ライフサイエンスコーパス: Ebstein

1 Ebstein anomaly and tricuspid valve dysplasia are rare c

2 Ebstein anomaly is a spectrum of tricuspid valvular and

3 Ebstein anomaly is the most common cause of primary tric

4 Ebstein's anomaly and other tricuspid valve abnormalitie

5 Ebstein's anomaly was diagnosed in one lithium-exposed f

6 Ebstein's malformation coexisted in 18 patients.

7 25%), tricuspid atresia (12 patients, 20%), Ebstein's anomaly (4 patients, 6.5%), pulmonic atresia o

8 trial to right ventricle bioprosthesis in 3, Ebstein's anomaly of the TV in 5, and other in 6), and 2

9 In this retrospective cohort study, 371 Ebstein patients that underwent tricuspid valve surgery

10 dum atrial septal defect (ASD) (n = 71), and Ebstein's malformation (n = 7) for NKX2.5 mutations.

11 orrected transposition of great arteries and Ebstein anomaly of the tricuspid valve.

12 ter category encompasses CHD lesions such as Ebstein anomaly, transposition of the great arteries wit

13 in human congenital heart diseases, such as Ebstein's anomaly.

14 The association between Ebstein anomaly and myocardial fibrosis, particularly in

15 irst report of individuals being affected by Ebstein anomaly because of a mutation in this gene and d

16 adults with congenital heart disease (CHD): Ebstein's anomaly, the failing Fontan, and pulmonary val

17 , including atrioventricular septal defects, Ebstein malformation of the tricuspid valve, and perimem

18 the great arteries, cyanotic heart disease, Ebstein anomaly, and Fontan circulation.

19 apy of tricuspid valve anomalies, especially Ebstein's malformation.

20 tricular septal defect, tetralogy of Fallot, Ebstein anomaly, transposition of the great vessels, and

21 Familial Ebstein anomaly is a rare form of congenital heart disea

22 Definitive operation for Ebstein's anomaly results in improved exercise tolerance

23 tional outcomes after undergoing surgery for Ebstein anomaly.

24 Surgery for Ebstein's anomaly can now be offered to older patients a

25 performed on adults with CHD are surgery for Ebstein's anomaly, Fontan revision, and pulmonary valve

26 mmunosuppression with anti-viral therapy for Ebstein-Barr virus (EBV) is the primary treatment for al

27 heart disease but have not been described in Ebstein anomaly, nor has the visual snow syndrome.

28 Left ventricular dysfunction in Ebstein's anomaly (EA) is associated with higher mortali

29 l dysfunction is a predictor of mortality in Ebstein anomaly, and RA dysfunction and hypertension are

30 the use of RVGLS for risk stratification in Ebstein anomaly, and further studies are required to ass

31 but its application has not been studied in Ebstein anomaly.

32 with the emergence of severe CHDs including Ebstein's anomaly, atrioventricular septal defect, and o

33 sed risk of cardiac malformations, including Ebstein's anomaly; the magnitude of this effect was smal

34 tacles to elucidating the natural history of Ebstein anomaly (EA).

35 ciated with a marked increase in the risk of Ebstein's anomaly (a right ventricular outflow tract obs

36 The classification of clinical severity of Ebstein anomaly still remains a challenge.

37 imaging measure for the clinical severity of Ebstein anomaly.

38 rofound cardiogenic shock caused by a severe Ebstein anomaly can be successfully salvaged with fenest

39 Stereotactic biopsy confirmed PCNSL due to Ebstein-Barr virus reactivation.

40 a mean age of 26+/-14 years with unrepaired Ebstein anomaly were examined in a prospective study.

41 The most frequent cardiac diagnoses were Ebstein's anomaly (40%), pulmonary atresia (11%), and te

42 The most common diagnoses were Ebstein's anomaly (n=44), septal defects (n=39), and sin

43 ts at the Mayo Clinic from 1987 to 2020 with Ebstein anomaly and CIED procedure were reviewed for pro

44 We included 57 adults with Ebstein anomaly (52% men; median age, 29.52 [interquarti

45 his was a retrospective study of adults with Ebstein anomaly who received care at Mayo Clinic from 20

46 This study identified adults with Ebstein anomaly with echocardiographic assessment of RV

47 ce of LV fibrosis replacement in adults with Ebstein anomaly, characterized by specific CMR and histo

48 utcomes in patients >/= 50 years of age with Ebstein anomaly (EA).

49 To present a case with Ebstein anomaly, a rare congenital heart disorder, with

50 Fetuses diagnosed with Ebstein anomaly and tricuspid valve dysplasia from 2005

51 A 10-year-old white girl was diagnosed with Ebstein anomaly.

52 viduals among 2 generations of 1 family with Ebstein anomaly.

53 s large, contemporary series of fetuses with Ebstein anomaly and tricuspid valve dysplasia, perinatal

54 e with severe tetralogy of Fallot, four with Ebstein's anomaly and two with single ventricle and pulm

55 electronic devices (CIEDs) in patients with Ebstein anomaly during tricuspid valve (TV) surgery is u

56 In patients with Ebstein anomaly undergoing TV surgery, the use of epicar

57 ze CIED management/outcomes in patients with Ebstein anomaly undergoing TV surgery.

58 1972, to January 1, 2006, 539 patients with Ebstein anomaly underwent 604 cardiac operations at the

59 ong-term functional outcome of patients with Ebstein anomaly who had cardiac operation at our institu

60 retrospective cohort of adult patients with Ebstein anomaly who underwent CMR.

61 In patients with Ebstein anomaly, the easily acquired index of right-side

62 longitudinal strain (RVGLS) in patients with Ebstein anomaly.

63 for LV systolic dysfunction in patients with Ebstein anomaly.

64 Patients with Ebstein's anomaly of the tricuspid valve may have exerci

65 nants of exercise tolerance in patients with Ebstein's anomaly.