fibrosis transmembrane conductance regulator (CFTR) gene encoding

68 The F508del mutation in the CF transmembrane conductance regulator (Cftr) gene induces

69 ted since the cloning of the cystic fibrosis transmembrane conductance regulator (CFTR) gene is being

70 The F508del mutation in the cystic fibrosis transmembrane conductance regulator (Cftr) gene is belie

71 kb -35 (DHS-35kb) 5' to the cystic fibrosis transmembrane conductance regulator (CFTR) gene is evide

72 he DeltaF508 mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) gene is the m

73 ease-causing mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) gene is the o

74 The most common cystic fibrosis transmembrane conductance regulator (CFTR) gene mutation

75 The cystic fibrosis transmembrane conductance regulator (CFTR) gene provides

76 brosis (CF) is caused by mutations in the CF transmembrane conductance regulator (CFTR) gene that imp

77 It is caused by mutations in the CF transmembrane conductance regulator (CFTR) gene that is

78 V1, expressing a full-length cystic fibrosis transmembrane conductance regulator (CFTR) gene, is capa

79 .7-kb promoter region of the cystic fibrosis transmembrane conductance regulator (CFTR) gene, we defi

80 s caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene, which e

81 the F508del mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

82 g chromatin structure at the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

83 CF), a disease caused by mutations in the CF transmembrane conductance regulator (CFTR) gene.

84 oss 250 kb, encompassing the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

85 e caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

86 e caused by mutations of the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

87 In those with severe CF transmembrane conductance regulator (CFTR) genotypes, IR

88 binding domain (NBD2) of the cystic fibrosis transmembrane conductance regulator (CFTR) has lagged be

89 e than 2000 mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) have been des

90 es (MPhis) with mutations in cystic fibrosis transmembrane conductance regulator (CFTR) have blunted

91 function of Slc26a6 and the cystic fibrosis transmembrane conductance regulator (CFTR) in HeLa cells

92 rosis homozygous for F508del-cystic fibrosis transmembrane conductance regulator (CFTR) in placebo-co

93 is to efficiently and safely express the CF transmembrane conductance regulator (CFTR) in the approp

94 Loss of function of the cystic fibrosis transmembrane conductance regulator (CFTR) in the biliar

95 The role of Pseudomonas aeruginosa and CF transmembrane conductance regulator (CFTR) in Treg regul

96 used by the F508 mutation in cystic fibrosis transmembrane conductance regulator (CFTR) include a "co

97 Cystic fibrosis transmembrane conductance regulator (CFTR) inhibitory fa

98 The virulence factor cystic fibrosis transmembrane conductance regulator (CFTR) inhibitory fa

99 PTEN and the CF transmembrane conductance regulator (CFTR) interacted di

100 Cystic fibrosis transmembrane conductance regulator (CFTR) is a cAMP-act

101 Cystic fibrosis transmembrane conductance regulator (CFTR) is a cAMP/pro

102 Cystic fibrosis transmembrane conductance regulator (CFTR) is a chloride

103 The Cystic Fibrosis Transmembrane conductance Regulator (CFTR) is a chloride

104 The cystic fibrosis transmembrane conductance regulator (CFTR) is a chloride

105 Cystic fibrosis transmembrane conductance regulator (CFTR) is a Cl(-)-se

106 cAMP-activated Cl(-) channel cystic fibrosis transmembrane conductance regulator (CFTR) is a major pr

107 brates, the chloride channel cystic fibrosis transmembrane conductance regulator (CFTR) is a master r

108 The cystic fibrosis transmembrane conductance regulator (CFTR) is a member o

109 Cystic fibrosis transmembrane conductance regulator (CFTR) is a membrane

110 Cystic fibrosis transmembrane conductance regulator (CFTR) is a multidom

111 The cystic fibrosis transmembrane conductance regulator (CFTR) is a plasma-m

112 The cystic fibrosis transmembrane conductance regulator (CFTR) is a unique i

113 Expression of the cystic fibrosis transmembrane conductance regulator (CFTR) is altered in

114 Cystic fibrosis transmembrane conductance regulator (CFTR) is an anion c

115 The cystic fibrosis transmembrane conductance regulator (CFTR) is an anion c

116 The cystic fibrosis transmembrane conductance regulator (CFTR) is an anion c

117 The cystic fibrosis transmembrane conductance regulator (CFTR) is an anion c

118 The cystic fibrosis transmembrane conductance regulator (CFTR) is an ATP-bin

119 ABSTRACT: Cystic fibrosis transmembrane conductance regulator (CFTR) is an ATP-gat

120 The cystic fibrosis transmembrane conductance regulator (CFTR) is an epithel

121 The cystic fibrosis transmembrane conductance regulator (CFTR) is an epithel

122 an DeltaF508 mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) is associated

123 Endocytic recycling of the cystic fibrosis transmembrane conductance regulator (CFTR) is blocked by

124 The cystic fibrosis transmembrane conductance regulator (CFTR) is expressed

125 modulator compounds for the cystic fibrosis transmembrane conductance regulator (CFTR) is key for th

126 Cystic fibrosis transmembrane conductance regulator (CFTR) is one ERAD s

127 08 deletion (F508del) in the cystic fibrosis transmembrane conductance regulator (CFTR) is the most c

128 Cystic fibrosis transmembrane conductance regulator (CFTR) is the only l

129 Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) is the secret

130 gamma stimulation in vivo in cystic fibrosis transmembrane conductance regulator (Cftr) knockout mice

131 binding domain (NBD1) of the cystic fibrosis transmembrane conductance regulator (CFTR) leads to defe

132 s or dysfunction of the cystic fibrosis (CF) transmembrane conductance regulator (CFTR) leads to impa

133 We hypothesized that cystic fibrosis transmembrane conductance regulator (CFTR) may be critic

134 s (FPOP) for footprinting of cystic fibrosis transmembrane conductance regulator (CFTR) membrane tran

135 mbination treatment with the cystic fibrosis transmembrane conductance regulator (CFTR) modulators te

136 The most prevalent cystic fibrosis transmembrane conductance regulator (CFTR) mutation caus

137 e carrying the most frequent cystic fibrosis transmembrane conductance regulator (CFTR) mutation in h

138 Using 20 variants from cystic fibrosis transmembrane conductance regulator (CFTR) nucleotide-bi

139 Inhibition of either cystic fibrosis transmembrane conductance regulator (CFTR) or Na(+)-K(+)

140 The chloride channel of the cystic fibrosis transmembrane conductance regulator (CFTR) participates

141 anine 508 (DeltaF508) in the cystic fibrosis transmembrane conductance regulator (CFTR) plasma membra

142 fold and increased wild-type cystic fibrosis transmembrane conductance regulator (CFTR) plasma membra

143 Ivacaftor is a cystic fibrosis transmembrane conductance regulator (CFTR) potentiator r

144 Ivacaftor, a cystic fibrosis transmembrane conductance regulator (CFTR) potentiator,

145 ed by defective or deficient cystic fibrosis transmembrane conductance regulator (CFTR) protein activ

146 DeltaPhe508 mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) protein impai

147 Cystic fibrosis transmembrane conductance regulator (CFTR) protein is a

148 ng the activity of defective cystic fibrosis transmembrane conductance regulator (CFTR) protein is a

149 and decreased apical cilia, cystic fibrosis transmembrane conductance regulator (CFTR) protein level

150 unction or deficiency of the cystic fibrosis transmembrane conductance regulator (CFTR) protein, an e

151 sing of the DeltaF508 mutant cystic fibrosis transmembrane conductance regulator (CFTR) protein.

152 is (CF) is due to a folding defect in the CF transmembrane conductance regulator (CFTR) protein.

153 by the lack of a functional cystic fibrosis transmembrane conductance regulator (CFTR) protein.

154 In the liver, the cystic fibrosis (CF) transmembrane conductance regulator (CFTR) regulates bil

155 hly PKA-phosphorylated human cystic fibrosis transmembrane conductance regulator (CFTR) regulatory re

156 type and variant (DeltaF508) cystic fibrosis transmembrane conductance regulator (CFTR) responsible f

157 Deletion of Phe508 from cystic fibrosis transmembrane conductance regulator (CFTR) results in a

158 binding domain (NBD1) of the cystic fibrosis transmembrane conductance regulator (CFTR) results in de

159 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) that compromi

160 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) that impair i

161 brosis (CF) is caused by mutations in the CF transmembrane conductance regulator (CFTR) that prevent

162 ftor is a potentiator of the cystic fibrosis transmembrane conductance regulator (CFTR) that reduces

163 lamotrigine), as well as the cystic fibrosis transmembrane conductance regulator (CFTR) trafficking c

164 Misfolding of DeltaF508 cystic fibrosis (CF) transmembrane conductance regulator (CFTR) underlies pat

165 amino acids inserted at the cystic fibrosis transmembrane conductance regulator (CFTR) W1282X PTC (a

166 ons of the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) which is an a

167 the apical chloride channel cystic fibrosis transmembrane conductance regulator (CFTR) with 90% of p

168 ons of the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) with a preval

169 nique ATP-gated ion channel (cystic fibrosis transmembrane conductance regulator (CFTR)).

170 functional abnormalities of cystic fibrosis transmembrane conductance regulator (CFTR), a 25% reduct

171 f apoptosis and involves the cystic fibrosis transmembrane conductance regulator (CFTR), a cAMP-regul

172 inylation and degradation of cystic fibrosis transmembrane conductance regulator (CFTR), a chloride c

173 we examined the role of the cystic fibrosis transmembrane conductance regulator (CFTR), a Cl(-) and

174 Malfunction of the cystic fibrosis transmembrane conductance regulator (CFTR), a gated path

175 F508del cystic fibrosis transmembrane conductance regulator (CFTR), a well-studi

176 (CF) results from mutations that disrupt CF transmembrane conductance regulator (CFTR), an anion cha

177 al PDZ domains bind the cystic fibrosis (CF) transmembrane conductance regulator (CFTR), an epithelia

178 ajor anion channels, such as cystic fibrosis transmembrane conductance regulator (CFTR), anoctamin-1(

179 he steady state level of the cystic fibrosis transmembrane conductance regulator (CFTR), but the unde

180 genes such as PRSS1, SPINK1, cystic fibrosis transmembrane conductance regulator (CFTR), chymotrypsin

181 ntify the interactome of the cystic fibrosis transmembrane conductance regulator (CFTR), demonstratin

182 of the common mutant of the cystic fibrosis transmembrane conductance regulator (CFTR), F508del, is

183 cal translation speed of the cystic fibrosis transmembrane conductance regulator (CFTR), leading to d

184 s caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR), of which the

185 illustrate that disrupted function of the CF transmembrane conductance regulator (CFTR), such as that

186 ould target the underlying defects in the CF transmembrane conductance regulator (CFTR), the Cystic F

187 shown previously that macrophages lacking CF transmembrane conductance regulator (CFTR), the gene mut

188 e caused by the DeltaF508 mutation in the CF transmembrane conductance regulator (CFTR), which disrup

189 the epithelial Cl(-) channel cystic fibrosis transmembrane conductance regulator (CFTR), which is def

190 KEY POINTS: The cystic fibrosis transmembrane conductance regulator (CFTR), which is def

191 smembrane channel called the cystic fibrosis transmembrane conductance regulator (CFTR), which regula

192 ts of low serum IGF-1 on the cystic fibrosis transmembrane conductance regulator (CFTR), whose defect

193 Golgi-localized cystic fibrosis transmembrane conductance regulator (CFTR)-associated li

194 assessed by forskolin-induced swelling in CF transmembrane conductance regulator (CFTR)-deficient org

195 % compared with control) and cystic fibrosis transmembrane conductance regulator (CFTR)-dependent and

196 estines that inherently lack cystic fibrosis transmembrane conductance regulator (CFTR)-dependent HCO

197 s, cAMP is known to regulate cystic fibrosis transmembrane conductance regulator (CFTR)-mediated anio

198 partially restored DeltaF508-cystic fibrosis transmembrane conductance regulator (CFTR)-mediated cAMP

199 These drugs activate cystic fibrosis transmembrane conductance regulator (CFTR)-mediated flui

200 s caused by mutations of the cystic fibrosis transmembrane conductance regulator (Cftr).

201 secretin receptor, cilia and cystic fibrosis transmembrane conductance regulator (CFTR).

202 c fibrosis (CF) is caused by mutations in CF transmembrane conductance regulator (CFTR).

203 coding for the anion channel cystic fibrosis transmembrane conductance regulator (CFTR).

204 the epithelial anion channel cystic fibrosis transmembrane conductance regulator (CFTR).

205 f Phe-508 (DeltaF508) in the cystic fibrosis transmembrane conductance regulator (CFTR).

206 ssive disorder affecting the cystic fibrosis transmembrane conductance regulator (CFTR).

207 pression and function of the cystic fibrosis transmembrane conductance regulator (CFTR).

208 lial Cl(-) secretion via the cystic fibrosis transmembrane conductance regulator (CFTR).

209 des for a Cl(-) channel, the cystic fibrosis transmembrane conductance regulator (CFTR).

210 ABC transporters such as the cystic fibrosis transmembrane conductance regulator (CFTR).

211 s and quality control of the cystic fibrosis transmembrane conductance regulator (CFTR).

212 ons for the membrane protein cystic fibrosis transmembrane conductance regulator (CFTR).

213 e transporter (AlgE) and the cystic fibrosis transmembrane conductance regulator (CFTR).

214 gene product DeltaF508 cystic fibrosis (CF) transmembrane conductance regulator (CFTR).

215 se (PKG), and opening of the cystic fibrosis transmembrane conductance regulator (CFTR).

216 ATP-gated anion channel, the cystic fibrosis transmembrane conductance regulator (CFTR).

217 lls expressing the misfolded cystic fibrosis transmembrane conductance regulator (CFTR).

218 ue the trafficking mutant of cystic fibrosis transmembrane conductance regulator (CFTR).

219 e epithelial-cell chloride channel called CF transmembrane conductance regulator (CFTR).

220 e result of mutations in the cystic fibrosis transmembrane conductance regulator (CFTR).

221 The cystic fibrosis transmembrane conductance regulator (CFTR, ABCC7), mutat

222 omal degradation of a mutant cystic fibrosis transmembrane conductance regulator (CFTRDeltaF508) was

223 red an rAAV vector containing a truncated CF transmembrane conductance regulator (CFTRDeltaR) combine

224 TT, in deletion of Phe508 in cystic fibrosis transmembrane conductance regulator (DeltaF508 CFTR), th

225 of phenylalanine 508 of the cystic fibrosis transmembrane conductance regulator (F508 CFTR) is the m

226 zed that transgenic expression of porcine CF transmembrane conductance regulator (pCFTR) cDNA under c

227 d pancreatic genes (albumin, cystic fibrosis transmembrane conductance regulator [CFTR], and insulin)

228 ctor-alpha downregulates the cystic fibrosis transmembrane conductance regulator across several organ

229 cells via a reduction in the cystic fibrosis transmembrane conductance regulator activity and biosynt

230 essure resulted in decreased cystic fibrosis transmembrane conductance regulator activity and liquid

231 /adenylyl cyclase-dependent, cystic fibrosis transmembrane conductance regulator activity.

232 ffects on the degradation of cystic fibrosis transmembrane conductance regulator and CPY*, which is a

233 he NHERF1-binding domains of cystic fibrosis transmembrane conductance regulator and Csk-binding prot

234 secretion appears to require cystic fibrosis transmembrane conductance regulator and electrogenic Na(

235 porters (ABC), including the cystic fibrosis transmembrane conductance regulator and P-glycoprotein.

236 was completely dependent on cystic fibrosis transmembrane conductance regulator and partially depend

237 -dependent activation of the cystic fibrosis transmembrane conductance regulator anion channel was in

238 codon in mRNAs encoding the cystic fibrosis transmembrane conductance regulator anion channel.

239 Opening and closing of the cystic fibrosis transmembrane conductance regulator are controlled by AT

240 We identify the cystic fibrosis transmembrane conductance regulator as a critical regula

241 slows the degradation of the cystic fibrosis transmembrane conductance regulator but does not impede

242 unction mutations in the chloride channel CF transmembrane conductance regulator can elevate the acti

243 re of the outer mouth of the cystic fibrosis transmembrane conductance regulator channel pore: TMs 6

244 ary Cl(-) conductance in the cystic fibrosis transmembrane conductance regulator Cl(-) channel requir

245 egments line the pore of the cystic fibrosis transmembrane conductance regulator Cl(-) channel; howev

246 tance is mediated by altered cystic fibrosis transmembrane conductance regulator expression and activ

247 e used mice deficient in the cystic fibrosis transmembrane conductance regulator gene (Cftr) to test

248 ate gene studies include the cystic fibrosis transmembrane conductance regulator gene (CFTR), as well

249 enetic disease caused by mutations in the CF transmembrane conductance regulator gene (CFTR).

250 almost 2,000 variants in the cystic fibrosis transmembrane conductance regulator gene CFTR have empir

251 d to efficiently deliver the cystic fibrosis transmembrane conductance regulator gene to human airway

252 ) cells after treatment with cystic fibrosis transmembrane conductance regulator inhibitor CFTR(inh)-

253 ence factors alkaline protease (AprA) and CF transmembrane conductance regulator inhibitory factor (C

254 eruginosa epoxide hydrolase, cystic fibrosis transmembrane conductance regulator inhibitory factor (C

255 Genetic variation in cystic fibrosis transmembrane conductance regulator is associated with a

256 n of our editase can correct cystic fibrosis transmembrane conductance regulator mRNA, restore full-l

257 As an ion channel, the cystic fibrosis transmembrane conductance regulator must form a continuo

258 ts of the disease-associated cystic fibrosis transmembrane conductance regulator mutant F508del.

259 F lung disease in a manner independent of CF transmembrane conductance regulator mutation.

260 the threshold, whereas, the cystic fibrosis transmembrane conductance regulator only contributes to

261 Cystic fibrosis transmembrane conductance regulator potentiation by ivac

262 ch was partially reversed by cystic fibrosis transmembrane conductance regulator potentiation with iv

263 e the feasibility of using a cystic fibrosis transmembrane conductance regulator potentiator, ivacaft

264 The Cystic Fibrosis Transmembrane Conductance Regulator protein (CFTR) is a

265 ny missense mutations in the cystic fibrosis transmembrane conductance regulator protein (CFTR) resul

266 he loss of chloride transport through the CF transmembrane conductance regulator protein (CFTR).

267 -length plasmid encoding the cystic fibrosis transmembrane conductance regulator protein was achieved

268 bed in CF including disabled cystic fibrosis transmembrane conductance regulator recruitment to phago

269 The cystic fibrosis transmembrane conductance regulator regulates fluid bala

270 ficient degradation of human cystic fibrosis transmembrane conductance regulator requires function of

271 ) lung disease, the absence of functional CF transmembrane conductance regulator results in Cl(-)/HCO

272 estigation proposes that the cystic fibrosis transmembrane conductance regulator transports extracell

273 Cystic fibrosis transmembrane conductance regulator was internalized in

274 creased levels of functional cystic fibrosis transmembrane conductance regulator were associated with

275 veolar macrophages from cystic fibrosis (CF) transmembrane conductance regulator(-/-) mice have impai

276 y the retention of the CFTR (cystic fibrosis transmembrane conductance regulator) mutant protein in t

277 ngle residue (F508) in CFTR (cystic fibrosis transmembrane conductance regulator) that disrupts the f

278 ease the level of functional cystic fibrosis transmembrane conductance regulator) with the need for m

279 al exocytosis of NHE3, CFTR (cystic fibrosis transmembrane conductance regulator), and GLUT5 required

280 psin-controlling gene or the cystic fibrosis transmembrane conductance regulator); a few patients hav

281 in gross mislocalization of cystic fibrosis transmembrane conductance regulator, causing marked redu

282 n amino acid deletion in the cystic fibrosis transmembrane conductance regulator, CFTR.

283 on through activation of the cystic fibrosis transmembrane conductance regulator, CFTR.

284 ation with and activation of cystic fibrosis transmembrane conductance regulator, one of its binding

285 ngiocyte functions including cystic fibrosis transmembrane conductance regulator, secretin receptor,

286 cretion via up-regulation of cystic fibrosis transmembrane conductance regulator, suggesting an impor

287 embrane K(ATP) channels, the cystic fibrosis transmembrane conductance regulator, the transient recep

288 ing functional defect in the cystic fibrosis transmembrane conductance regulator, there is still an u

289 romone, Ste6* (sterile), and cystic fibrosis transmembrane conductance regulator, undergo Ubr1-depend

290 including the anion channel cystic fibrosis transmembrane conductance regulator, which shunt the tra

291 -fibrosis-associated protein cystic fibrosis transmembrane conductance regulator, which upon deletion

292 es, at least in part through cystic fibrosis transmembrane conductance regulator-associated channels,

293 These findings link loss of cystic fibrosis transmembrane conductance regulator-dependent alkaliniza

294 oncentration of bicarbonate, which mimics CF transmembrane conductance regulator-mediated anion secre

295 tide-binding domain from the cystic fibrosis transmembrane conductance regulator.

296 en through activation of the cystic fibrosis transmembrane conductance regulator.

297 lesser effects on misfolded cystic fibrosis transmembrane conductance regulator.

298 ction in the gene coding for cystic fibrosis transmembrane conductance regulator.

299 denosine 3',5'-monophosphate/cystic fibrosis transmembrane conductance regulator/chloride bicarbonate

300 The cystic fibrosis transmembrane-conductance regulator (CFTR) chloride chan