ライフサイエンスコーパス: transmembrane conductance

1 stance arteries ex vivo, the cystic fibrosis transmembrane conductance regulator (1) is critical for

2 nger regulatory factor-1 and cystic fibrosis transmembrane conductance regulator (a key player in the

3 Because the cystic fibrosis transmembrane conductance regulator (ABCC7) is closely r

4 s to the gating mutations of cystic fibrosis transmembrane conductance regulator (CFTR or ABCC7; i.e.

5 Cystic fibrosis transmembrane conductance regulator (CFTR) (ABCC7), uniq

6 ol of cell proliferation and cystic fibrosis transmembrane conductance regulator (CFTR) -driven fluid

7 coid dexamethasone increases cystic fibrosis transmembrane conductance regulator (CFTR) abundance in

8 linone CFTRact-J027 (4) as a cystic fibrosis transmembrane conductance regulator (CFTR) activator wit

9 ates that ivacaftor improves cystic fibrosis transmembrane conductance regulator (CFTR) activity and

10 The cystic fibrosis transmembrane conductance regulator (CFTR) acts as a cha

11 tal cells and frequently coexpressed with CF transmembrane conductance regulator (CFTR) along with tr

12 ons to the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) also cause pa

13 membrane, which include the cystic fibrosis transmembrane conductance regulator (CFTR) and Ca(2+)-ac

14 ainst other proteins such as cystic fibrosis transmembrane conductance regulator (CFTR) and dystrophi

15 ulated by apically expressed cystic fibrosis transmembrane conductance regulator (CFTR) and large-con

16 nal HCO3(-) exit mediated by cystic fibrosis transmembrane conductance regulator (CFTR) and solute ca

17 regulates the biogenesis of cystic fibrosis transmembrane conductance regulator (CFTR) and the epith

18 l permeability and decreased cystic fibrosis transmembrane conductance regulator (Cftr) and the Na-K-

19 hrough the chloride channels cystic fibrosis transmembrane conductance regulator (CFTR) and TMEM16A (

20 g cassette (ABC) transporter cystic fibrosis transmembrane conductance regulator (CFTR) and two other

21 alanine 508 (F508del) in the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

22 on special properties of the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

23 The Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) anion channel

24 fibrosis (CF) pigs, loss of cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

25 in the gene that encodes the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

26 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

27 and secrete Cl- through the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

28 s caused by mutations of the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) anion channel

29 alanine 508 (F508del) in the cystic fibrosis transmembrane conductance regulator (CFTR) anion channel

30 loride permeation pathway in cystic fibrosis transmembrane conductance regulator (CFTR) as a short na

31 three nonsense mutations of cystic fibrosis transmembrane conductance regulator (CFTR) associated wi

32 minal truncation mutation of cystic fibrosis transmembrane conductance regulator (CFTR) associated wi

33 ts in functional expression defect of the CF transmembrane conductance regulator (CFTR) at the apical

34 ions that stabilize the cystic fibrosis (CF) transmembrane conductance regulator (CFTR) at the apical

35 Small-molecule modulators of cystic fibrosis transmembrane conductance regulator (CFTR) biology show

36 Mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) cause recurri

37 ginine would enhance F508del-cystic fibrosis transmembrane conductance regulator (CFTR) channel activ

38 The cystic fibrosis transmembrane conductance regulator (CFTR) channel is ac

39 F) mice with a nonfunctional cystic fibrosis transmembrane conductance regulator (CFTR) channel was r

40 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) channel, whic

41 caused by loss of functional cystic fibrosis transmembrane conductance regulator (CFTR) channel.

42 The role of epithelial cystic fibrosis (CF) transmembrane conductance regulator (CFTR) chloride chan

43 used by loss of a functional cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

44 e: functional defects of the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

45 eine scanning studies of the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

46 y the functional expression defect of the CF transmembrane conductance regulator (CFTR) chloride chan

47 of-function mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

48 ssive disease, caused by mutations in the CF transmembrane conductance regulator (CFTR) chloride chan

49 ppropriate activation of the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

50 esults from mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) chloride chan

51 eads to an inhibition of the cystic fibrosis transmembrane conductance regulator (CFTR) Cl(-) channel

52 Cystic fibrosis transmembrane conductance regulator (CFTR) Cl(-) channel

53 tation DeltaF508 on the gene encoding the CF transmembrane conductance regulator (CFTR) Cl(-) channel

54 ability, and function of the cystic fibrosis transmembrane conductance regulator (CFTR) Cl(-) channel

55 the loss of function of the cystic fibrosis transmembrane conductance regulator (CFTR) combined with

56 of-function mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) compromise ep

57 A pathway for cystic fibrosis transmembrane conductance regulator (CFTR) degradation i

58 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) disrupt epith

59 Smoking is reported to cause cystic fibrosis transmembrane conductance regulator (CFTR) dysfunction i

60 um (OE) of mice deficient in cystic fibrosis transmembrane conductance regulator (CFTR) exhibits ion

61 els (TMEM16A), including the cystic fibrosis transmembrane conductance regulator (CFTR) expressed on

62 n epithelial cells decreases cystic fibrosis transmembrane conductance regulator (CFTR) expression an

63 arette smoke decreased AMPhi cystic fibrosis transmembrane conductance regulator (CFTR) expression, p

64 main interaction between the cystic fibrosis transmembrane conductance regulator (CFTR) first cytosol

65 as correctors of the F508del-cystic fibrosis transmembrane conductance regulator (CFTR) folding defec

66 re needed to reliably assess Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) function in v

67 e findings are directly caused by loss of CF transmembrane conductance regulator (CFTR) function or s

68 is a genetic disorder caused by defective CF Transmembrane Conductance Regulator (CFTR) function.

69 attributable to increases in cystic fibrosis transmembrane conductance regulator (CFTR) function.

70 Mutations in the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) gene affect C

71 Mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene cause cy

72 hesis that disruption of the cystic fibrosis transmembrane conductance regulator (CFTR) gene directly

73 of-function mutations of the cystic fibrosis transmembrane conductance regulator (CFTR) gene encoding

74 The F508del mutation in the CF transmembrane conductance regulator (Cftr) gene induces

75 ted since the cloning of the cystic fibrosis transmembrane conductance regulator (CFTR) gene is being

76 The F508del mutation in the cystic fibrosis transmembrane conductance regulator (Cftr) gene is belie

77 kb -35 (DHS-35kb) 5' to the cystic fibrosis transmembrane conductance regulator (CFTR) gene is evide

78 ease-causing mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) gene is the o

79 The most common cystic fibrosis transmembrane conductance regulator (CFTR) gene mutation

80 The cystic fibrosis transmembrane conductance regulator (CFTR) gene provides

81 sease, caused by genetic diversity in the CF transmembrane conductance regulator (CFTR) gene, a cycli

82 s caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene, encodin

83 ssive disorder caused by mutations in the CF transmembrane conductance regulator (CFTR) gene, encodin

84 V1, expressing a full-length cystic fibrosis transmembrane conductance regulator (CFTR) gene, is capa

85 enetic disease caused by mutations in the CF transmembrane conductance regulator (CFTR) gene, resulti

86 e caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene, resulti

87 s caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene, which e

88 e caused by mutations of the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

89 the F508del mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

90 g chromatin structure at the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

91 CF), a disease caused by mutations in the CF transmembrane conductance regulator (CFTR) gene.

92 oss 250 kb, encompassing the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

93 r caused by mutations in the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) gene.

94 hibitor gene (SPINK1) or the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

95 e caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene.

96 In those with severe CF transmembrane conductance regulator (CFTR) genotypes, IR

97 binding domain (NBD2) of the cystic fibrosis transmembrane conductance regulator (CFTR) has lagged be

98 e than 2000 mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) have been des

99 es (MPhis) with mutations in cystic fibrosis transmembrane conductance regulator (CFTR) have blunted

100 binding domain (NBD1) of the cystic fibrosis transmembrane conductance regulator (CFTR) have distinct

101 2)AR)-mediated activation of cystic fibrosis transmembrane conductance regulator (CFTR) in epithelial

102 function of Slc26a6 and the cystic fibrosis transmembrane conductance regulator (CFTR) in HeLa cells

103 rosis homozygous for F508del-cystic fibrosis transmembrane conductance regulator (CFTR) in placebo-co

104 The role of Pseudomonas aeruginosa and CF transmembrane conductance regulator (CFTR) in Treg regul

105 st to assess the role of the cystic fibrosis transmembrane conductance regulator (CFTR) in urinary HC

106 used by the F508 mutation in cystic fibrosis transmembrane conductance regulator (CFTR) include a "co

107 demonstrate the efficacy of cystic fibrosis transmembrane conductance regulator (CFTR) inhibitor (R)

108 The virulence factor cystic fibrosis transmembrane conductance regulator (CFTR) inhibitory fa

109 PTEN and the CF transmembrane conductance regulator (CFTR) interacted di

110 Cystic fibrosis transmembrane conductance regulator (CFTR) is a chloride

111 The cystic fibrosis transmembrane conductance regulator (CFTR) is a chloride

112 Cystic fibrosis transmembrane conductance regulator (CFTR) is a Cl(-)-se

113 cAMP-activated Cl(-) channel cystic fibrosis transmembrane conductance regulator (CFTR) is a major pr

114 brates, the chloride channel cystic fibrosis transmembrane conductance regulator (CFTR) is a master r

115 The cystic fibrosis transmembrane conductance regulator (CFTR) is a member o

116 Cystic fibrosis transmembrane conductance regulator (CFTR) is a multidom

117 The cystic fibrosis transmembrane conductance regulator (CFTR) is a plasma m

118 The cystic fibrosis transmembrane conductance regulator (CFTR) is a plasma-m

119 Expression of the cystic fibrosis transmembrane conductance regulator (CFTR) is altered in

120 The cystic fibrosis transmembrane conductance regulator (CFTR) is an anion c

121 The cystic fibrosis transmembrane conductance regulator (CFTR) is an anion c

122 Cystic fibrosis transmembrane conductance regulator (CFTR) is an anion c

123 The cystic fibrosis transmembrane conductance regulator (CFTR) is an anion c

124 The cystic fibrosis transmembrane conductance regulator (CFTR) is an apical

125 The cystic fibrosis transmembrane conductance regulator (CFTR) is an ATP-bin

126 ABSTRACT: Cystic fibrosis transmembrane conductance regulator (CFTR) is an ATP-gat

127 The cystic fibrosis transmembrane conductance regulator (CFTR) is an epithel

128 The cystic fibrosis transmembrane conductance regulator (CFTR) is an epithel

129 The cystic fibrosis transmembrane conductance regulator (CFTR) is an ion cha

130 an DeltaF508 mutation in the cystic fibrosis transmembrane conductance regulator (CFTR) is associated

131 Endocytic recycling of the cystic fibrosis transmembrane conductance regulator (CFTR) is blocked by

132 modulator compounds for the cystic fibrosis transmembrane conductance regulator (CFTR) is key for th

133 The cystic fibrosis transmembrane conductance regulator (CFTR) is mutated in

134 Cystic fibrosis transmembrane conductance regulator (CFTR) is one ERAD s

135 08 deletion (F508del) in the cystic fibrosis transmembrane conductance regulator (CFTR) is the most c

136 Cystic fibrosis transmembrane conductance regulator (CFTR) is the only l

137 Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) is the secret

138 gamma stimulation in vivo in cystic fibrosis transmembrane conductance regulator (Cftr) knockout mice

139 s or dysfunction of the cystic fibrosis (CF) transmembrane conductance regulator (CFTR) leads to impa

140 We hypothesized that cystic fibrosis transmembrane conductance regulator (CFTR) may be critic

141 s (FPOP) for footprinting of cystic fibrosis transmembrane conductance regulator (CFTR) membrane tran

142 Cystic fibrosis transmembrane conductance regulator (CFTR) modulators co

143 mbination treatment with the cystic fibrosis transmembrane conductance regulator (CFTR) modulators te

144 o boost the response to cystic fibrosis (CF) transmembrane conductance regulator (CFTR) modulators, l

145 The most prevalent cystic fibrosis transmembrane conductance regulator (CFTR) mutation caus

146 e carrying the most frequent cystic fibrosis transmembrane conductance regulator (CFTR) mutation in h

147 es the common human Phe508del (DeltaF508) CF transmembrane conductance regulator (CFTR) mutation, whe

148 Using 20 variants from cystic fibrosis transmembrane conductance regulator (CFTR) nucleotide-bi

149 Inhibition of either cystic fibrosis transmembrane conductance regulator (CFTR) or Na(+)-K(+)

150 . explored the role that the cystic fibrosis transmembrane conductance regulator (CFTR) plays in plat

151 Ivacaftor is a cystic fibrosis transmembrane conductance regulator (CFTR) potentiator r

152 Ivacaftor, a cystic fibrosis transmembrane conductance regulator (CFTR) potentiator,

153 ed by defective or deficient cystic fibrosis transmembrane conductance regulator (CFTR) protein activ

154 Cystic fibrosis transmembrane conductance regulator (CFTR) protein is a

155 and decreased apical cilia, cystic fibrosis transmembrane conductance regulator (CFTR) protein level

156 unction or deficiency of the cystic fibrosis transmembrane conductance regulator (CFTR) protein, an e

157 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) protein, and

158 sing of the DeltaF508 mutant cystic fibrosis transmembrane conductance regulator (CFTR) protein.

159 is (CF) is due to a folding defect in the CF transmembrane conductance regulator (CFTR) protein.

160 (CF) is caused by defective Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) protein.

161 In the liver, the cystic fibrosis (CF) transmembrane conductance regulator (CFTR) regulates bil

162 hly PKA-phosphorylated human cystic fibrosis transmembrane conductance regulator (CFTR) regulatory re

163 binding domain (NBD1) of the cystic fibrosis transmembrane conductance regulator (CFTR) results in de

164 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) that compromi

165 ons in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) that impair i

166 ftor is a potentiator of the cystic fibrosis transmembrane conductance regulator (CFTR) that reduces

167 Misfolding of DeltaF508 cystic fibrosis (CF) transmembrane conductance regulator (CFTR) underlies pat

168 amino acids inserted at the cystic fibrosis transmembrane conductance regulator (CFTR) W1282X PTC (a

169 ons of the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) which is an a

170 the apical chloride channel cystic fibrosis transmembrane conductance regulator (CFTR) with 90% of p

171 ons of the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR) with a preval

172 nique ATP-gated ion channel (cystic fibrosis transmembrane conductance regulator (CFTR)).

173 functional abnormalities of cystic fibrosis transmembrane conductance regulator (CFTR), a 25% reduct

174 f apoptosis and involves the cystic fibrosis transmembrane conductance regulator (CFTR), a cAMP-regul

175 caused by mutations in the gene encoding CF transmembrane conductance regulator (CFTR), a chloride c

176 Malfunction of the cystic fibrosis transmembrane conductance regulator (CFTR), a gated path

177 oss-of-function mutations of cystic fibrosis transmembrane conductance regulator (CFTR), a phosphoryl

178 F508del cystic fibrosis transmembrane conductance regulator (CFTR), a well-studi

179 al PDZ domains bind the cystic fibrosis (CF) transmembrane conductance regulator (CFTR), an epithelia

180 ajor anion channels, such as cystic fibrosis transmembrane conductance regulator (CFTR), anoctamin-1(

181 genes such as PRSS1, SPINK1, cystic fibrosis transmembrane conductance regulator (CFTR), chymotrypsin

182 ntify the interactome of the cystic fibrosis transmembrane conductance regulator (CFTR), demonstratin

183 of the common mutant of the cystic fibrosis transmembrane conductance regulator (CFTR), F508del, is

184 cal translation speed of the cystic fibrosis transmembrane conductance regulator (CFTR), leading to d

185 s caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR), of which the

186 t VX-809, a corrector of the cystic fibrosis transmembrane conductance regulator (CFTR), reduces cyst

187 in Cl(-) extrusion, such as cystic fibrosis transmembrane conductance regulator (CFTR), should reduc

188 illustrate that disrupted function of the CF transmembrane conductance regulator (CFTR), such as that

189 ies targeting defects in the cystic fibrosis transmembrane conductance regulator (CFTR), which are li

190 KEY POINTS: The cystic fibrosis transmembrane conductance regulator (CFTR), which is def

191 the epithelial Cl(-) channel cystic fibrosis transmembrane conductance regulator (CFTR), which is def

192 smembrane channel called the cystic fibrosis transmembrane conductance regulator (CFTR), which regula

193 ts of low serum IGF-1 on the cystic fibrosis transmembrane conductance regulator (CFTR), whose defect

194 brosis (CF) is caused by mutations in the CF transmembrane conductance regulator (CFTR), with approxi

195 Golgi-localized cystic fibrosis transmembrane conductance regulator (CFTR)-associated li

196 assessed by forskolin-induced swelling in CF transmembrane conductance regulator (CFTR)-deficient org

197 % compared with control) and cystic fibrosis transmembrane conductance regulator (CFTR)-dependent and

198 estines that inherently lack cystic fibrosis transmembrane conductance regulator (CFTR)-dependent HCO

199 s, cAMP is known to regulate cystic fibrosis transmembrane conductance regulator (CFTR)-mediated anio

200 partially restored DeltaF508-cystic fibrosis transmembrane conductance regulator (CFTR)-mediated cAMP

201 These drugs activate cystic fibrosis transmembrane conductance regulator (CFTR)-mediated flui

202 ells, motile ciliated cells, cystic fibrosis transmembrane conductance regulator (CFTR)-rich ionocyte

203 e transporter (AlgE) and the cystic fibrosis transmembrane conductance regulator (CFTR).

204 se (PKG), and opening of the cystic fibrosis transmembrane conductance regulator (CFTR).

205 ATP-gated anion channel, the cystic fibrosis transmembrane conductance regulator (CFTR).

206 lls expressing the misfolded cystic fibrosis transmembrane conductance regulator (CFTR).

207 ue the trafficking mutant of cystic fibrosis transmembrane conductance regulator (CFTR).

208 e epithelial-cell chloride channel called CF transmembrane conductance regulator (CFTR).

209 e result of mutations in the cystic fibrosis transmembrane conductance regulator (CFTR).

210 secretin receptor, cilia and cystic fibrosis transmembrane conductance regulator (CFTR).

211 c fibrosis (CF) is caused by mutations in CF transmembrane conductance regulator (CFTR).

212 coding for the anion channel cystic fibrosis transmembrane conductance regulator (CFTR).

213 the epithelial anion channel cystic fibrosis transmembrane conductance regulator (CFTR).

214 n caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR).

215 f Phe-508 (DeltaF508) in the cystic fibrosis transmembrane conductance regulator (CFTR).

216 pression and function of the cystic fibrosis transmembrane conductance regulator (CFTR).

217 lial Cl(-) secretion via the cystic fibrosis transmembrane conductance regulator (CFTR).

218 e caused by mutations of the cystic fibrosis transmembrane conductance regulator (CFTR).

219 des for a Cl(-) channel, the cystic fibrosis transmembrane conductance regulator (CFTR).

220 binding domain (NBD1) of the cystic fibrosis transmembrane conductance regulator (CFTR).

221 active Cl- secretion via the cystic fibrosis transmembrane conductance regulator (CFTR).

222 ase causing mutations within cystic fibrosis transmembrane conductance regulator (CFTR).

223 e caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR).

224 s caused by mutations of the cystic fibrosis transmembrane conductance regulator (Cftr).

225 ssive disorder affecting the cystic fibrosis transmembrane conductance regulator (CFTR).

226 The cystic fibrosis transmembrane conductance regulator (CFTR, ABCC7), mutat

227 red an rAAV vector containing a truncated CF transmembrane conductance regulator (CFTRDeltaR) combine

228 TT, in deletion of Phe508 in cystic fibrosis transmembrane conductance regulator (DeltaF508 CFTR), th

229 of phenylalanine 508 of the cystic fibrosis transmembrane conductance regulator (F508 CFTR) is the m

230 zed that transgenic expression of porcine CF transmembrane conductance regulator (pCFTR) cDNA under c

231 cells via a reduction in the cystic fibrosis transmembrane conductance regulator activity and biosynt

232 essure resulted in decreased cystic fibrosis transmembrane conductance regulator activity and liquid

233 /adenylyl cyclase-dependent, cystic fibrosis transmembrane conductance regulator activity.

234 Reduced expression of cystic fibrosis transmembrane conductance regulator and dilation of acin

235 secretion appears to require cystic fibrosis transmembrane conductance regulator and electrogenic Na(

236 porters (ABC), including the cystic fibrosis transmembrane conductance regulator and P-glycoprotein.

237 was completely dependent on cystic fibrosis transmembrane conductance regulator and partially depend

238 -dependent activation of the cystic fibrosis transmembrane conductance regulator anion channel was in

239 codon in mRNAs encoding the cystic fibrosis transmembrane conductance regulator anion channel.

240 cidic pH produced by loss of cystic fibrosis transmembrane conductance regulator anion channels or pr

241 Opening and closing of the cystic fibrosis transmembrane conductance regulator are controlled by AT

242 We identify the cystic fibrosis transmembrane conductance regulator as a critical regula

243 unction mutations in the chloride channel CF transmembrane conductance regulator can elevate the acti

244 e used mice deficient in the cystic fibrosis transmembrane conductance regulator gene (Cftr) to test

245 ate gene studies include the cystic fibrosis transmembrane conductance regulator gene (CFTR), as well

246 enetic disease caused by mutations in the CF transmembrane conductance regulator gene (CFTR).

247 almost 2,000 variants in the cystic fibrosis transmembrane conductance regulator gene CFTR have empir

248 d to efficiently deliver the cystic fibrosis transmembrane conductance regulator gene to human airway

249 phils confirm a role for the cystic fibrosis transmembrane conductance regulator in maintaining HOCl

250 lucose co-transporter-1, and cystic fibrosis transmembrane conductance regulator in the jejunum.

251 ) cells after treatment with cystic fibrosis transmembrane conductance regulator inhibitor CFTR(inh)-

252 ence factors alkaline protease (AprA) and CF transmembrane conductance regulator inhibitory factor (C

253 eruginosa epoxide hydrolase, cystic fibrosis transmembrane conductance regulator inhibitory factor (C

254 n of our editase can correct cystic fibrosis transmembrane conductance regulator mRNA, restore full-l

255 As an ion channel, the cystic fibrosis transmembrane conductance regulator must form a continuo

256 F lung disease in a manner independent of CF transmembrane conductance regulator mutation.

257 Cystic fibrosis transmembrane conductance regulator potentiation by ivac

258 ch was partially reversed by cystic fibrosis transmembrane conductance regulator potentiation with iv

259 e the feasibility of using a cystic fibrosis transmembrane conductance regulator potentiator, ivacaft

260 The Cystic Fibrosis Transmembrane Conductance Regulator protein (CFTR) is a

261 he loss of chloride transport through the CF transmembrane conductance regulator protein (CFTR).

262 -length plasmid encoding the cystic fibrosis transmembrane conductance regulator protein was achieved

263 bed in CF including disabled cystic fibrosis transmembrane conductance regulator recruitment to phago

264 ficient degradation of human cystic fibrosis transmembrane conductance regulator requires function of

265 ) lung disease, the absence of functional CF transmembrane conductance regulator results in Cl(-)/HCO

266 Cystic fibrosis transmembrane conductance regulator was internalized in

267 creased levels of functional cystic fibrosis transmembrane conductance regulator were associated with

268 veolar macrophages from cystic fibrosis (CF) transmembrane conductance regulator(-/-) mice have impai

269 ed by mutations in the CFTR (cystic fibrosis transmembrane conductance regulator) gene that encodes a

270 toxemia, unaffected by CFTR (cystic fibrosis transmembrane conductance regulator) modulation, and res

271 acaftor-ivacaftor is a CFTR (cystic fibrosis transmembrane conductance regulator) modulator combinati

272 y the retention of the CFTR (cystic fibrosis transmembrane conductance regulator) mutant protein in t

273 icate a human-relevant CFTR (cystic fibrosis transmembrane conductance regulator) variant.Objectives:

274 al exocytosis of NHE3, CFTR (cystic fibrosis transmembrane conductance regulator), and GLUT5 required

275 tionale: Enhancing non-CFTR (cystic fibrosis transmembrane conductance regulator)-mediated anion secr

276 o for lumen formation, CFTR (cystic fibrosis transmembrane conductance regulator).

277 ociliary function in the absence of CFTR (CF transmembrane conductance regulator).Objectives: To test

278 egion Y-box 9+) to a mature (cystic fibrosis transmembrane conductance regulator+/secretin receptor+)

279 cellular adhesion molecule, cystic fibrosis transmembrane conductance regulator, and anion exchanger

280 in gross mislocalization of cystic fibrosis transmembrane conductance regulator, causing marked redu

281 on through activation of the cystic fibrosis transmembrane conductance regulator, CFTR.

282 n amino acid deletion in the cystic fibrosis transmembrane conductance regulator, CFTR.

283 ation with and activation of cystic fibrosis transmembrane conductance regulator, one of its binding

284 ngiocyte functions including cystic fibrosis transmembrane conductance regulator, secretin receptor,

285 embrane K(ATP) channels, the cystic fibrosis transmembrane conductance regulator, the transient recep

286 ing functional defect in the cystic fibrosis transmembrane conductance regulator, there is still an u

287 romone, Ste6* (sterile), and cystic fibrosis transmembrane conductance regulator, undergo Ubr1-depend

288 including the anion channel cystic fibrosis transmembrane conductance regulator, which shunt the tra

289 -fibrosis-associated protein cystic fibrosis transmembrane conductance regulator, which upon deletion

290 es, at least in part through cystic fibrosis transmembrane conductance regulator-associated channels,

291 These findings link loss of cystic fibrosis transmembrane conductance regulator-dependent alkaliniza

292 oncentration of bicarbonate, which mimics CF transmembrane conductance regulator-mediated anion secre

293 TEER) (>400 Ohms.cm(2)), and cystic fibrosis transmembrane conductance regulator-mediated short-circu

294 tide-binding domain from the cystic fibrosis transmembrane conductance regulator.

295 en through activation of the cystic fibrosis transmembrane conductance regulator.

296 lesser effects on misfolded cystic fibrosis transmembrane conductance regulator.

297 ells with a functional or mutated form of CF transmembrane conductance regulator.

298 denosine 3',5'-monophosphate/cystic fibrosis transmembrane conductance regulator/chloride bicarbonate

299 The cystic fibrosis transmembrane-conductance regulator (CFTR) chloride chan

300 ciated degradation (ERAD) of Cystic fibrosis transmembrane-conductance regulator (CFTR) is largely un